NCT06183931

Brief Summary

The primary objective of this study is to access the efficacy of ALXN2220 in the treatment of adult participants with ATTR-CM by evaluating the difference between the ALXN2220 and placebo groups as assessed by the total occurrences of all-cause mortality (ACM) and cardiovascular (CV) clinical events.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
1,181

participants targeted

Target at P75+ for phase_3

Timeline
15mo left

Started Jan 2024

Typical duration for phase_3

Geographic Reach
26 countries

207 active sites

Status
active not recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress65%
Jan 2024Oct 2027

First Submitted

Initial submission to the registry

November 15, 2023

Completed
1 month until next milestone

First Posted

Study publicly available on registry

December 28, 2023

Completed
14 days until next milestone

Study Start

First participant enrolled

January 11, 2024

Completed
3.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 7, 2027

Expected
4 months until next milestone

Study Completion

Last participant's last visit for all outcomes

October 5, 2027

Last Updated

February 23, 2026

Status Verified

February 1, 2026

Enrollment Period

3.4 years

First QC Date

November 15, 2023

Last Update Submit

February 20, 2026

Conditions

Keywords

Amyloid DepleterALXN2220All-cause mortality (ACM)Cardiovascular (CV)Transthyretin Amyloid CardiomyopathyTransthyretin amyloid (ATTR)Transthyretin (TTR)N-terminal pro b-type natriuretic peptide (NT-proBNP)NT-proBNPAmyloidosisATTR-CM

Outcome Measures

Primary Outcomes (1)

  • Total Occurrence of ACM and CV clinical events during the Blinded Treatment Period

    Baseline up to the end study (up to Month 48)

Secondary Outcomes (5)

  • Change From Baseline in Kansas City Cardiomyopathy Questionnaire-Overall Score (KCCQ-OS) at Month 24

    Baseline, Month 24

  • Time to CV-related Mortality

    Baseline up to the end of study (up to Month 48)

  • Change from Baseline in Six-minute Walk Test (6MWT) at Month 24

    Baseline, Month 24

  • Total Occurrences of CV Clinical Events

    Baseline up to the end of study (up to Month 48)

  • Time to ACM

    Baseline up to the end of study (up to Month 48)

Study Arms (2)

ALXN2220

EXPERIMENTAL

Participants will receive weight-based dose of ALXN2220 via intravenous (IV) infusion every 4 weeks (q4w) for at least 24 months up to a maximum of 48 months.

Drug: ALXN2220

Placebo

PLACEBO COMPARATOR

Participants will receive placebo via IV infusion q4w for at least 24 months up to a maximum of 48 months.

Drug: Placebo

Interventions

Participants will receive ALXN2220 via IV infusion.

ALXN2220

Participants will receive placebo via IV infusion.

Placebo

Eligibility Criteria

Age18 Years - 90 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Diagnosis of ATTR-CM with either wild-type or variant TTR genotype
  • End-diastolic interventricular septal wall thickness ≥ 12 mm on echocardiography measured at Screening
  • NT-proBNP \> 2000 pg/mL at Screening
  • Treatment with a loop diuretic for at least 30 days prior to Screening
  • History of heart failure NYHA Class II-IV at Screening
  • Life expectancy of ≥ 6 months as per the Investigator's judgment
  • Males and females of childbearing ability must use contraception

You may not qualify if:

  • Known leptomeningeal amyloidosis
  • Known light chain (AL) or secondary amyloidosis (AA), or any other form of systemic amyloidosis
  • Acute coronary syndrome, unstable angina, stroke, transient ischemic attack, coronary revascularization, cardiac device implantation, cardiac valve repair, or major surgery within 3 months of Screening
  • Uncontrolled clinically significant cardiac arrhythmia, per Investigator's assessment
  • LVEF \< 30% on echocardiography
  • Renal failure requiring dialysis or an eGFR \< 20 mL/min/1.73 m2 at Screening
  • Polyneuropathy with PND score IV

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (212)

Research Site

Irvine, California, 92614, United States

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La Jolla, California, 92037, United States

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Palo Alto, California, 94304, United States

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San Francisco, California, 94143, United States

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Aurora, Colorado, 80045, United States

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Washington D.C., District of Columbia, 20010, United States

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Jacksonville, Florida, 32224, United States

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Weston, Florida, 33331, United States

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Atlanta, Georgia, 30309, United States

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Atlanta, Georgia, 30322, United States

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Chicago, Illinois, 60611, United States

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Indianapolis, Indiana, 46202, United States

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Boston, Massachusetts, 02115, United States

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Boston, Massachusetts, 02118, United States

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Kansas City, Missouri, 64111, United States

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St Louis, Missouri, 63110, United States

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New York, New York, 10016, United States

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New York, New York, 10032, United States

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Stony Brook, New York, 11794, United States

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Chapel Hill, North Carolina, 27599, United States

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Durham, North Carolina, 27705, United States

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Cleveland, Ohio, 44195, United States

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Columbus, Ohio, 43210, United States

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Portland, Oregon, 97239, United States

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Danville, Pennsylvania, 17822, United States

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Philadelphia, Pennsylvania, 19104, United States

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Charleston, South Carolina, 29425, United States

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Greenville, South Carolina, 29605, United States

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Memphis, Tennessee, 38120, United States

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Fort Worth, Texas, 76104, United States

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Houston, Texas, 77030, United States

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Salt Lake City, Utah, 84132, United States

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Falls Church, Virginia, 22042, United States

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Richmond, Virginia, 23298, United States

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Seattle, Washington, 98195, United States

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Madison, Wisconsin, 53705, United States

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Buenos Aires, 1425, Argentina

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CABA, C1025ABI, Argentina

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Ciudad de Buenos Aires, C1181ACH, Argentina

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Ciudad de Buenos Aires, C1428, Argentina

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Córdoba, X5016KEH, Argentina

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Bedford Park, 5042, Australia

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Box Hill, 3128, Australia

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Brisbane, 4102, Australia

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Darlinghurst, 2010, Australia

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Joondalup, 6027, Australia

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Melbourne, 3004, Australia

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Westmead, 2145, Australia

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Graz, 8036, Austria

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Innsbruck, 6020, Austria

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Vienna, 1090, Austria

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Vienna, 1160, Austria

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Wels, 4600, Austria

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Bruges, 8000, Belgium

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Brussels, 1070, Belgium

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Genk, 3600, Belgium

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Aracaju, 49015-380, Brazil

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Campinas, 13083, Brazil

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Fortaleza, 60430-375, Brazil

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Porto Alegre, 90560-030, Brazil

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Ribeirão Preto, 14026-020, Brazil

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Ribeirão Preto, 14051-140, Brazil

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Rio de Janeiro, 20551-030, Brazil

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Rio de Janeiro, 22270-005, Brazil

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São Paulo, 01323-001, Brazil

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São Paulo, 04012-909, Brazil

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São Paulo, 05403-000, Brazil

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São Paulo, 05652-900, Brazil

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Calgary, Alberta, T2N 1N4, Canada

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Winnipeg, Manitoba, R2H 2A6, Canada

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London, Ontario, N6C 2R5, Canada

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Toronto, Ontario, M5G 2C4, Canada

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Chicoutimi, Quebec, G7H 5H6, Canada

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Montreal, Quebec, H1T 1C8, Canada

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Montreal, Quebec, H2X 1R9, Canada

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Rimouski, Quebec, G5L 5T1, Canada

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Beijing, 100034, China

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Beijing, 100037, China

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Beijing, 100191, China

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Beijing, 100730, China

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Changsha, 430033, China

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Chengdu, 610000, China

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Chengdu, 610072, China

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Chongqing, 400042, China

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Fuzhou, 350005, China

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Guangzhou, 510080, China

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Guiyang, 550044, China

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Hangzhou, 310003, China

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Hangzhou, 310009, China

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Harbin, 150080, China

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Hefei, 230001, China

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Jinan, 250021, China

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Nanjing, 210029, China

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Shanghai, 201114, China

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Tianjin, 300457, China

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Wuhan, 430030, China

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Xi'an, 710061, China

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Prague, 128 08, Czechia

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Prague, 140 00, Czechia

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Aarhus, 8200, Denmark

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Odense C, 5000, Denmark

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Bron, 69677, France

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Chambray-lès-Tours, 37170, France

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Créteil, 94010, France

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Marseille, 13005, France

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Montpellier, 34295, France

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Paris, 75018, France

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Paris, 75651, France

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Pessac, 33604, France

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Poitiers, 86021, France

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Rennes, 35033, France

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Saint-Herblain, 44093, France

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Toulouse, 31059, France

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Berlin, 10117, Germany

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Cologne, 50937, Germany

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Essen, 45147, Germany

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Giessen, 35392, Germany

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Hamburg, 22767, Germany

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Hanover, 30625, Germany

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Heidelberg, 69120, Germany

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Homburg, 66421, Germany

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Kiel, 24105, Germany

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Leipzig, 04103, Germany

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München, 81377, Germany

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Münster, 48149, Germany

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Würzburg, 97078, Germany

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Athens, 11528, Greece

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Dublin, 8, Ireland

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Beer Yaakov, 70300, Israel

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Haifa, 31096, Israel

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Haifa, 34362, Israel

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Jerusalem, 91120, Israel

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Jerusalem, 9372212, Israel

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Petah Tikva, 4941492, Israel

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Rehovot, 76100, Israel

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Bologna, 40138, Italy

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Ferrara, 44124, Italy

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Florence, 50134, Italy

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Forlì, 47121, Italy

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Messina, 98124, Italy

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Milan, 20122, Italy

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Naples, 80131, Italy

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Padua, 35128, Italy

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Pavia, 27100, Italy

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Pisa, 56124, Italy

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Roma, 00189, Italy

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Torino, 10154, Italy

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Trieste, 34128, Italy

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Bunkyō City, 113-8431, Japan

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Kumamoto, 860-8556, Japan

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Kurume-shi, 830-0011, Japan

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Kyoto, 602-8566, Japan

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Matsumoto-shi, 390-8621, Japan

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Sapporo, 060-8543, Japan

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Shinjuku-ku, 160-8582, Japan

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Suita-shi, 564-8565, Japan

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Groningen, 9713 GZ, Netherlands

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Maastricht, 6229 HX, Netherlands

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Rotterdam, 3015 GD, Netherlands

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Utrecht, 3584 CX, Netherlands

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Lørenskog, N-1478, Norway

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Oslo, 0372, Norway

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Trondheim, 7030, Norway

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Gdansk, 80-952, Poland

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Poznan, 61-848, Poland

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Warsaw, 02-097, Poland

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Busan, 49241, South Korea

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Seoul, 03080, South Korea

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Seoul, 03722, South Korea

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Seoul, 06351, South Korea

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Seoul, 06591, South Korea

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Seoul, 5505, South Korea

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Wŏnju, 26426, South Korea

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A Coruña, 15009, Spain

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Barcelona, 8035, Spain

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El Palmar, 30120, Spain

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Jaén, 23007, Spain

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L'Hospitalet de Llobregat, 08907, Spain

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Madrid, 28027, Spain

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Majadahonda, 28222, Spain

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Málaga, 29010, Spain

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Palma de Mallorca, 07198, Spain

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Pamplona, 31008, Spain

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Salamanca, 37007, Spain

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Santiago de Compostela-Coruña, 15706, Spain

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Valencia, 46010, Spain

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Gothenburg, 413 45, Sweden

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Lund, 22242, Sweden

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Skellefteå, 93186, Sweden

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Stockholm, 171 64, Sweden

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Basel, 4031, Switzerland

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Bern, 3010, Switzerland

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Lucerne, 6000, Switzerland

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Sankt Gallen, 9007, Switzerland

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Zurich, 8091, Switzerland

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New Taipei City, 220, Taiwan

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Taichung, 404, Taiwan

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Taichung, 40705, Taiwan

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Taipei, 10002, Taiwan

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Taipei, 11217, Taiwan

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Ankara, 06230, Turkey (Türkiye)

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Dinar, 03400, Turkey (Türkiye)

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Eskişehir, 26480, Turkey (Türkiye)

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Istanbul, 34303, Turkey (Türkiye)

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Mersin, 33079, Turkey (Türkiye)

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Birmingham, B15 2SQ, United Kingdom

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Cardiff, CF15 9SS, United Kingdom

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Glasgow, G20 0SP, United Kingdom

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Hexham, NE46 1QJ, United Kingdom

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London, NW3 2QG, United Kingdom

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London, SE1 1YR, United Kingdom

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Manchester, M15 6SE, United Kingdom

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MeSH Terms

Conditions

Amyloidosis

Condition Hierarchy (Ancestors)

Proteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 15, 2023

First Posted

December 28, 2023

Study Start

January 11, 2024

Primary Completion (Estimated)

June 7, 2027

Study Completion (Estimated)

October 5, 2027

Last Updated

February 23, 2026

Record last verified: 2026-02

Data Sharing

IPD Sharing
Will share

Alexion has a public commitment to allow requests for access to study data and will be supplying a protocol, CSR, and plain language summaries.

Shared Documents
STUDY PROTOCOL, SAP, CSR

Locations