NCT04105972

Brief Summary

This study will evaluate the efficacy, safety, and pharmacodynamics of elexacaftor (ELX, VX-445) in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are homozygous for F508del.

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
176

participants targeted

Target at P25-P50 for phase_3

Timeline
Completed

Started Oct 2019

Shorter than P25 for phase_3

Geographic Reach
4 countries

35 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

September 24, 2019

Completed
2 days until next milestone

First Posted

Study publicly available on registry

September 26, 2019

Completed
7 days until next milestone

Study Start

First participant enrolled

October 3, 2019

Completed
10 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 24, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

July 24, 2020

Completed
1.1 years until next milestone

Results Posted

Study results publicly available

August 18, 2021

Completed
Last Updated

August 18, 2021

Status Verified

July 1, 2021

Enrollment Period

10 months

First QC Date

September 24, 2019

Results QC Date

July 23, 2021

Last Update Submit

July 23, 2021

Conditions

Outcome Measures

Primary Outcomes (1)

  • Absolute Change in CF Questionnaire-Revised (CFQ-R) Respiratory Domain Score

    The CFQ-R is a validated participant-reported outcome measuring health-related quality of life for participants with cystic fibrosis. Respiratory domain assessed respiratory symptoms, score range: 0-100; higher scores indicating fewer symptoms and better health-related quality of life.

    From Baseline Through Week 24

Secondary Outcomes (3)

  • Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)

    From Baseline Through Week 24

  • Absolute Change in Sweat Chloride (SwCl)

    From Baseline Through Week 24

  • Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)

    From Day 1 in the Treatment Period up to 28 Days After Last Dose of Study Drug or to the Completion of Study Participation Date, Whichever Occurs First (up to Week 28)

Study Arms (2)

TEZ/IVA

ACTIVE COMPARATOR

Following TEZ/IVA run-in period of 4 weeks, participants received TEZ 100 milligrams (mg) once daily (qd)/IVA 150 mg every 12 hours (q12h) in the treatment period for 24 weeks.

Drug: TEZ/IVADrug: IVA

ELX/TEZ/IVA

EXPERIMENTAL

Following TEZ/IVA run-in period of 4 weeks, participants received ELX 200 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 24 weeks.

Drug: ELX/TEZ/IVADrug: IVA

Interventions

FDC tablet for oral administration.

Also known as: VX-445/VX-661/VX-770, elexacaftor/tezacaftor/ivacaftor
ELX/TEZ/IVA

Fixed-dose combination (FDC) tablet for oral administration.

Also known as: VX-661/VX-770, tezacaftor/ivacaftor
TEZ/IVA
IVADRUG

Mono tablet for oral administration.

Also known as: VX-770, ivacaftor
ELX/TEZ/IVATEZ/IVA

Eligibility Criteria

Age12 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Homozygous for the F508del mutation (F/F)
  • Forced expiratory volume in 1 second (FEV1) value ≥40% and ≤90% of predicted mean for age, sex, and height

You may not qualify if:

  • Clinically significant cirrhosis with or without portal hypertension
  • Lung infection with organisms associated with a more rapid decline in pulmonary status
  • Solid organ or hematological transplantation

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (35)

The Prince Charles Hospital

Chermside, Australia

Location

Institute for Respiratory Health

Nedlands, Australia

Location

Perth Children's Hospital

Nedlands, Australia

Location

John Hunter Hospital & Hunter Medical Research Institute and John Hunter Children's Hospital

New Lambton, Australia

Location

The Royal Children's Hospital

Parkville, VIC, Australia

Location

Queensland Children's Hospital

South Brisbane, Australia

Location

Universitair Ziekenhuis Brussel - Campus Jette

Brussels, Belgium

Location

UZ Antwerpen

Edegem, Belgium

Location

Universitair Ziekenhuis Gent

Ghent, Belgium

Location

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, Belgium

Location

Charite Paediatric Pulmonology Department

Berlin, Germany

Location

Universitaetsklinkum Koeln, CF-Studienzentrum

Cologne, Germany

Location

Ruhrlandklinik Westdeutsches Lungenzentrum am Klinikum Essen

Essen, Germany

Location

Universitatsklinikum Essen (AoR), Kinderklinik III, Abt. fur Pneumologie

Essen, Germany

Location

Johann Wolfgang Goethe University

Frankfurt, Germany

Location

Mukeviszidose-Zentrum am Universitatsklinikum Jena, Klinik fuer Kinder- und Jugendmedizin

Jena, Germany

Location

Klinikum Innenstadt, University of Munich

München, Germany

Location

Pneumologisches Studienzentrum Muenchen-West

München, Germany

Location

Belfast City Hospital

Belfast, United Kingdom

Location

University Hospitals Birmingham NHS Foundation Trust

Birmingham, United Kingdom

Location

University Hospitals Bristol NHS Foundation Trust, Bristol Royal Hospital

Bristol, United Kingdom

Location

Papworth Hospital NHS Foundation Trust, Papworth Everard

Cambridge, United Kingdom

Location

Western General Hospital

Edinburgh, United Kingdom

Location

Royal Devon and Exeter NHS Foundation Trust, Royal Devon and Exeter Hospital

Exeter, United Kingdom

Location

Clinical Research Facility, Queen Elizabeth University Hospital

Glasgow, United Kingdom

Location

St. James University Hospital

Leeds, United Kingdom

Location

Leeds General Infirmary

Leeds, West Yorkshire, United Kingdom

Location

Alder Hey Children's Alder Hey Children's NHS Foundation Trust

Liverpool, United Kingdom

Location

Great Ormond Street Hospital for Sick Children

London, United Kingdom

Location

London and St Bartholomew's Hospital

London, United Kingdom

Location

The University Hospital of South Manchester

Manchester, United Kingdom

Location

The Newcastle upon Tyne Hospitals NHS Foundation Trust, The Royal Victoria Infirmary

Newcastle upon Tyne, United Kingdom

Location

Nottingham University Hospitals NHS Trust, Queens Medical Center

Nottingham, United Kingdom

Location

All Wales Adult Cystic Fibrosis Centre, University Hospital Llandough

Penarth, United Kingdom

Location

Southampton General Hospital

Southampton, United Kingdom

Location

Related Publications (3)

  • Heneghan M, Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2023 Nov 20;11(11):CD010966. doi: 10.1002/14651858.CD010966.pub4.

  • Sutharsan S, McKone EF, Downey DG, Duckers J, MacGregor G, Tullis E, Van Braeckel E, Wainwright CE, Watson D, Ahluwalia N, Bruinsma BG, Harris C, Lam AP, Lou Y, Moskowitz SM, Tian S, Yuan J, Waltz D, Mall MA; VX18-445-109 study group. Efficacy and safety of elexacaftor plus tezacaftor plus ivacaftor versus tezacaftor plus ivacaftor in people with cystic fibrosis homozygous for F508del-CFTR: a 24-week, multicentre, randomised, double-blind, active-controlled, phase 3b trial. Lancet Respir Med. 2022 Mar;10(3):267-277. doi: 10.1016/S2213-2600(21)00454-9. Epub 2021 Dec 20.

  • Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2020 Dec 17;12(12):CD010966. doi: 10.1002/14651858.CD010966.pub3.

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

elexacaftor, ivacaftor, tezacaftor drug combinationtezacaftor, ivacaftor drug combinationivacaftor

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR
Expanded Access
Yes

Study Record Dates

First Submitted

September 24, 2019

First Posted

September 26, 2019

Study Start

October 3, 2019

Primary Completion

July 24, 2020

Study Completion

July 24, 2020

Last Updated

August 18, 2021

Results First Posted

August 18, 2021

Record last verified: 2021-07

Data Sharing

IPD Sharing
Will not share

Details on Vertex data sharing criteria and process for requesting access can be found at: https://www.vrtx.com/independent research/clinical-trial-data-sharing.

Locations