NCT04663308

Brief Summary

The purpose of this clinical research study is to learn more about the use of the study medicine, volixibat, for the treatment of pruritus (itching) associated with Primary Sclerosing Cholangitis (PSC), and to assess the possible impact on the disease progression of PSC.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
182

participants targeted

Target at P75+ for phase_2

Timeline
11mo left

Started Dec 2020

Longer than P75 for phase_2

Geographic Reach
14 countries

103 active sites

Status
active not recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress86%
Dec 2020Apr 2027

First Submitted

Initial submission to the registry

November 17, 2020

Completed
24 days until next milestone

First Posted

Study publicly available on registry

December 11, 2020

Completed
7 days until next milestone

Study Start

First participant enrolled

December 18, 2020

Completed
5.5 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 1, 2026

Expected
10 months until next milestone

Study Completion

Last participant's last visit for all outcomes

April 1, 2027

Last Updated

February 4, 2026

Status Verified

February 1, 2026

Enrollment Period

5.5 years

First QC Date

November 17, 2020

Last Update Submit

February 2, 2026

Conditions

Keywords

PruritusPSCItchItchingCholestasis

Outcome Measures

Primary Outcomes (1)

  • Mean change in the daily itch scores using the Adult Itch Reported Outcome (Adult ItchRO) questionnaire

    The Adult ItchRO is an 11-point NRS measurement of itch severity ranging from 0=no itch to 10=worst possible itch.

    Baseline through to Week 28

Secondary Outcomes (8)

  • Proportion of participants with itch response using the Adult ItchRO

    Baseline through to Week 28

  • The incidence of adverse events

    Baseline through to Week 28

  • Changes in serum bile acid levels

    Baseline through to Week 28

  • Changes in alkaline phosphatase

    Baseline through to Week 28

  • Changes in total bilirubin levels

    Baseline through to Week 28

  • +3 more secondary outcomes

Study Arms (5)

Part 1 Arm 1: Volixibat 20mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 20mg twice daily.

Drug: Volixibat

Part 1 Arm 2: Volixibat 80mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 80mg twice daily.

Drug: Volixibat

Part 1 Arm 3: Placebo

PLACEBO COMPARATOR

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Drug: Placebo

Part 2 Arm 1: Volixibat Selected Dose 20mg

EXPERIMENTAL

Participants randomized to this arm will receive volixibat 20mg twice daily.

Drug: Volixibat

Part 2 Arm 2: Placebo

PLACEBO COMPARATOR

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Drug: Placebo

Interventions

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Also known as: SHP626
Part 1 Arm 1: Volixibat 20mgPart 1 Arm 2: Volixibat 80mgPart 2 Arm 1: Volixibat Selected Dose 20mg

Capsules matched to study drug minus active substance

Part 1 Arm 3: PlaceboPart 2 Arm 2: Placebo

Eligibility Criteria

Age12 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Provide freely signed informed consent and assent (as applicable) and be willing to comply with all study visits and requirements through end of study, including the follow-up period.
  • Subjects aged ≥12 years for eligible regions; otherwise ≥18 years
  • Confirmed diagnosis of large duct or small duct PSC based on American Association for the Study of Liver Disease (AASLD) guidelines.
  • Pruritus associated with PSC as assessed by Adult ItchRO.
  • Ursodeoxycholic acid (UDCA) and anti-pruritic medication use will be allowed if meeting additional criteria.
  • Concomitant Inflammatory Bowel Disease (IBD) is allowed if meeting additional criteria.

You may not qualify if:

  • Pruritus associated with an etiology other than PSC
  • Evidence or clinical suspicion of decompensated cirrhosis, or a history of decompensation events
  • History of ileostomy or small bowel surgery/resection or other surgeries that may have disrupted the enterohepatic circulation
  • Evidence, history, or suspicion of other liver disease; PSC patients with AIH are not excluded.
  • Bile duct stent or percutaneous bile duct drain placement, or balloon dilatation procedure of a stricture within 12 weeks of Screening
  • Exceeding pre-defined biochemical values for alanine aminotransferase/aspartate aminotransferase (ALT/AST), estimated glomerular filtration rate (eGFR),serum creatinine (sCr), platelet count, international normalized ratio (INR) and total bilirubin
  • History of liver transplantation

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (103)

Southern California Research Center

Coronado, California, 92118, United States

Location

Cedars Sinai Medical Center

Los Angeles, California, 90048, United States

Location

University of California, Davis

Sacramento, California, 95817, United States

Location

California Pacific Medical Center Research Institute

San Francisco, California, 94109, United States

Location

University of Colorado - Anschutz Medical Campus

Aurora, Colorado, 80045, United States

Location

MedStar Georgetown University Hospital

Washington D.C., District of Columbia, 20007, United States

Location

Florida Research Institute

Lakewood Rch, Florida, 34211, United States

Location

University of Miami - Schiff Center for Liver Diseases

Miami, Florida, 33136, United States

Location

Tampa General Hospital

Tampa, Florida, 33606, United States

Location

Beth Israel Deaconess Medical Center

Boston, Massachusetts, 02215, United States

Location

Henry Ford Hospital

Detroit, Michigan, 48202, United States

Location

Mayo Clinic

Rochester, Minnesota, 55905, United States

Location

Southern Therapy and Advanced Research LLC

Jackson, Mississippi, 39216, United States

Location

Northwell Health

Manhasset, New York, 11030, United States

Location

New York University Langone Health

New York, New York, 10016, United States

Location

Weill Cornell Medical College

New York, New York, 10021, United States

Location

Columbia University Medical Center - Presbyterian Hospital and Vanderbilt Clinic

New York, New York, 10032, United States

Location

University of Rochester Medical Center - Strong Memorial Hospital

Rochester, New York, 14642, United States

Location

Duke Health - Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

Science 37, Inc (Remote-homebased Telemedicine)

Morrisville, North Carolina, 27560, United States

Location

Cleveland Clinic

Cleveland, Ohio, 44195, United States

Location

Einstein Healthcare Network - Einstein Medical Center

Philadelphia, Pennsylvania, 19141, United States

Location

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, 15213, United States

Location

Galen Medical Group

Hixson, Tennessee, 37343, United States

Location

Vanderbilt University Medical Center

Nashville, Tennessee, 37232, United States

Location

The Liver Institute At Methodist Dallas Medical Center

Dallas, Texas, 75203, United States

Location

University of Texas Southwestern Medical Center

Dallas, Texas, 75390, United States

Location

Houston Methodist Hospital

Houston, Texas, 77030, United States

Location

Liver Associates of Texas

Houston, Texas, 77030, United States

Location

University of Utah Health Care

Salt Lake City, Utah, 84132, United States

Location

Bon Secours Liver Institution of Hampton Roads Mary Immaculate Hospital Office

Newport News, Virginia, 23603, United States

Location

Richmond Community Hospital LLC

Richmond, Virginia, 23226, United States

Location

University of Washington - Harborview Medical Center

Seattle, Washington, 98104, United States

Location

Liver Institute Northwest

Seattle, Washington, 98105, United States

Location

Hospital Italiano de Buenos Aires

Buenos Aires, C1199, Argentina

Location

Glenny Corp S.A.

Ciudad AutĂ³noma Buenos Aires, C1430, Argentina

Location

Hospital El Cruce

San Juan Bautista, B1888, Argentina

Location

Royal Adelaide Hospital

Adelaide, 5000, Australia

Location

Northern Health

Epping, VIC 3076, Australia

Location

Liverpool Hospital

Liverpool, 2170, Australia

Location

Austin Health

Melbourne, 3084, Australia

Location

University of the Sunshine Coast

Sippy Downs, 4556, Australia

Location

Cliniques Universitaires Saint-Luc

Brussels, 1200, Belgium

Location

Universitair Ziekenhuis Antwerpen (UZA)

Ghent, 9000, Belgium

Location

University Hospital Ghent

Ghent, 9000, Belgium

Location

Hospital das Clinicas da UFMG

Belo Horizonte, 30140-080, Brazil

Location

Hospital Das Clinicas Da Ufg

GoiĂ¢nia, 74535-170, Brazil

Location

Hospital de Clinicas de Porto Alegre

Porto Alegre, 90035-903, Brazil

Location

Escola Bahiana de Medicina e Saude Publica

Salvador, 40290-000, Brazil

Location

Hospital do Rim e Hipertensao

SĂ£o Paulo, 04038-002, Brazil

Location

University of Alberta

Edmonton, Alberta, T6G 2R3, Canada

Location

McMaster University Hospital

Hamilton, Ontario, L8L 0A4, Canada

Location

The Ottawa Hospital - General Campus

Ottawa, Ontario, Canada

Location

University Health Network - Toronto General Hospital

Toronto, Ontario, M5G 2C4, Canada

Location

University of Calgary

Calgary, T2N 4Z6, Canada

Location

London Health Sciences Centre University Hospital

London, N6A 5A5, Canada

Location

McGill University Health Centre - Royal Victoria Hospital

Montreal, H4A 3J1, Canada

Location

Centre Hospitalier Universitaire Grenoble Alpes (CHU Grenoble Alpes)

Grenoble, 38043, France

Location

Centre Hospitalier Universitaire De Lille

Lille, 59037, France

Location

APHP-HĂ´pital Saint Antoine

Paris, 75571, France

Location

CHU Bordeaux - Haut LĂ©vĂªque

Pessac, 33600, France

Location

Hannover Medical School

Hanover, Lower Saxony, 30625, Germany

Location

Universitaetsklinikum Bonn

Bonn, Nordrhine-Westphalia, 53127, Germany

Location

Charité Universtitätsmedizin - Campus Virchow-Klinikum

Berlin, 13353, Germany

Location

Universitaetsklinikum Erlangen

Erlangen, 91054, Germany

Location

Universitätsklinikum Schleswig-Holstein - Campus Kiel

Kiel, 24105, Germany

Location

Universitatsklinikum Leipzig

Leipzig, 04103, Germany

Location

Otto-von-Guericke-Universitat Magdeburg

Magdeburg, 39120, Germany

Location

University Hospital Tubingen Medical Clinic

TĂ¼bingen, 72076, Germany

Location

St. Josefs-Hospital Wiesbaden

Wiesbaden, 65189, Germany

Location

Hillel Yaffe Medical Center

Hadera, 38100, Israel

Location

Rambam Medical Center

Haifa, 3109601, Israel

Location

Carmel Medical Center

Haifa, 3434104, Israel

Location

Shaare Zedek Medical Center

Jerusalem, 9103102, Israel

Location

Hadassah Medical Center - Ein Karem

Jerusalem, 91120, Israel

Location

Galilee Medical Center

Nahariya, 2210001, Israel

Location

Rabin Medical Center

Petah Tikva, 4941492, Israel

Location

Sheba Medical Center

Ramat Gan, 52621, Israel

Location

Tel Aviv Sourasky Medical Center

Tel Aviv, 6423906, Israel

Location

Azienda Ospedaliero-Universitaria di Bologna - Policlinico S. Orsola-Malpighi

Bologna, 40138, Italy

Location

Fondazione IRCCS Ca Granda Ospedale Maggiore Policlinico

Milan, 20122, Italy

Location

ASST Grande Ospedale Metropolitano Niguarda

Milan, 20162, Italy

Location

Fondazione IRCCS San Gerardo dei Tintori

Monza, 20900, Italy

Location

A.O.U. Federico II

Naples, 80131, Italy

Location

Azienda Ospedale Universita Padova

Padua, 35100, Italy

Location

Amsterdam UMC - VU Medisch Centrum (VUmc)

Amsterdam, 1081 HV, Netherlands

Location

Universitair Medisch Centrum Groningen

Groningen, 9713 GZ, Netherlands

Location

Radboud University Medical Centre (MC)

Nijmegen, 6525 GA, Netherlands

Location

Erasmus University Medical Center

Rotterdam, 3015 GD, Netherlands

Location

Hospital Clinic Barcelona

Barcelona, 08036, Spain

Location

Hospital General Universitario Gregorio Maranon

Madrid, 28007, Spain

Location

University Hospital Zurich

Zurich, 8091, Switzerland

Location

Royal Free Hospital

London, Hampstead, NW3 2QG, United Kingdom

Location

John Radcliffe Hospital

Oxford, Headington, OX3 9DU, United Kingdom

Location

Royal Victoria Hospital

Belfast, BT12 6BA, United Kingdom

Location

University Hospitals Birmingham NHS Foundation Trust - Wellcome Trust Birmingham Clinical Research Facility

Birmingham, B15 2TH, United Kingdom

Location

Cambridge University Hospitals NHS Foundation Trust - Addenbrooke's Hospital

Cambridge, CB2 0QQ, United Kingdom

Location

Lothian NHS Board

Edinburgh, EH164SA, United Kingdom

Location

St James' University Hospital Leeds Teaching Hospitals NHS Trust

Leeds, LS9 7TF, United Kingdom

Location

King's College Hospital NHS Foundation Trust

London, SE5 9RS, United Kingdom

Location

The Newcastle upon Tyne Hospitals NHS Foundation Trust - Royal Victoria Infirmary

Newcastle upon Tyne, NE1 4LP, United Kingdom

Location

Nottingham University Hospital NHS Trust

Nottingham, NG7 2FT, United Kingdom

Location

University Hospital Southampton NHS Foundation Trust

Southampton, United Kingdom

Location

MeSH Terms

Conditions

Cholangitis, SclerosingPruritusCholestasis

Interventions

volixibat

Condition Hierarchy (Ancestors)

CholangitisBile Duct DiseasesBiliary Tract DiseasesDigestive System DiseasesSkin DiseasesSkin and Connective Tissue DiseasesSkin ManifestationsSigns and SymptomsPathological Conditions, Signs and Symptoms

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
DOUBLE
Who Masked
PARTICIPANT, INVESTIGATOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 17, 2020

First Posted

December 11, 2020

Study Start

December 18, 2020

Primary Completion (Estimated)

June 1, 2026

Study Completion (Estimated)

April 1, 2027

Last Updated

February 4, 2026

Record last verified: 2026-02

Locations