NCT04058366

Brief Summary

This study evaluated the long-term safety, efficacy, and pharmacodynamics of elexacaftor (ELX, VX-445) in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are heterozygous for the F508del mutation and a gating or residual function mutation (F/G and F/RF genotypes).

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
251

participants targeted

Target at P50-P75 for phase_3

Timeline
Completed

Started Dec 2019

Typical duration for phase_3

Geographic Reach
12 countries

84 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

August 14, 2019

Completed
1 day until next milestone

First Posted

Study publicly available on registry

August 15, 2019

Completed
4 months until next milestone

Study Start

First participant enrolled

December 5, 2019

Completed
3 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 16, 2022

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

December 16, 2022

Completed
1.1 years until next milestone

Results Posted

Study results publicly available

January 16, 2024

Completed
Last Updated

January 16, 2024

Status Verified

December 1, 2023

Enrollment Period

3 years

First QC Date

August 14, 2019

Results QC Date

December 15, 2023

Last Update Submit

December 15, 2023

Conditions

Outcome Measures

Primary Outcomes (1)

  • Part A: Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)

    From Baseline up to Week 100

Secondary Outcomes (6)

  • Part A: Absolute Change From Parent Study Baseline in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)

    From Baseline at Week 96

  • Part A: Absolute Change From Parent Study Baseline in Sweat Chloride (SwCl)

    From Baseline at Week 96

  • Part A: Absolute Change From Parent Study Baseline in Body Mass Index (BMI)

    From Baseline at Week 96

  • Part A: Absolute Change From Parent Study Baseline in BMI Z-score

    From Baseline at Week 96

  • Part A: Absolute Change From Parent Study Baseline in Body Weight

    From Baseline at Week 96

  • +1 more secondary outcomes

Study Arms (1)

ELX/TEZ/IVA

EXPERIMENTAL

Part A: Participants received ELX (elexacaftor) 200 milligram (mg) once daily (qd)/TEZ 100 mg qd/IVA 150 mg every 12 hours (q12h) in the treatment period for 96 weeks. Part B: Participants from certain countries participated in Part B and continued to receive ELX 200 mg qd /TEZ 100 mg qd/IVA 150 mg q12h in the treatment period for 48 weeks.

Drug: ELX/TEZ/IVADrug: IVA

Interventions

Fixed-dose combination (FDC) tablet for oral administration.

Also known as: VX-445/VX-661/VX-770, elexacaftor/tezacaftor/ivacaftor
ELX/TEZ/IVA
IVADRUG

Tablet for oral administration.

Also known as: VX-770, ivacaftor
ELX/TEZ/IVA

Eligibility Criteria

Age12 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Completed study drug treatment in parent study (VX18-445-104); or had study drug interruption(s) in parent study but completed study visits up to the last scheduled visit of the Treatment Period in the parent study

You may not qualify if:

  • History of study drug intolerance in parent study

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (84)

Banner University of Arizona Medical Center

Tucson, Arizona, 85724, United States

Location

Miller Children's Hospital / Long Beach Memorial

Long Beach, California, 90806, United States

Location

Stanford University

Palo Alto, California, 94304, United States

Location

University of California Davis Medical Center

Sacramento, California, 95817, United States

Location

University of California San Francisco, Lung Transplant Program

San Francisco, California, 94143, United States

Location

National Jewish Health

Denver, Colorado, 80206, United States

Location

University of Miami Miller School of Medicine

Miami, Florida, 33136, United States

Location

Central Florida Pulmonary Group, PA

Orlando, Florida, 32803, United States

Location

Indiana University

Indianapolis, Indiana, 46202, United States

Location

University of Kansas Medical Center

Kansas City, Kansas, 66160, United States

Location

University of Kentucky

Lexington, Kentucky, 40536, United States

Location

Massachusetts General Hospital Cystic Fibrosis Center Clinical Rsearch Center

Boston, Massachusetts, 02114, United States

Location

Boston Children's Hospital

Boston, Massachusetts, 02115, United States

Location

Michigan Medicine

Ann Arbor, Michigan, 48109-5212, United States

Location

University of Minnesota

Minneapolis, Minnesota, 55455, United States

Location

Washington University School of Medicine / St. Louis Children's Hospital

St Louis, Missouri, 63110, United States

Location

Mount Sinai Beth Israel

New York, New York, 10003, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

University of North Carolina Hospitals

Chapel Hill, North Carolina, 27514, United States

Location

UC Health Holmes

Cincinnati, Ohio, 45220, United States

Location

Rainbow Babies and Children's Hospital/University Hospitals Cleveland Medical Center

Cleveland, Ohio, 44106, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, 43205, United States

Location

ProMedica Toledo Hospital/Toledo Children's Hospital/Pediatric Pulmonary & Cystic Fibrosis Center

Toledo, Ohio, 43606, United States

Location

University of Oklahoma Health Sciences Center

Oklahoma City, Oklahoma, 73104, United States

Location

Oregon Health & Science University

Portland, Oregon, 97239, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, 15224, United States

Location

Dell Children's Medical Group

Austin, Texas, 78723, United States

Location

The University of Texas Southwestern Medical Center

Dallas, Texas, 75390, United States

Location

Texas Children's Hospital

Houston, Texas, 77030, United States

Location

University of Utah / Primary Children's Medical Center

Salt Lake City, Utah, 84132, United States

Location

University of Washington Medical Center

Seattle, Washington, 98195, United States

Location

University of Wisconsin Hospital and Clinics

Madison, Wisconsin, 53792, United States

Location

The Prince Charles Hospital

Chermside, Australia

Location

Alfred Hospital

Melbourne, Australia

Location

Telethon Kids Institute

Nedlands, Australia

Location

The Royal Children's Hospital

Parkville, Australia

Location

Mater Adult Hospital

South Brisbane, Australia

Location

Queensland Children's Hospital

South Brisbane, Australia

Location

Westmead Hospital

Westmead, Australia

Location

Cliniques Universitaires de Bruxelles Hopital Erasme

Brussels, Belgium

Location

Universitair Ziekenhuis Brussel - Campus Jette

Brussels, Belgium

Location

Universitair Ziekenhuis Gent

Ghent, Belgium

Location

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, Belgium

Location

McGill University Health Center

Montreal, Canada

Location

St. Paul's Hospital

Vancouver, Canada

Location

Juliane Marie Center, Rigshospitalet

Copenhagen, Denmark

Location

Centre Hospitalier Lyon Sud

Benite Cedex, France

Location

Groupe Hospitaler Pellegrin, CHU De Bordeaux

Bordeaux, France

Location

CHRU de Lille - Hopital Albert Calmette

Lille, France

Location

CHU Marseille - Hopital Nord

Marseille, France

Location

CHU de Montpellier - Hopital Arnaud de Villeneuve

Montpellier, France

Location

Hopital Cochin

Paris, France

Location

Hopital Necker, Enfants Malades

Paris, France

Location

Hopital Pontchaillou CHU de Rennes

Rennes, France

Location

Charite Paediatric Pulmonology Department

Berlin, Germany

Location

Ruhrlandklinik Westdeutsches Lungenzentrum am Klinikum Essen

Essen, Germany

Location

Justus-Liebig-Universitaet Gießen Zentrum fur Kinderheilkunde und Jugendmedizin

Giessen, Germany

Location

Universitätsklinikum Halle (Saale) / Universitätsklinik und Poliklinik für Innere Medizin, Schwerpunkt Pneumologie

Halle, Germany

Location

Pneumologisches Studienzentrum Muenchen-West

München, Germany

Location

University Hospital Wuerzburg

Würzburg, Germany

Location

Beaumont Hospital

Dublin, Ireland

Location

Children's Health Ireland at Crumlin

Dublin, Ireland

Location

St. Vincent's University Hospital

Dublin, Ireland

Location

University Hospital Limerick (Adults)

Limerick, Ireland

Location

Azienda Ospedaliero Universitaria Ospedale Riuniti

Ancona, Italy

Location

IRCCS Istituto Giannina Gaslini-Ospedale Pediatrico

Genova, Italy

Location

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico

Milan, Italy

Location

Ospedale Pediatrico Bambino Gesu

Rome, Italy

Location

Azienda Ospedaliera di Verona-Ospedale Civile Maggiore

Verona, Italy

Location

Academic Medical Center

Amsterdam, Netherlands

Location

University Medical Center, Utrecht, Department of Pulmonology and Tuberculosis

Heidelberglaan, Netherlands

Location

Hospital Universitari Vall d´Hebron Servicio de Broncoscopia

Barcelona, Spain

Location

Hospital Virgen de la Arrixaca

Murcia, Spain

Location

Hospital Universitario Virgen del Rocio

Seville, Spain

Location

Hospital Universitario y Politecnico La Fe

Valencia, Spain

Location

Papworth Hospital NHS Foundation Trust, Papworth Everard

Cambridge, United Kingdom

Location

Royal Devon and Exeter NHS Foundation Trust, Royal Devon and Exeter Hospital

Exeter, United Kingdom

Location

Clinical Research Facility, Queen Elizabeth University Hospital

Glasgow, United Kingdom

Location

St. James University Hospital

Leeds, United Kingdom

Location

Liverpool Heart and Chest Hospital

Liverpool, United Kingdom

Location

Royal Brompton & Harefield NHS Foundation Trust, Royal Brompton Hospital

London, United Kingdom

Location

Wythenshawe Hospital

Manchester, United Kingdom

Location

Southampton General Hospital

Southampton, United Kingdom

Location

Related Publications (2)

  • Heneghan M, Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2023 Nov 20;11(11):CD010966. doi: 10.1002/14651858.CD010966.pub4.

  • Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2020 Dec 17;12(12):CD010966. doi: 10.1002/14651858.CD010966.pub3.

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

elexacaftor, ivacaftor, tezacaftor drug combinationivacaftor

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR
Expanded Access
Yes

Study Record Dates

First Submitted

August 14, 2019

First Posted

August 15, 2019

Study Start

December 5, 2019

Primary Completion

December 16, 2022

Study Completion

December 16, 2022

Last Updated

January 16, 2024

Results First Posted

January 16, 2024

Record last verified: 2023-12

Data Sharing

IPD Sharing
Will not share

Details on Vertex data sharing criteria and process for requesting access can be found at: https://www.vrtx.com/independent research/clinical-trial-data-sharing.

Locations