NCT06128629

Brief Summary

To evaluate the efficacy and safety of a single dose of NTLA-2001 compared to placebo in participants with ATTR-CM.

Trial Health

88
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
1,200

participants targeted

Target at P75+ for phase_3

Timeline
23mo left

Started Dec 2023

Typical duration for phase_3

Geographic Reach
25 countries

130 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress56%
Dec 2023Apr 2028

First Submitted

Initial submission to the registry

November 8, 2023

Completed
5 days until next milestone

First Posted

Study publicly available on registry

November 13, 2023

Completed
1 month until next milestone

Study Start

First participant enrolled

December 13, 2023

Completed
4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 1, 2027

Expected
4 months until next milestone

Study Completion

Last participant's last visit for all outcomes

April 1, 2028

Last Updated

March 27, 2026

Status Verified

March 1, 2026

Enrollment Period

4 years

First QC Date

November 8, 2023

Last Update Submit

March 23, 2026

Conditions

Keywords

TTRAmyloidosisCardiomyopathyNTLA-2001ATTR-CMTransthyretinATTRTTR-mediated amyloidosisAmyloidosis, HereditaryAmyloidosis, Hereditary, Transthyretin-Related AmyloidosisTransthyretin amyloid cardiomyopathyTTR cardiomyopathyWild-type TTRV122IAmyloidosis, Wild TypeCRISPR/Cas9

Outcome Measures

Primary Outcomes (1)

  • Composite outcome of cardiovascular (CV) mortality and CV events

    Maximum study duration is dependent on event rates and is estimated to be at least 18 months and up to approximately 5 years

Secondary Outcomes (2)

  • Change in baseline to month 18 in serum TTR

    Baseline, Month 18

  • Change from baseline to month 18 in KCCQ-OS score

    Baseline, Month 18

Study Arms (2)

NTLA-2001

EXPERIMENTAL

Single intravenous (IV) infusion of NTLA-2001

Biological: NTLA-2001

Placebo

PLACEBO COMPARATOR

Single IV infusion of normal saline

Drug: Placebo

Interventions

NTLA-2001BIOLOGICAL

NTLA-2001 (55mg) by IV infusion

NTLA-2001

Normal saline (0.9% NaCl) by IV infusion

Placebo

Eligibility Criteria

Age18 Years - 90 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Documented diagnosis of ATTR amyloidosis with cardiomyopathy
  • Medical history of heart failure (HF)
  • Symptoms of HF are optimally managed and clinically stable within 28 days prior to administration of study intervention
  • Screening NT-proBNP, a blood marker of HF severity, greater than or equal to 600 pg/mL and less than 10,000 pg/mL

You may not qualify if:

  • New York Heart Association (NYHA) Class IV HF
  • Polyneuropathy Disability score of IV (confined to wheelchair or bed)
  • Has hepatitis B, hepatitis C or human immunodeficiency virus (HIV) infection
  • History of active malignancy within 3 years prior to screening
  • RNA silencer therapy (patisiran, inotersen and/or eplontersen) within 12 months prior to dosing. Any prior vutrisiran use is not allowed
  • Initiation of tafamidis or acoramidis within 56 days prior to study dosing
  • Estimated glomerular filtration rate (eGFR) \<30 mL/min/1.73m\^2
  • History of liver disease
  • Uncontrolled blood pressure
  • Unable or unwilling to take vitamin A supplementation for the duration of the study

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (132)

University of Arizona

Tucson, Arizona, 85724, United States

RECRUITING

Cedars-Sinai Medical Center

Los Angeles, California, 90048, United States

RECRUITING

Western Greater Los Angeles VA Medical Center

Los Angeles, California, 90073, United States

RECRUITING

Stanford University

Palo Alto, California, 94305, United States

RECRUITING

University of California, San Diego (UCSD) - Medical Center

San Diego, California, 92103, United States

RECRUITING

University of Colorado Denver

Denver, Colorado, 80045, United States

RECRUITING

Yale University School of Medicine

New Haven, Connecticut, 06510, United States

RECRUITING

MedStar Washington Hospital Center - MedStar Heart and Vascular Institute

Washington D.C., District of Columbia, 20010, United States

RECRUITING

Mayo Clinic - Jacksonville

Jacksonville, Florida, 32224, United States

RECRUITING

Cleveland Clinic of Florida

Weston, Florida, 33331, United States

RECRUITING

Emory University School of Medicine

Atlanta, Georgia, 30322, United States

RECRUITING

Northwestern University

Chicago, Illinois, 60611, United States

RECRUITING

Indiana University Health

Indianapolis, Indiana, 46202, United States

RECRUITING

University of Kentucky Gill Heart Institute

Lexington, Kentucky, 40536, United States

RECRUITING

Johns Hopkins University

Baltimore, Maryland, 21287, United States

RECRUITING

Brigham and Women's Hospital

Boston, Massachusetts, 02115, United States

RECRUITING

Boston University School of Medicine

Boston, Massachusetts, 02118, United States

RECRUITING

University of Michigan

Ann Arbor, Michigan, 48109, United States

RECRUITING

Barbara Ann Karmanos Cancer Institute

Detroit, Michigan, 48201, United States

WITHDRAWN

Mayo Clinic

Rochester, Minnesota, 55905, United States

RECRUITING

St. Luke's Hospital

Kansas City, Missouri, 64111, United States

RECRUITING

New York University (NYU) School of Medicine - Langone Medical Center

New York, New York, 10016, United States

RECRUITING

Columbia University Medical Center

New York, New York, 10032, United States

RECRUITING

Duke University Medical Center

Durham, North Carolina, 27710, United States

RECRUITING

Cleveland Clinic

Cleveland, Ohio, 44195, United States

RECRUITING

Ohio Health Research Institute

Columbus, Ohio, 43214, United States

RECRUITING

Oregon Health and Science University (OHSU)

Portland, Oregon, 97239, United States

RECRUITING

Penn Presbyterian Medical Center

Philadelphia, Pennsylvania, 19104, United States

RECRUITING

Allegheny General Hospital

Pittsburgh, Pennsylvania, 15212, United States

RECRUITING

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, 15219, United States

RECRUITING

Medical University of South Carolina

Charleston, South Carolina, 29425, United States

RECRUITING

Baylor Scott & White Research Institute

Dallas, Texas, 75201, United States

RECRUITING

University of Texas Southwestern Medical Center

Dallas, Texas, 75390, United States

RECRUITING

Baylor College of Medicine

Houston, Texas, 77030, United States

RECRUITING

Houston Methodist Hospital

Houston, Texas, 77030, United States

RECRUITING

Baylor Scott and White - The Heart Hospital Baylor Plano

Plano, Texas, 75093, United States

RECRUITING

INOVA Fairfax Hospital

Falls Church, Virginia, 22042, United States

RECRUITING

Virginia Commonwealth University - Department of Internal Medicine

Richmond, Virginia, 23298, United States

RECRUITING

Fundacion Favalro

Buenos Aires, Argentina

RECRUITING

Hospital Italiano de Buenos Aires

Buenos Aires, Argentina

RECRUITING

ICBA

Buenos Aires, Argentina

RECRUITING

Fundacion Favaloro

Ciudad Autonoma de Buenos Aire, Argentina

RECRUITING

Hospital Italiano de Buenos Aires

Ciudad Autonoma de Buenos Aire, Argentina

RECRUITING

Hospital Privado de Rosario

Rosario, Argentina

RECRUITING

The Canberra Hospital

Garran, Australian Capital Territory, Australia

RECRUITING

Westmead Hospital

Westmead, New South Wales, Australia

RECRUITING

Cairns Hospital

Cairns, Queensland, Australia

WITHDRAWN

Eastern Health - Box Hill Hospital

Box Hill, Victoria, Australia

RECRUITING

Fiona Stanley Hospital

Perth, Western Australia, Australia

RECRUITING

Royal Adelaide Hospital

Adelaide, Australia

RECRUITING

The Alfred Hospital

Melbourne, Australia

RECRUITING

Princess Alexandra Hospital

Woolloongabba, Australia

RECRUITING

Medizinische Universitaet Innsbruck

Innsbruck, Austria

RECRUITING

Universitaesklinikum St. Poelten

Sankt Pölten, Austria

RECRUITING

AZ Sint-Jan Brugge

Bruges, Belgium

RECRUITING

Universite Libre de Bruxelles (ULB) - Hopital Erasme

Brussels, Belgium

RECRUITING

Antwerp University Hospital

Edegem, Belgium

RECRUITING

UZ Leuven

Leuven, Belgium

RECRUITING

Centre Hospitalier Regional de la Citadelle

Liège, Belgium

RECRUITING

Centro de Pesquisa NUPEC - Instituto Orizonti em Belo Horizonte

Belo Horizonte, Brazil

RECRUITING

Complexo Hospitalar de Niterói (CHN-DASA)

Niterói, Brazil

RECRUITING

CAPED - Centro Avancado de Pesquisa

Ribeirão Preto, Brazil

RECRUITING

HCFMRP - Hospital das Clinicas da Faculdade de Medicina de Ribeirao Preto

Ribeirão Preto, Brazil

RECRUITING

Cardiopulmonar da Bahia S. A. (Hospital Cardio Pulmonar)

Salvador, Brazil

RECRUITING

Hospital Israelita Albert Einstein

São Paulo, Brazil

RECRUITING

Instituto Dante Pazzanese de Cardiologia

São Paulo, Brazil

RECRUITING

Instituto do Coracao (InCor) do Hospital das Clinicas da FMUSP

São Paulo, Brazil

RECRUITING

PSEG Centro de Pesquisa Clinica S.A.

São Paulo, Brazil

RECRUITING

Alberta Health Services - University of Calgary

Calgary, Alberta, Canada

RECRUITING

Vancouver Coastal Health Research Institute

Vancouver, British Columbia, Canada

RECRUITING

University Health Network - Toronto General Hospital

Toronto, Ontario, Canada

RECRUITING

McGill University Health Centre

Montreal, Quebec, Canada

RECRUITING

Fakultni nemocnice u sv. Anny v Brne

Brno, Czechia

RECRUITING

Aarhus University Hospital

Aarhus, Denmark

RECRUITING

Rigshospitalet

Copenhagen, Denmark

RECRUITING

AP-HP Hopital Henri Mondor

Créteil, France

RECRUITING

AP-HM - Hopital de la Timone

Marseille, France

RECRUITING

AP-HP Hopital Bichat - Claude Bernard

Paris, France

RECRUITING

CHU Rennes - Hopital Pontchaillou

Rennes, France

RECRUITING

CHU de Toulouse - Hopital Rangueil

Toulouse, France

RECRUITING

Charite Universitaetsmedizin Berlin

Berlin, Germany

RECRUITING

Universitaetsklinikum Essen

Essen, Germany

RECRUITING

Universitaetsklinikum Heidelberg

Heidelberg, Germany

RECRUITING

Universitaetsklinikum Wuerzburg

Würzburg, Germany

RECRUITING

Semmelweis Egyetem Belgyogyaszati es Hematologiai Klinika

Budapest, Hungary

RECRUITING

Rambam Health Care Campus

Haifa, Israel

RECRUITING

Hadassah University Hospital, Ein Karem

Jerusalem, Israel

RECRUITING

Sheba Medical Center

Tel Litwinsky, Israel

RECRUITING

IRCCS Azienda Ospedaliero-Universitaria di Bologna - Policlinico di Sant'Orsola

Bologna, Italy

RECRUITING

Azienda Ospedaliero-Universitaria di Ferrara-Arcispedale Sant'Anna

Cona, Italy

RECRUITING

Azienda Ospedaliero-Universitaria Careggi

Florence, Italy

RECRUITING

Ospedale Policlinico San Martino IRCCS

Genova, Italy

RECRUITING

Fondazione IRCCS Policlinico San Matteo

Pavia, Italy

RECRUITING

Fondazione Toscana Gabriele Monasterio per la Ricerca Medica

Pisa, Italy

RECRUITING

Azienda sanitaria universitaria Giuliano Isontina (ASU GI) - Ospedale di Cattinara

Trieste, Italy

RECRUITING

Kumamoto University Hospital

Kumamoto, Japan

RECRUITING

National Cerebral and Cardiovascular Center

Osaka, Japan

RECRUITING

The University of Tokyo Hospital

Tokyo, Japan

RECRUITING

Toyama University Hospital

Toyama, Japan

RECRUITING

Instituto Nacional de Ciencias Medicas y Nutricion Salvador Zubiran

Mexico City, Mexico

RECRUITING

University Medical Center

Groningen, Netherlands

RECRUITING

Erasmus MC

Rotterdam, Netherlands

RECRUITING

Universitair Medisch Centrum Utrecht

Utrecht, Netherlands

RECRUITING

New Zealand Clinical Research

Auckland, New Zealand

RECRUITING

New Zealand Clinical Research

Christchurch, New Zealand

RECRUITING

Oslo University Hospital - Rikshospitalet

Oslo, Norway

RECRUITING

Centro Hospitalar Universitario de Lisboa Norte

Lisbon, Portugal

RECRUITING

Centro Hospitalar Universitario do Porto

Porto, Portugal

RECRUITING

National Heart Centre

Singapore, Singapore

RECRUITING

National University Hospital

Singapore, Singapore

RECRUITING

Chonnam National University Hospital

Gwangju, South Korea

WITHDRAWN

Samsung Medical Center

Seoul, South Korea

WITHDRAWN

Seoul National University Hospital

Seoul, South Korea

WITHDRAWN

Severance Hospital, Yonsei University Health System

Seoul, South Korea

WITHDRAWN

Hospital Universitario de A Coruna

A Coruña, Spain

RECRUITING

Hospital Universitari de Bellvitge

Barcelona, Spain

RECRUITING

Hospital Universitario Vall d'Hebron

Barcelona, Spain

RECRUITING

Hospital Universitario Puerta de Hierro

Majadahonda, Spain

RECRUITING

Hospital Universitario Virgen de la Victoria

Málaga, Spain

RECRUITING

Hospital Universitario Son Llatzer

Palma de Mallorca, Spain

RECRUITING

Karolinska University Hospital

Stockholm, Sweden

RECRUITING

University Hospital of Umea

Umeå, Sweden

RECRUITING

Far Eastern Memorial Hospital

New Taipei City, Taiwan

RECRUITING

National Taiwan University Hospital

Taipei, Taiwan

RECRUITING

Taipai Veterans General Hospital

Taipei, Taiwan

RECRUITING

Synexus Midlands Clinical Research Centre

Birmingham, United Kingdom

ACTIVE NOT RECRUITING

Synexus Wales Clinical Research Centre

Cardiff, United Kingdom

ACTIVE NOT RECRUITING

Synexus Scotland Clinical Research Centre

Glasgow, United Kingdom

ACTIVE NOT RECRUITING

Synexus Hexham Clinical Research Centre

Hexham, United Kingdom

ACTIVE NOT RECRUITING

Synexus Merseyside Clinical Research Centre

Liverpool, United Kingdom

ACTIVE NOT RECRUITING

Richmond Pharmacology

London, United Kingdom

RECRUITING

Synexus Manchester Clinical Research Centre

Manchester, United Kingdom

ACTIVE NOT RECRUITING

MeSH Terms

Conditions

Amyloidosis, Hereditary, Transthyretin-RelatedAmyloidosisCardiomyopathiesAmyloidosis, Familial

Interventions

NTLA-2001

Condition Hierarchy (Ancestors)

Proteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic DiseasesHeart DiseasesCardiovascular DiseasesMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Central Study Contacts

Trial Manager at Intellia

CONTACT

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Model Details: Participants will be randomized in a 2:1 ratio to NTLA-2001 or placebo
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 8, 2023

First Posted

November 13, 2023

Study Start

December 13, 2023

Primary Completion (Estimated)

December 1, 2027

Study Completion (Estimated)

April 1, 2028

Last Updated

March 27, 2026

Record last verified: 2026-03

Data Sharing

IPD Sharing
Will not share

Locations