NCT02055781

Brief Summary

Phase 3, randomized, controlled study to evaluate the safety and efficacy of oral pacritinib compared to Best Available Therapy (BAT) in patients with thrombocytopenia and primary or secondary myelofibrosis.

Trial Health

68
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
311

participants targeted

Target at P50-P75 for phase_3

Timeline
Completed

Started Feb 2014

Geographic Reach
12 countries

122 active sites

Status
terminated

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

February 1, 2014

Completed
2 days until next milestone

First Submitted

Initial submission to the registry

February 3, 2014

Completed
2 days until next milestone

First Posted

Study publicly available on registry

February 5, 2014

Completed
2.2 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 1, 2016

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

April 1, 2016

Completed
5.6 years until next milestone

Results Posted

Study results publicly available

November 18, 2021

Completed
Last Updated

November 18, 2021

Status Verified

October 1, 2021

Enrollment Period

2.2 years

First QC Date

February 3, 2014

Results QC Date

November 23, 2020

Last Update Submit

October 21, 2021

Conditions

Keywords

MyelofibrosisPost-Polycythemia Vera MyelofibrosisPost-Essential Thrombocythemia MyelofibrosisPrimary MyelofibrosisPolycythemia VeraEssential ThrombocythemiaBone Marrow DiseaseHematologic DiseasesHemorrhagic DisordersSplenomegalyPacritinibMPN-SAFMPN-SAF TSSAnemiaMyeloproliferative NeoplasmSpleen volumeThrombocytopeniaSB1518

Outcome Measures

Primary Outcomes (2)

  • Spleen Volume Reduction

    Proportion of patients achieving a ≥ 35% reduction in spleen volume from baseline to week 24 as measured by magnetic resonance imaging (MRI) or computed tomography (CT).

    Baseline to Week 24

  • Total Symptom Score (TSS) Reduction

    Proportion of patients achieving a ≥ 50% reduction in the total symptom score from baseline to Week 24 on the Myeloproliferative Neoplasm Symptom Assessment Form 2.0 (MPN-SAF TSS 2.0). Responses (on a scale from 0 \[absent\] to 10 \[worst imaginable\]) to questions about symptoms (tiredness, early satiety, abdominal discomfort, night sweats, pruritus, bone pain, and pain under the ribs on the left side) were used to calculate the TSS.

    Baseline to Week 24

Study Arms (3)

Pacritinib, Once Daily

EXPERIMENTAL

Pacritinib 400 mg QD

Drug: Pacritinib

Pacritinib, Twice Daily

EXPERIMENTAL

Pacritinib 200 mg BID

Drug: Pacritinib

Best Available Therapy

ACTIVE COMPARATOR

BAT includes any physician-selected treatment for myelofibrosis, such as approved JAK2 inhibitors administered according to package insert for patients with thrombocytopenia, and may include any treatment received before study entry.

Drug: Best Available Therapy

Interventions

Pacritinib, Once DailyPacritinib, Twice Daily
Best Available Therapy

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Intermediate -1 or -2 or high-risk Myelofibrosis (per Passamonti et al 2010)
  • Thrombocytopenia (platelet count ≤ 100,000/µL) at any time after signing informed consent
  • Palpable splenomegaly ≥ 5 cm on physical examination
  • Total Symptom Score ≥ 13 on the MPN-SAF TSS 2.0, not including the inactivity question
  • Patients who are platelet or red blood cell transfusion-dependent are eligible
  • Adequate white blood cell counts (with low blast counts), liver function, and renal function
  • At least 6 months from prior splenic irradiation
  • At least 1-4 weeks since prior myelofibrosis therapy, including any erythropoietic or thrombopoietic agent
  • Not pregnant, not lactating, and agree to use effective birth control
  • Able and willing to undergo frequent MRI or CT assessments and complete symptom assessments using a patient-reported outcome instrument

You may not qualify if:

  • Prior treatment with more than 2 JAK2 inhibitors or with pacritinib
  • There is no maximum cumulative prior JAK2 inhibitor treatment
  • History of (or plans to undergo) spleen removal surgery or allogeneic stem cell transplant
  • Ongoing gastrointestinal medical condition such as Crohn's disease, Inflammatory bowel disease, chronic diarrhea, or constipation
  • Active bleeding that requires hospitalization during the screening period
  • Cardiovascular disease, including recent history or currently clinically symptomatic and uncontrolled: congestive heart failure, arrhythmia, angina, QTc prolongation or other QTc risk factors, myocardial infarction
  • Other malignancy within last 3 years other than certain limited skin, cervical, prostate, breast, or bladder cancers
  • Other ongoing, uncontrolled illnesses (including HIV infection and active hepatitis A, B, or C), psychiatric disorder, or social situation that would prevent good care on this study
  • Life expectancy \< 6 months

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (122)

Mayo Clinic Arizona

Scottsdale, Arizona, 85259, United States

Location

Arizona Clinical Research Center

Tucson, Arizona, 85715, United States

Location

City of Hope

Duarte, California, 91010, United States

Location

Moores Cancer Centre

La Jolla, California, 92093, United States

Location

USC Norris Comprehensive Cancer Center

Los Angeles, California, 90033, United States

Location

Stanford Cancer Center

Stanford, California, 94305, United States

Location

Rocky Mountain Cancer Center

Boulder, Colorado, 80303, United States

Location

George Washington University- Medical Faculty Associates

Washington D.C., District of Columbia, 20037, United States

Location

SCRI- Florida Cancer Specialists South Region

Fort Myers, Florida, 33916, United States

Location

SCRI - Florida Cancer Specialists North Region

St. Petersburg, Florida, 33705, United States

Location

H. Lee Moffitt Cancer Center & Research Institute

Tampa, Florida, 33612, United States

Location

Northwestern University

Chicago, Illinois, 60611, United States

Location

Carle Cancer Center

Urbana, Illinois, 61801, United States

Location

Indiana University Goshen Cancer Centre

Goshen, Indiana, 46526, United States

Location

Investigative Clinical Research of Indiana

Indianapolis, Indiana, 46260, United States

Location

University of Iowa Hospitals and Clinics

Iowa City, Iowa, 52242, United States

Location

Siouxland Hematology-Oncology Associates, L.L.P (SHOA)

Sioux City, Iowa, 51101, United States

Location

Norton Cancer Institute, Suburban

Louisville, Kentucky, 40207, United States

Location

St Joseph Mercy Hospital

Ann Arbor, Michigan, 48106, United States

Location

University of Michigan

Ann Arbor, Michigan, 48109, United States

Location

Henry Ford Health System

Detroit, Michigan, 48202, United States

Location

Providence Cancer Institute

Southfield, Michigan, 48075, United States

Location

Washington University School of Medicine Division of Oncology

St Louis, Missouri, 63110, United States

Location

Nebraska Hematology-Oncology, P.C.

Lincoln, Nebraska, 68506, United States

Location

Hackensack University

Hackensack, New Jersey, 07601, United States

Location

Hematology-Oncology Associates of Northern Jersey

Morristown, New Jersey, 07962, United States

Location

New Mexico Cancer Care Alliance

Albuquerque, New Mexico, 87106, United States

Location

Mount Sinai Medical Center

New York, New York, 10029, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

Stony Brook University Medical Center

Stony Brook, New York, 11794, United States

Location

SCRI-Oncology Hematology Care

Cincinnati, Ohio, 45242, United States

Location

Cleveland Clinic-Taussig Cancer Center

Cleveland, Ohio, 44195, United States

Location

University of Oklahoma

Oklahoma City, Oklahoma, 73104, United States

Location

Thomas Jefferson University

Philadelphia, Pennsylvania, 19107, United States

Location

UPMC Hillman Cancer Center

Pittsburgh, Pennsylvania, 15232, United States

Location

Upstate Oncology Associates

Greenville, South Carolina, 29601, United States

Location

Sarah Cannon Research Institute (SCRI)

Nashville, Tennessee, 37203, United States

Location

Texas Onocolgy-Baylor Sammons Cancer Center

Dallas, Texas, 75246, United States

Location

UT Southwestern Medical Center

Dallas, Texas, 75390, United States

Location

UTMB Galveston

Galveston, Texas, 77555, United States

Location

Houston Methodist

Houston, Texas, 77030, United States

Location

University of Texas MD Anderson Cancer Center

Houston, Texas, 77030, United States

Location

Cancer Care Centers of South Texas

San Antonio, Texas, 78229, United States

Location

Huntsman Cancer Hospital

Salt Lake City, Utah, 84112, United States

Location

Virginia Cancer Specialists

Leesburg, Virginia, 20176, United States

Location

Providence Regional Cancer Partnership

Everett, Washington, 98201, United States

Location

Fred Hutchinson Cancer Research Center

Seattle, Washington, 98109, United States

Location

Green Bay Oncology

Green Bay, Wisconsin, 54301, United States

Location

Froedtert Hospital and the Medical College of Wisconsin

Milwaukee, Wisconsin, 53226, United States

Location

Medical College of Wisconsin

Milwaukee, Wisconsin, 53226, United States

Location

St George Hospital

Kogarah, New South Wales, 2217, Australia

Location

Royal Adelaide Hospital

Adelaide, South Australia, 5000, Australia

Location

Box Hill Hospital

Box Hill, Victoria, 3128, Australia

Location

Monash Health - Monash Medical Centre

Clayton, Victoria, 3168, Australia

Location

Perth Blood Institute

Nedlands, Western Australia, 6009, Australia

Location

Haematology and Oncology Clinics of Australia

Chermside, 4032, Australia

Location

Prince of Wales Hospital

Randwick, 2031, Australia

Location

Centre Hospitalier de Jolimont-Lobbes

Haine-Saint-Paul, Hainaut, Belgium

Location

ZNA - Stuivenberg

Antwerp, 2060, Belgium

Location

AZ Sint Jan Brugge-Oostende AV

Bruges, 8000, Belgium

Location

Hopital Brugmann

Brussels, 1020, Belgium

Location

Cliniques Universitaires St-Luc

Brussels, 1200, Belgium

Location

St Augustinus

Wilrijk, 2610, Belgium

Location

UC Louvain

Yvoir, 5530, Belgium

Location

Saint John Regional Hospital

Saint John, New Brunswick, E2L 4L2, Canada

Location

Princess Margaret Cancer Center

Toronto, Ontario, M5G2M9, Canada

Location

Fakultní nemocnice Brno

Brno, NAP, 62500, Czechia

Location

Faculty Hospital Olomouc

Olomouc, NAP, 775 20, Czechia

Location

Fakultní nemocnice Plzeň

Pilsen, NAP, 30460, Czechia

Location

University Hospital Hradec Kralove

Králová, 500 05, Czechia

Location

Chu d'Amiens Hopital Sud

Amiens, Cedex 1, 80054, France

Location

Hôpital Caremeau

Nîmes, Cedex 9, 30029, France

Location

CHU Rennes

Rennes, Cedex 9, 35033, France

Location

CHU Purpan

Toulouse, Cedex 9, 31059, France

Location

CH de Mulhouse

Mulhouse, Cedex, 68070, France

Location

CHU de CAEN

Caen, 14000, France

Location

Centre Hospitalier de Lens

Lens, 62300, France

Location

Hopital l'Archet, CHU de Nice

Nice, BP 30 79 06202, France

Location

Saint Antoine Hospital

Paris, 75012, France

Location

Centre Hospitalier Lyon Sud

Pierre-Bénite, 69495, France

Location

CHU de Strasbourg

Strasbourg, 67091, France

Location

Institut Gustave Roussy

Villejuif, 94805, France

Location

Charite-Medical University

Berlin, 12203, Germany

Location

Klinik I fur Innere Medizin, Universitat Koln

Cologne, 50924, Germany

Location

Gemeinschaftspraxis Hämatologie/Onkologie

Dresden, 01307, Germany

Location

University Hospital Essen

Essen, D-45122, Germany

Location

Uniklinik Freiburg

Freiburg im Breisgau, 79106, Germany

Location

Universitatsklinikum Halle (Saale)

Halle, 06120, Germany

Location

University Hospital Leipzig

Leipzig, 04103, Germany

Location

Städtisches Klinikum München GmbH

München, 81737, Germany

Location

University of Munster

Münster, 48149, Germany

Location

University Hospital Ulm

Ulm, 89081, Germany

Location

Semmelweis Egyetem AOK

Budapest, 1083, Hungary

Location

University of Debrecen, Belgyogyaszati Intezet

Debrecen, 4032, Hungary

Location

Bekes Megyei Pandy Kalman Korhaz

Gyula, 5700, Hungary

Location

Kaposi Mór Oktató Kórház

Kaposvár, 7400, Hungary

Location

SZTE II. sz Belgyogyoszati Klinika es Kardiologiai Kozpont

Szeged, 6720, Hungary

Location

Jász-Nagykun-Szolnok Megyei Hetényi Géza Kórház-Rendelőint

Szolnok, 5004, Hungary

Location

University Hospital Maastricht

Maastricht, 6229 HX, Netherlands

Location

Erasmus MC

Rotterdam, 3015 CE, Netherlands

Location

Auckland District Health Board, Auckland City Hospital

Auckland, 1023, New Zealand

Location

Middlemore Hospital

Auckland, 1640, New Zealand

Location

Canterbury District Health Board

Christchurch, 8001, New Zealand

Location

North Shore Hospital

Takapuna, 0740, New Zealand

Location

CCDHB - Wellington Hospital

Wellington, 6021, New Zealand

Location

Bashkir State Medical University

Ufa, Bashkortostan Republic, 450083, Russia

Location

Saratov State Medical University

Saratov, Saratov Oblast, 410028, Russia

Location

National Haematology Research Center

Moscow, 125167, Russia

Location

Republican Hopsital n.a. V.A. Baranov

Petrozavodsk, 185019, Russia

Location

Ryazan Regional Clinical Hospital

Ryazan, 390039, Russia

Location

Russian Research Institute of Hematology and Transfusiology

Saint Petersburg, 191024, Russia

Location

Military Medical Academy n.a. S.M. Kirov

Saint Petersburg, 194044, Russia

Location

Royal Liverpool University Hospital

Liverpool, Merseyside, L7 8XP, United Kingdom

Location

Belfast Health and Social Care Trust

Belfast, Northern Ireland, BT9 7AB, United Kingdom

Location

Birmingham Heartlands Hospital

Birmingham, B9 5SS, United Kingdom

Location

Beatson West of Scotland Cancer Centre

Glasgow, G12 OYN, United Kingdom

Location

Leicester Royal Infirmary

Leicester, LE1 5WW, United Kingdom

Location

Guy's Hospital

London, SE1 9RT, United Kingdom

Location

Hammersmith Hosp - ICH NHS Trust

London, W12 OHS, United Kingdom

Location

The Christie NHS Foundation Trust

Manchester, M20 4BX, United Kingdom

Location

Oxford University Hospitals NHS Trust

Oxford, OX3 7LE, United Kingdom

Location

Royal Hallamshire Hospital

Sheffield, S10 2JF, United Kingdom

Location

Related Publications (4)

  • Mascarenhas J, Hoffman R, Talpaz M, Gerds AT, Stein B, Gupta V, Szoke A, Drummond M, Pristupa A, Granston T, Daly R, Al-Fayoumi S, Callahan JA, Singer JW, Gotlib J, Jamieson C, Harrison C, Mesa R, Verstovsek S. Pacritinib vs Best Available Therapy, Including Ruxolitinib, in Patients With Myelofibrosis: A Randomized Clinical Trial. JAMA Oncol. 2018 May 1;4(5):652-659. doi: 10.1001/jamaoncol.2017.5818.

    PMID: 29522138BACKGROUND
  • Ajufo H, Bewersdorf JP, Harrison C, Palandri F, Mascarenhas J, Palmer J, Gerds A, Kiladjian JJ, Buckley S, Derkach A, Roman-Torres K, Rampal RK. Pacritinib Response Is Associated With Overall Survival in Myelofibrosis: PERSIST-2 Landmark Analysis of Survival. Eur J Haematol. 2025 Feb;114(2):238-247. doi: 10.1111/ejh.14321. Epub 2024 Oct 14.

  • Verstovsek S, Mesa R, Talpaz M, Kiladjian JJ, Harrison CN, Oh ST, Vannucchi AM, Rampal R, Scott BL, Buckley SA, Craig AR, Roman-Torres K, Mascarenhas JO. Retrospective analysis of pacritinib in patients with myelofibrosis and severe thrombocytopenia. Haematologica. 2022 Jul 1;107(7):1599-1607. doi: 10.3324/haematol.2021.279415.

  • Tremblay D, Mesa R, Scott B, Buckley S, Roman-Torres K, Verstovsek S, Mascarenhas J. Pacritinib demonstrates spleen volume reduction in patients with myelofibrosis independent of JAK2V617F allele burden. Blood Adv. 2020 Dec 8;4(23):5929-5935. doi: 10.1182/bloodadvances.2020002970.

MeSH Terms

Conditions

Primary MyelofibrosisPolycythemia VeraThrombocythemia, EssentialBone Marrow DiseasesHematologic DiseasesHemorrhagic DisordersSplenomegalyAnemiaMyeloproliferative DisordersThrombocytopenia

Interventions

11-(2-pyrrolidin-1-ylethoxy)-14,19-dioxa-5,7,26-triazatetracyclo(19.3.1.1(2,6).1(8,12))heptacosa-1(25),2(26),3,5,8,10,12(27),16,21,23-decaene

Condition Hierarchy (Ancestors)

Hemic and Lymphatic DiseasesBone Marrow NeoplasmsHematologic NeoplasmsNeoplasms by SiteNeoplasmsBlood Coagulation DisordersThrombocytosisBlood Platelet DisordersHypertrophyPathological Conditions, AnatomicalPathological Conditions, Signs and SymptomsCytopenia

Results Point of Contact

Title
Beth Ziemba
Organization
CTI BioPharma Corp.

Study Officials

  • Simran Singh

    Sr. Director, Head of Clinical Operations

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 3, 2014

First Posted

February 5, 2014

Study Start

February 1, 2014

Primary Completion

April 1, 2016

Study Completion

April 1, 2016

Last Updated

November 18, 2021

Results First Posted

November 18, 2021

Record last verified: 2021-10

Locations