NCT06541262

Brief Summary

The purpose of this study is to evaluate the investigational drug, silmitasertib (a pill taken by mouth), in combination with FDA approved drugs for solid tumors. An investigational drug is one that has not been approved by the U.S. Food \& Drug Administration (FDA), or any other regulatory authorities around the world for use alone or in combination with any drug, for the condition or illness it is being used to treat. The goals of this part of the study are:

  • Establish a recommended dose of silmitasertib in combination with chemotherapy
  • Test the safety and tolerability of silmitasertib in combination with chemotherapy in subjects with cancer
  • To determine the activity of study treatments chosen based on:
  • How each subject responds to the study treatment
  • How long a subject lives without their disease returning/progressing

Trial Health

80
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
104

participants targeted

Target at P75+ for phase_1

Timeline
116mo left

Started Oct 2024

Longer than P75 for phase_1

Geographic Reach
2 countries

21 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress14%
Oct 2024Nov 2035

First Submitted

Initial submission to the registry

August 2, 2024

Completed
5 days until next milestone

First Posted

Study publicly available on registry

August 7, 2024

Completed
3 months until next milestone

Study Start

First participant enrolled

October 30, 2024

Completed
6 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

November 1, 2030

Expected
5 years until next milestone

Study Completion

Last participant's last visit for all outcomes

November 1, 2035

Last Updated

April 9, 2026

Status Verified

April 1, 2026

Enrollment Period

6 years

First QC Date

August 2, 2024

Last Update Submit

April 7, 2026

Conditions

Outcome Measures

Primary Outcomes (3)

  • Phase I- Number of Participants with Adverse Events as a Measure of Safety and Tolerability

    To characterize the safety profile of silmitasertib in combination with chemotherapy

    2 years plus 30 days

  • Phase I- Number of Participants with Dose Limiting Toxicities to determine RP2D

    To determine the Recommended Phase 2 Dose (RP2D) of silmitasertib in combination with chemotherapy

    21 days

  • Phase II- Determine the Overall Response Rate (ORR) of Participants using INRC

    To evaluate the efficacy of silmitasertib in combination with chemotherapy in 2 disease cohorts, based upon Overall response rate (ORR)

    2 years

Secondary Outcomes (5)

  • Phase I- Determine the Overall Response Rate (ORR) of Participants using INRC

    2 years

  • Number of participants with progression free survival (PFS) during study

    2 years

  • Phase II- Length of time that participants experience Overall Survival (OS)

    7 years

  • Phase II- Number of Participants with Adverse Events as a Measure of Safety and Tolerability

    2 years plus 30 days

  • Phase II - Determine the Disease Control Rate (DCR) of participants based on response

    2 years plus 30 days

Study Arms (4)

Phase I- Dose level 1

EXPERIMENTAL

Silmitasertib 600 mg/m2 twice a day plus Neuroblastoma: Regimen A: Irinotecan and Temozolomide Sarcoma: Regimen B: Vincristine, Irinotecan and Temozolomide

Drug: SilmitasertibDrug: IrinotecanDrug: TemozolomideDrug: Vincristine

Phase I- Dose level 2

EXPERIMENTAL

Silmitasertib 800 mg/m2 twice a day plus Neuroblastoma: Regimen A: Irinotecan and Temozolomide Sarcoma: Regimen B: Vincristine, Irinotecan and Temozolomide

Drug: SilmitasertibDrug: IrinotecanDrug: TemozolomideDrug: Vincristine

Phase II- Relapsed/refractory Neuroblastoma

EXPERIMENTAL

Silmitasertib RP2D twice a day plus Irinotecan and Temozolomide

Drug: SilmitasertibDrug: IrinotecanDrug: Temozolomide

Phase II- Relapsed/refractory Ewing sarcoma

EXPERIMENTAL

Silmitasertib RP2D twice a day plus Vincristine, irinotecan and temozolomide

Drug: SilmitasertibDrug: IrinotecanDrug: TemozolomideDrug: Vincristine

Interventions

Capsules

Also known as: CX-4945
Phase I- Dose level 1Phase I- Dose level 2Phase II- Relapsed/refractory Ewing sarcomaPhase II- Relapsed/refractory Neuroblastoma

IV

Phase I- Dose level 1Phase I- Dose level 2Phase II- Relapsed/refractory Ewing sarcomaPhase II- Relapsed/refractory Neuroblastoma

Oral

Phase I- Dose level 1Phase I- Dose level 2Phase II- Relapsed/refractory Ewing sarcomaPhase II- Relapsed/refractory Neuroblastoma

IV

Phase I- Dose level 1Phase I- Dose level 2Phase II- Relapsed/refractory Ewing sarcoma

Eligibility Criteria

AgeUp to 30 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Age: Less than 30 years old at initial diagnosis
  • Pathology All subjects must have a confirmed diagnosis of tumor type. Phase I: Relapsed/refractory solid tumors: Neuroblastoma, Ewing Sarcoma, Osteosarcoma, Rhabdomyosarcoma, Liposarcoma
  • Phase II:
  • Relapsed/refractory Neuroblastoma
  • Relapsed/refractory Ewing sarcoma
  • Tumor assessment:
  • Disease assessment is required for eligibility and must be done after last dose of previous therapy and prior to first dose of study drug.
  • Disease Status:
  • Relapsed/Refractory Neuroblastoma Relapsed disease defined as neuroblastoma that was previously in remission after standard therapy (at least 4 cycles of aggressive multi-drug induction chemotherapy, with or without radiation and surgery, followed by immunotherapy, or according to a standard high-risk treatment/neuroblastoma protocol) and has now relapsed and is in any number of relapses.
  • Refractory disease defined as High-risk neuroblastoma (as defined by INRG) that failed to achieve CR after at least 4 cycles of aggressive multi-drug induction chemotherapy, progression during upfront therapy or with disease remaining after standard immunotherapy.
  • International Neuroblastoma Risk Group Staging System (INRG) High Risk NB defined as one of the following:
  • Any age with International Neuroblastoma Risk Group (INRG) Stage L2, MS, or M with MYCN amplification
  • Age ≥ 547 days and INRG Stage M regardless of biologic features
  • Any age initially diagnosed with INRG Stage L1 MYCN amplified NBL who have progressed to Stage M without systemic chemotherapy
  • Age ≥ 547 days of age initially diagnosed with INRG Stage L1, L2, or MS who have progressed to Stage M without systemic chemotherapy
  • +24 more criteria

You may not qualify if:

  • Investigational Drugs: Subjects who are currently receiving another investigational drug are excluded from participation.
  • Anti-cancer Agents: Subjects who are currently receiving other anticancer agents are not eligible. Subjects must have fully recovered from the hematological and bone marrow suppression effects of prior therapy.
  • Subjects who are currently receiving Vitamin K antagonists (warfarin).
  • Subjects who are currently receiving the class of lipid-lowering medications HMG-CoA reductase inhibitors (statins).
  • Infection: Subjects who have an uncontrolled infection are not eligible until the infection is judged to be well controlled in the opinion of the investigator.
  • Subjects who, in the opinion of the investigator, may not be able to comply with the safety monitoring requirements of the study, or in whom compliance is likely to be suboptimal, should be excluded.
  • Subjects with any clinically significant unrelated systemic illness (serious infections or significant cardiac, pulmonary, hepatic or other organ dysfunction), that in the opinion of the investigator would compromise the subject's ability to tolerate protocol therapy, put them at additional risk for toxicity or would interfere with the study procedures or results.
  • Subjects with any of the following gastrointestinal disorders:
  • Active malabsorption (e.g. short gut) syndrome.
  • Uncontrolled diarrhea (excess of 4 stools/day)
  • Gastritis, ulcerative colitis, Chron's disease or hemorrhagic coloproctitis
  • History of gastric or small bowel surgery involving any extent of gastric or small bowel resection
  • Lactating subjects are not eligible unless they have agreed to not breastfeed their infants. There is an unknown but potential risk for adverse events in nursing infants secondary to treatment of the nursing subject with silmitasertib. (NOTE: breast milk cannot be stored for future use while the nursing subject is being treated on study.)
  • Subjects with a history of any other malignancy.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (21)

University of Alabama/Children's of Alabama

Birmingham, Alabama, 35233, United States

RECRUITING

Phoenix Children's Hospital

Phoenix, Arizona, 85016, United States

RECRUITING

UCSF Benioff Children's Hospital Oakland

Oakland, California, 94609, United States

RECRUITING

Rady Children's Hospital

San Diego, California, 92123, United States

RECRUITING

University of Florida

Gainesville, Florida, 32611, United States

RECRUITING

Nicklaus Children's Hospital

Miami, Florida, 33155, United States

RECRUITING

Arnold Palmer Hospital for Children

Orlando, Florida, 32806, United States

RECRUITING

All Children's Hospital Johns Hopkins Medicine

St. Petersburg, Florida, 33701, United States

RECRUITING

St. Joseph's Children's Hospital

Tampa, Florida, 33614, United States

RECRUITING

Kapiolani Medical Center for Women and Children

Honolulu, Hawaii, 96813, United States

RECRUITING

Norton Children's Research Institute/Affiliated with University of Louisville School of Medicine

Louisville, Kentucky, 40202, United States

RECRUITING

Children's Mercy Hospitals and Clinics

Kansas City, Missouri, 64108, United States

RECRUITING

Cardinal Glennon Children's Medical Center

St Louis, Missouri, 63104, United States

RECRUITING

Hackensack University Medical Center

Hackensack, New Jersey, 07601, United States

RECRUITING

Penn State Milton S. Hershey Medical Center and Children's Hospital

Hershey, Pennsylvania, 17033, United States

RECRUITING

Hasbro Children's Hospital

Providence, Rhode Island, 02903, United States

RECRUITING

Monroe Carrell Jr. Children's Hospital at Vanderbilt

Nashville, Tennessee, 37232, United States

RECRUITING

Children's Medical Center

Dallas, Texas, 75235, United States

RECRUITING

Primary Children's Hospital

Salt Lake City, Utah, 84113, United States

RECRUITING

Virginia Commonwealth University

Richmond, Virginia, 23284, United States

RECRUITING

UHC Sainte-Justine

Montreal, Quebec, QC H3S 2G4, Canada

RECRUITING

Related Links

MeSH Terms

Conditions

NeuroblastomaSarcoma, EwingOsteosarcomaRhabdomyosarcomaLiposarcoma

Interventions

silmitasertibIrinotecanTemozolomideVincristine

Condition Hierarchy (Ancestors)

Neuroectodermal Tumors, Primitive, PeripheralNeuroectodermal Tumors, PrimitiveNeoplasms, NeuroepithelialNeuroectodermal TumorsNeoplasms, Germ Cell and EmbryonalNeoplasms by Histologic TypeNeoplasmsNeoplasms, Glandular and EpithelialNeoplasms, Nerve TissueNeoplasms, Bone TissueNeoplasms, Connective TissueNeoplasms, Connective and Soft TissueSarcomaMyosarcomaNeoplasms, Muscle TissueNeoplasms, Adipose Tissue

Intervention Hierarchy (Ancestors)

CamptothecinAlkaloidsHeterocyclic CompoundsDacarbazineTriazenesOrganic ChemicalsImidazolesAzolesHeterocyclic Compounds, 1-RingVinca AlkaloidsSecologanin Tryptamine AlkaloidsIndole AlkaloidsIndolesHeterocyclic Compounds, 2-RingHeterocyclic Compounds, Fused-RingIndolizidinesIndolizines

Study Officials

  • Chandrika Behura, MD

    Penn State Health Children's Hospital

    STUDY CHAIR

Central Study Contacts

Study Design

Study Type
interventional
Phase
phase 1
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
SEQUENTIAL
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Beat Childhood Cancer Chair

Study Record Dates

First Submitted

August 2, 2024

First Posted

August 7, 2024

Study Start

October 30, 2024

Primary Completion (Estimated)

November 1, 2030

Study Completion (Estimated)

November 1, 2035

Last Updated

April 9, 2026

Record last verified: 2026-04

Data Sharing

IPD Sharing
Will not share

Locations