NCT05050136

Brief Summary

The purpose of this clinical research study is to learn more about the use of the study medicine, volixibat, for the treatment of pruritus (itching) associated with Primary Biliary Cholangitis (PBC), and to assess the possible impact on the disease progression of PBC.

Trial Health

88
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
260

participants targeted

Target at P75+ for phase_2

Timeline
14mo left

Started Sep 2021

Longer than P75 for phase_2

Geographic Reach
15 countries

130 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress80%
Sep 2021Jul 2027

First Submitted

Initial submission to the registry

September 9, 2021

Completed
11 days until next milestone

First Posted

Study publicly available on registry

September 20, 2021

Completed
2 days until next milestone

Study Start

First participant enrolled

September 22, 2021

Completed
5.5 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 1, 2027

Expected
3 months until next milestone

Study Completion

Last participant's last visit for all outcomes

July 1, 2027

Last Updated

May 4, 2026

Status Verified

April 1, 2026

Enrollment Period

5.5 years

First QC Date

September 9, 2021

Last Update Submit

April 30, 2026

Conditions

Keywords

PruritusPBCItchingCholangitisPrimary Biliary CholangitisHepatobiliary disorders

Outcome Measures

Primary Outcomes (1)

  • Mean change in the daily itch scores using the Adult Itch Reported Outcome (Adult ItchRO) questionnaire

    The Adult ItchRO is an 11-point NRS measurement of itch severity ranging from 0=no itch to 10=worst possible itch.

    Baseline to week 28

Secondary Outcomes (8)

  • Proportion of participants with itch response using the Adult ItchRO

    Baseline to week 28

  • Incidence of adverse events

    Baseline to week 28

  • Changes in alkaline phosphatase

    Baseline to week 28

  • Changes in total bilirubin

    Baseline to week 28

  • Changes in serum bile acid levels

    Baseline to week 28

  • +3 more secondary outcomes

Study Arms (5)

Part 1 Arm 1: Volixibat 20mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 20mg twice daily.

Drug: Volixibat

Part 1 Arm 2: Volixibat 80mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 80mg twice daily.

Drug: Volixibat

Part 1 Arm 3: Placebo

PLACEBO COMPARATOR

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Drug: Placebo

Part 2 Arm 1: Volixibat Selected Dose 20mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 20mg twice daily.

Drug: Volixibat

Part 2 Arm 2: Placebo

PLACEBO COMPARATOR

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Drug: Placebo

Interventions

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Also known as: SHP626
Part 1 Arm 1: Volixibat 20mgPart 1 Arm 2: Volixibat 80mgPart 2 Arm 1: Volixibat Selected Dose 20mg

Capsules matched to study drug without the active pharmaceutical ingredient

Part 1 Arm 3: PlaceboPart 2 Arm 2: Placebo

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Provide signed informed consent at the screening visit as well as comply with all study visits and requirements through the end of the study
  • Male or female, age ≥18 years at the screening visit
  • Confirmed diagnosis of PBC in line with the AASLD guidelines
  • UDCA, anti-pruritic medication and PPAR agonist use will be allowed if meeting additional criteria
  • Qualified pruritus associated with PBC as assessed by Adult ItchRO

You may not qualify if:

  • Pruritus associated with an etiology other than PBC
  • Evidence or clinical suspicion of decompensated cirrhosis or a history of decompensation events
  • Current symptomatic cholelithiasis or inflammatory gallbladder disease
  • History of small bowel surgery/resection impacting the terminal ileum that may disrupt the enterohepatic circulation.
  • Evidence, history, or suspicion of other liver diseases; PBC patients with AIH are not excluded
  • History of Liver transplantation

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (130)

Southern California Research Center

Coronado, California, 92218, United States

TERMINATED

Cedars Sinai Medical Center

Los Angeles, California, 90048, United States

ACTIVE NOT RECRUITING

University of California Los Angeles

Los Angeles, California, 90095, United States

ACTIVE NOT RECRUITING

UC Davis

Sacramento, California, 95817, United States

ACTIVE NOT RECRUITING

University of Colorado

Aurora, Colorado, 80045, United States

ACTIVE NOT RECRUITING

Yale University Digestive Diseases

New Haven, Connecticut, 06510, United States

ACTIVE NOT RECRUITING

Covenant Metabolic Specialists

Fort Myers, Florida, 33912, United States

TERMINATED

UF Hepatology Research at CTRB

Gainesville, Florida, 32610, United States

ACTIVE NOT RECRUITING

UF Health Gastroenterology- Emerson

Jacksonville, Florida, 32209, United States

TERMINATED

IHS Health

Kissimmee, Florida, 34741, United States

TERMINATED

Schiff Center for Liver Diseases

Miami, Florida, 33136, United States

TERMINATED

Advanced Research Institute, Inc

New Port Richey, Florida, 34653, United States

ACTIVE NOT RECRUITING

Covenant Research and Clinics, LLC

Sarasota, Florida, 34240, United States

TERMINATED

Tampa General Hospital

Tampa, Florida, 33606, United States

ACTIVE NOT RECRUITING

Cleveland Clinic Florida

Weston, Florida, 33331, United States

ACTIVE NOT RECRUITING

Southeast Clinical Research Center

Dalton, Georgia, 30720, United States

TERMINATED

Northwestern University

Chicago, Illinois, 60611, United States

TERMINATED

Loyola University Health System - Loyola Outpatient Center

Maywood, Illinois, 60153, United States

ACTIVE NOT RECRUITING

University of Iowa Hospitals & Clinics

Iowa City, Iowa, 52242, United States

ACTIVE NOT RECRUITING

Ochsner Clinic Foundation-Baton Rouge

Baton Rouge, Louisiana, 70836, United States

ACTIVE NOT RECRUITING

LSU Health Science Center Shreveport

Shreveport, Louisiana, 71103, United States

ACTIVE NOT RECRUITING

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

ACTIVE NOT RECRUITING

Beth Israel Deaconess

Boston, Massachusetts, 02215, United States

ACTIVE NOT RECRUITING

Mayo Clinic

Rochester, Minnesota, 55905, United States

ACTIVE NOT RECRUITING

Jackson Liver and GI Specialists

Jackson, Mississippi, 39216, United States

TERMINATED

CHI Health Clinic (Alegent Creighton Clinic)- Gastroenterology-Bergan

Omaha, Nebraska, 68124, United States

ACTIVE NOT RECRUITING

Virtua Center for Liver Disease-Camden

Camden, New Jersey, 08103, United States

ACTIVE NOT RECRUITING

Montefiore Medical Center

The Bronx, New York, 10467, United States

ACTIVE NOT RECRUITING

Science 37, Inc (Remote-homebased Telemedicine)

Morrisville, North Carolina, 27560, United States

ACTIVE NOT RECRUITING

Cleveland Clinic - Main Campus

Cleveland, Ohio, 44195, United States

ACTIVE NOT RECRUITING

Einstein Healthcare Network - Einstein Medical Center

Philadelphia, Pennsylvania, 19141, United States

ACTIVE NOT RECRUITING

Methodist Le Bonheur Healthcare

Memphis, Tennessee, 38104, United States

TERMINATED

Galen Medical Group, P.C

Tennessee City, Tennessee, 37343, United States

ACTIVE NOT RECRUITING

Amel Med LLC

Austin, Texas, 78750, United States

TERMINATED

The Liver Institute at Methodist Dallas Medical Center

Dallas, Texas, 75203, United States

ACTIVE NOT RECRUITING

Soma Clinical Trials

Denison, Texas, 75020, United States

TERMINATED

Baylor College of Medicine

Houston, Texas, 77030, United States

ACTIVE NOT RECRUITING

Liver Associates of Texas

Houston, Texas, 77030, United States

ACTIVE NOT RECRUITING

Impact Research

Waco, Texas, 76710, United States

TERMINATED

University of Utah Health Care

Salt Lake City, Utah, 84132, United States

ACTIVE NOT RECRUITING

MedStar Health Research Institute

Fairfax, Virginia, 22031, United States

ACTIVE NOT RECRUITING

Bon Secours Liver Institute of Hampton Roads Mary Immaculate Hospital

Newport News, Virginia, 23602, United States

TERMINATED

Bon Secours Richmond Community Hospital LLC d/b/a Bon Secours Liver Institute of Richmond

Richmond, Virginia, 23226, United States

ACTIVE NOT RECRUITING

Liver Institute Northwest

Seattle, Washington, 98105, United States

ACTIVE NOT RECRUITING

Hospital de Alta Complejidad En Red El Cruce

San Juan Bautista, Buenos Aires, 1888, Argentina

ACTIVE NOT RECRUITING

Hospital Provincial Del Centenario

Rosario, Santa Fe Province, 2000, Argentina

ACTIVE NOT RECRUITING

Glenny Corp S.A

CABA, 1430, Argentina

ACTIVE NOT RECRUITING

Clínica de Nefrología, Urología y Enfermedades Cardiovasculares

Santa Fe, 3000, Argentina

ACTIVE NOT RECRUITING

Universitair Ziekenhuis Antwerpe UZA

Antwerp, 2650, Belgium

ACTIVE NOT RECRUITING

Cliniques Universitaires Saint-Luc

Brussels, 1200, Belgium

ACTIVE NOT RECRUITING

UZ Gent

Ghent, 9000, Belgium

ACTIVE NOT RECRUITING

Centro de Pesquisa Clínica da Bahiana Saúde

Salvador, Estado de Bahia, 40290-000, Brazil

ACTIVE NOT RECRUITING

Hospital Das Clínicas Da Ufg

Goiânia, Goiás, 74605-050, Brazil

ACTIVE NOT RECRUITING

Centro de Pesquisas Clínicas do HC/UFMG-EBSERH

Belo Horizonte, Minas Gerais, 30130-100, Brazil

ACTIVE NOT RECRUITING

Hospital de Clínicas de Porto Alegre

Porto Alegre, Rio Grande do Sul, 90035903, Brazil

ACTIVE NOT RECRUITING

Hospital Universitário Clementino Fraga Filho - Secretaria de Hepatologia

Rio de Janeiro, 21941-617, Brazil

ACTIVE NOT RECRUITING

Instituto de Educação, Pesquisa e Gestão em Saúde

Rio de Janeiro, 22775-001, Brazil

ACTIVE NOT RECRUITING

Fundação Oswaldo Ramos

São Paulo, 04038-002, Brazil

ACTIVE NOT RECRUITING

Gordon and Leslie Diamond Health Care Centre, Division of Gastroenterology

Vancouver, British Columbia, V5Z 1M9, Canada

ACTIVE NOT RECRUITING

(G.I.R.I.) GI Research Institute Foundation

Vancouver, British Columbia, V6Z 2K5, Canada

ACTIVE NOT RECRUITING

McMaster University Medical Center

Hamilton, Ontario, L8S 4K1, Canada

ACTIVE NOT RECRUITING

University Hospital, LHSC

London, Ontario, N6A5A5, Canada

ACTIVE NOT RECRUITING

Toronto General Hospital

Toronto, Ontario, M5G 1Z5, Canada

ACTIVE NOT RECRUITING

McGill University Health Centre

Montreal, Quebec, H4A 3J1, Canada

ACTIVE NOT RECRUITING

University of Alberta

Edmonton, T6G 2X8, Canada

ACTIVE NOT RECRUITING

CRCHUM (Centre de Recherche du Centre Hospitalier de l'Université de Montréal)

Montreal, H2X 0A9, Canada

ACTIVE NOT RECRUITING

Mengchao Hepatobiliary Hospital of Fujian Medical University

Fuzhou, Fujian, 350028, China

ACTIVE NOT RECRUITING

Union Hospital Tongji Medical College Huazhong University of Science and Technology

Wuhan, Hubei, 430022, China

ACTIVE NOT RECRUITING

The First Hospital of Jilin University

Changchun, Jilin, 130031, China

ACTIVE NOT RECRUITING

The First Affiliated Hospital, Zhejiang University School of Medicine

Hangzhou, Zhejiang, 310003, China

ACTIVE NOT RECRUITING

Beijing Youan Hospital, Capital Medical University

Beijing, 100069, China

ACTIVE NOT RECRUITING

Beijing Friendship Hospital, Capital Medical University

Beijing, 10050, China

ACTIVE NOT RECRUITING

Sir Run Run Shaw Hospital -Zhejiang University School of Medicine

Hangzhou, 310009, China

ACTIVE NOT RECRUITING

CHU Grenoble - Hôpital MICHALLON

Grenoble, 38043, France

ACTIVE NOT RECRUITING

Hopital Claude Huriez-Digestive system disease clinic

Lille, 59037, France

RECRUITING

CHU de NICE- Hospital L'Archet 2

Nice, 06202, France

ACTIVE NOT RECRUITING

Hospital Saint Antoine

Paris, 75012, France

ACTIVE NOT RECRUITING

Nouvel Hospital Civil

Strasbourg, 67091, France

ACTIVE NOT RECRUITING

Hospital Paul Brousse- APHP

Villejuif, 94800, France

ACTIVE NOT RECRUITING

Klinikum Chemnitz gGmbH

Chemnitz, 09116, Germany

ACTIVE NOT RECRUITING

Universitätsklinikum Frankfurt am Main

Frankfurt, Germany

ACTIVE NOT RECRUITING

Medizinische Hochschule Hannover (MHH)

Hanover, 30625, Germany

ACTIVE NOT RECRUITING

Universitätsklinikum Schleswig-Holstein

Kiel, 24105, Germany

ACTIVE NOT RECRUITING

Universitätsklinikum Leipzig, Klinik und Poliklinik für Onkologie, Gastroenterologie, Hepatologie und Pneumologie

Leipzig, 04103, Germany

ACTIVE NOT RECRUITING

Otto-von-Guericke-Universität Klinik für Gastroenterologie, Hepatologie und Infektiologie Universitätsklinikum Magdeburg A.ö.R.

Magdeburg, 39120, Germany

ACTIVE NOT RECRUITING

University Hospital Munster

Münster, 48149, Germany

ACTIVE NOT RECRUITING

University Hospital Tübingen Medical clinic

Tübingen, 72076, Germany

ACTIVE NOT RECRUITING

St. Josefs-Hospital Wiesbaden

Wiesbaden, 65189, Germany

ACTIVE NOT RECRUITING

Hillel Yaffe Medical Center

Hadera, 3810101, Israel

TERMINATED

Rambam Medical Center

Haifa, 3109601, Israel

ACTIVE NOT RECRUITING

Carmel Medical Center

Haifa, 3434104, Israel

ACTIVE NOT RECRUITING

Shaare Zedek Medical Center

Jerusalem, 9103102, Israel

TERMINATED

Hadassah Medical Center - Ein Karem, Liver Institute Kiryat Hadassah POB 12000

Jerusalem, 9112001, Israel

ACTIVE NOT RECRUITING

Galilee Medical Center

Nahariya, 2210001, Israel

ACTIVE NOT RECRUITING

Rabin Medical Center

Petah Tikva, 4941492, Israel

ACTIVE NOT RECRUITING

Sheba Medical Center

Ramat Gan, 52621, Israel

ACTIVE NOT RECRUITING

The Tel Aviv Sourasky Medical Center

Tel Aviv, 6423906, Israel

TERMINATED

Universita Politecnica delle Marche- Ospedali Riuniti

Ancona, Italy

ACTIVE NOT RECRUITING

ASST Papa Giovanni XXIII

Bergamo, 24127, Italy

ACTIVE NOT RECRUITING

Fondazione Ca Granda

Milan, 20122, Italy

TERMINATED

ASST Grande Ospedale Metropolitano Niguarda

Milan, 20162, Italy

ACTIVE NOT RECRUITING

Azienda Ospedaliero Universitaria Di Modena

Modena, 41126, Italy

ACTIVE NOT RECRUITING

Fondazione IRCCS San Gerardo dei Tintori

Monza, 20900, Italy

ACTIVE NOT RECRUITING

Azienda Ospedale-Università di Padova

Padova, 35128, Italy

ACTIVE NOT RECRUITING

Azienda Ospedaliera Universitaria Policlinico Paolo Giaccone

Palermo, 90127, Italy

ACTIVE NOT RECRUITING

Azienda Ospedaliero Universitaria Pisana (AOUP)

Pisa, 56124, Italy

ACTIVE NOT RECRUITING

Istituto Clinico Humanitas

Rozzano, Italy

ACTIVE NOT RECRUITING

National Hospital Organization Nagasaki Medical Center

Ōmura, Nagasaki, 856-8562, Japan

ACTIVE NOT RECRUITING

Ehime University Hospital

Ehime, 791-0295, Japan

ACTIVE NOT RECRUITING

Teine Keijinkai Hospital

Hokkaido, 006-8555, Japan

ACTIVE NOT RECRUITING

Osaka Rosai Hospital

Osaka, 591-8025, Japan

ACTIVE NOT RECRUITING

Toranomon Hospital

Tokyo, 105-8470, Japan

ACTIVE NOT RECRUITING

Amstedam University Medical Centers

Amsterdam, 1081 HV, Netherlands

ACTIVE NOT RECRUITING

Radboudumc

Nijmegen, 6525 GA, Netherlands

ACTIVE NOT RECRUITING

Erasmus medical center

Rotterdam, Netherlands

ACTIVE NOT RECRUITING

Hospital Universitari Vall d' Hebron

Barcelona, 08035, Spain

ACTIVE NOT RECRUITING

Hospital Clínic de Barcelona

Barcelona, 08036, Spain

ACTIVE NOT RECRUITING

Hospital Universitari Parc Tauli

Barcelona, 08208, Spain

ACTIVE NOT RECRUITING

Hospital General Universitario Gregorio Maranon

Madrid, 28007, Spain

ACTIVE NOT RECRUITING

Hospital Universitario Virgen del Rocio

Seville, 41013, Spain

ACTIVE NOT RECRUITING

Hospital Universitario Miguel Servet

Zaragoza, 50009, Spain

ACTIVE NOT RECRUITING

Ente Ospedaliero Cantonale

Lugano, 6900, Switzerland

ACTIVE NOT RECRUITING

University Hospital Zurich(USZ)

Zurich, 8091, Switzerland

ACTIVE NOT RECRUITING

University Hospital Southampton NHS Foundation Trust

Southampton, Hampshire, S016 6YD, United Kingdom

ACTIVE NOT RECRUITING

University Hospitals Birmingham NHS Foundation Trust of Trust Headquarters

Birmingham, West Midlands, B15 2GW, United Kingdom

ACTIVE NOT RECRUITING

Belfast Health & Social Care Trust (BHSCT) Royal Victoria Hospital

Belfast, BT12 6BA, United Kingdom

ACTIVE NOT RECRUITING

Royal Free Hospital NHS Foundation Trust

London, NW3 2QZ, United Kingdom

ACTIVE NOT RECRUITING

King's College Hospital NHS Foundation Trust

London, SE5 9RS, United Kingdom

ACTIVE NOT RECRUITING

Freeman Hospital

Newcastle upon Tyne, NE7 7DN, United Kingdom

ACTIVE NOT RECRUITING

Nottingham University Hospitals NHS Trust

Nottingham, United Kingdom

ACTIVE NOT RECRUITING

Related Publications (1)

  • Klatzkow H, Bhavsar-Burke I, Pearson M, Wentworth BJ. Primary Biliary Cholangitis in 2025: A New Frontier. Am J Gastroenterol. 2025 Dec 1;120(12):2746-2749. doi: 10.14309/ajg.0000000000003559. Epub 2025 May 29. No abstract available.

MeSH Terms

Conditions

Liver Cirrhosis, BiliaryPruritusCholangitisDigestive System Diseases

Interventions

volixibat

Condition Hierarchy (Ancestors)

Cholestasis, IntrahepaticCholestasisBile Duct DiseasesBiliary Tract DiseasesLiver DiseasesLiver CirrhosisFibrosisPathologic ProcessesPathological Conditions, Signs and SymptomsSkin DiseasesSkin and Connective Tissue DiseasesSkin ManifestationsSigns and Symptoms

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
DOUBLE
Who Masked
PARTICIPANT, INVESTIGATOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

September 9, 2021

First Posted

September 20, 2021

Study Start

September 22, 2021

Primary Completion (Estimated)

April 1, 2027

Study Completion (Estimated)

July 1, 2027

Last Updated

May 4, 2026

Record last verified: 2026-04

Locations