NCT03525548

Brief Summary

This study will evaluate the efficacy of VX-445 in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are homozygous for the F508del mutation (F/F)

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
113

participants targeted

Target at P25-P50 for phase_3

Timeline
Completed

Started Aug 2018

Shorter than P25 for phase_3

Geographic Reach
4 countries

44 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

May 2, 2018

Completed
13 days until next milestone

First Posted

Study publicly available on registry

May 15, 2018

Completed
3 months until next milestone

Study Start

First participant enrolled

August 3, 2018

Completed
5 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 28, 2018

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

December 28, 2018

Completed
1.1 years until next milestone

Results Posted

Study results publicly available

January 27, 2020

Completed
Last Updated

January 27, 2020

Status Verified

January 1, 2020

Enrollment Period

5 months

First QC Date

May 2, 2018

Results QC Date

December 20, 2019

Last Update Submit

January 24, 2020

Conditions

Outcome Measures

Primary Outcomes (1)

  • Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)

    FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration.

    From Baseline at Week 4

Secondary Outcomes (4)

  • Absolute Change in Sweat Chloride (SwCl)

    From Baseline at Week 4

  • Absolute Change in Cystic Fibrosis Questionnaire-Revised (CFQ-R) Respiratory Domain Score

    From Baseline at Week 4

  • Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (AEs) and Serious Adverse Events (SAEs)

    From first dose of study drug in TC treatment period up to 28 days after last dose of study drug or to the completion of study participation date, whichever occurs first (up to Week 8)

  • Observed Pre-Dose Concentration (Ctrough) of VX-445, TEZ, TEZ Metabolite (M1-TEZ), and IVA

    Day 1 and Week 4

Study Arms (2)

TEZ/IVA

ACTIVE COMPARATOR

Following a run-in period of 4 weeks with Tezacaftor (TEZ)/Ivacaftor (IVA), participants received TEZ 100 milligram (mg)/IVA 150 mg as fixed-dose combination (FDC) tablet in the morning and IVA 150 mg as mono tablet in the evening for 4 weeks in the triple combination (TC) treatment period.

Drug: TEZ/IVADrug: IVADrug: Placebo

VX-445/TEZ/IVA TC

EXPERIMENTAL

Following a run-in period of 4 weeks with TEZ/IVA, participants received VX-445 200 mg/TEZ 100 mg/IVA 150 mg as FDC tablets in the morning and IVA 150 mg as mono tablet in the evening for 4 weeks in the TC treatment period.

Drug: VX-445/TEZ/IVADrug: IVADrug: Placebo

Interventions

Participants received VX-445/TEZ/IVA orally once daily in the morning.

Also known as: VX-445/VX-661/VX-770, VX-445/tezacaftor/ivacaftor
VX-445/TEZ/IVA TC

Participants received TEZ/IVA orally once daily in the morning.

Also known as: VX-661/VX-770, tezacaftor/ivacaftor
TEZ/IVA
IVADRUG

Participants received IVA orally once daily in the evening.

Also known as: VX-770, ivacaftor
TEZ/IVAVX-445/TEZ/IVA TC

Participants received placebo matched to VX-445/TEZ/IVA orally once daily in the morning.

TEZ/IVA

Eligibility Criteria

Age12 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Homozygous for the F508del mutation (F/F)
  • Forced expiratory volume in 1 second (FEV1) value ≥40% and ≤90% of predicted mean for age, sex, and height

You may not qualify if:

  • Clinically significant cirrhosis with or without portal hypertension
  • Lung infection with organisms associated with a more rapid decline in pulmonary status
  • Solid organ or hematological transplantation

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (44)

Banner University of Arizona Medical Center

Tucson, Arizona, 85724, United States

Location

University of Arkansas for Medical Sciences

Little Rock, Arkansas, 72205, United States

Location

Miller Children's Hospital/ Long Beach Memorial

Long Beach, California, 90806, United States

Location

Children's Hospital Los Angeles

Los Angeles, California, 90027, United States

Location

Valley Children's Hospital

Madera, California, 93636, United States

Location

National Jewish Health

Denver, Colorado, 80206, United States

Location

Joe DiMaggio Cystic Fibrosis & Pulmonary Center/ Joe DiMaggio Children's Hospital/ Memorial Regional Hospital

Hollywood, Florida, 33021, United States

Location

Central Florida Pulmonary Group, PA

Orlando, Florida, 32803, United States

Location

Nemours Children's Hospital

Orlando, Florida, 32827, United States

Location

Tampa General Hospital Cardiac and Lung Transplant Clinic

Tampa, Florida, 33606, United States

Location

Northwestern Memorial Hospital

Chicago, Illinois, 60611, United States

Location

Saint Francis Medical Center/ Children's Hospital of Illinoise/OSF

Peoria, Illinois, 61637, United States

Location

Tulane Medical Center

New Orleans, Louisiana, 70112, United States

Location

Massachusetts General Hospital Cystic Fibrosis Center Clinical Research Center

Boston, Massachusetts, 02114, United States

Location

Harper University Hospital

Detroit, Michigan, 48201, United States

Location

New York Medical College

Valhalla, New York, 10595, United States

Location

UNC Marisco Clinical Research Center

Chapel Hill, North Carolina, 27517, United States

Location

Rainbow Babies and Children's Hospital/University Hospitals Cleveland Medical Center

Cleveland, Ohio, 44106, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, 43205, United States

Location

Dayton Children's Hospital

Dayton, Ohio, 45404, United States

Location

ProMedica Toledo Hospital/ Toledo Children's Hospital/ Pediatric Pulmonary & Cystic Fibrosis Center

Toledo, Ohio, 43606, United States

Location

University of Oklahoma Health Sciences Center

Oklahoma City, Oklahoma, 73104, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

Medical University of South Carolina

Charleston, South Carolina, 29425, United States

Location

The University of Texas Southwestern Medical Center

Dallas, Texas, 75390, United States

Location

Vermont Lung Center

Colchester, Vermont, 05446, United States

Location

University of Virginia Primary Care Center

Charlottesville, Virginia, 22908, United States

Location

West Virginia University

Morgantown, West Virginia, 26506, United States

Location

Cliniques Universitaires de Bruxelles Hopital Erasme

Brussels, Belgium

Location

Universitair Ziekenhuis Brussel - Campus Jette

Brussels, Belgium

Location

UZ Antwerpen

Edegem, Belgium

Location

Universitair Ziekenhuis Gent

Ghent, Belgium

Location

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, Belgium

Location

Academic Medical Center

Amsterdam, Netherlands

Location

University Medical Center, Utrecht, Department of Pulmonology and Tuberculosis

Heidelberglaan, Netherlands

Location

UMC St. Radboud

Nijmegen, Netherlands

Location

Erasmus Medical Center

Rotterdam, Netherlands

Location

HagaZiekenhuis van den Haag

The Hague, Netherlands

Location

The Royal Belfast Hospital for Sick Children

Belfast, United Kingdom

Location

Heart of England NHS Foundation Trust, Birmingham Heartlands Hospital

Birmingham, United Kingdom

Location

Royal Devon and Exeter NHS Foundation Trust, Royal Devon and Exeter Hospital

Exeter, United Kingdom

Location

Leeds General Infirmary

Leeds, United Kingdom

Location

King's College Hospital

London, United Kingdom

Location

Southampton General Hospital

Southampton, United Kingdom

Location

Related Publications (1)

  • Heijerman HGM, McKone EF, Downey DG, Van Braeckel E, Rowe SM, Tullis E, Mall MA, Welter JJ, Ramsey BW, McKee CM, Marigowda G, Moskowitz SM, Waltz D, Sosnay PR, Simard C, Ahluwalia N, Xuan F, Zhang Y, Taylor-Cousar JL, McCoy KS; VX17-445-103 Trial Group. Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial. Lancet. 2019 Nov 23;394(10212):1940-1948. doi: 10.1016/S0140-6736(19)32597-8. Epub 2019 Oct 31.

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

ivacaftortezacaftor, ivacaftor drug combination

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR
Expanded Access
Yes

Study Record Dates

First Submitted

May 2, 2018

First Posted

May 15, 2018

Study Start

August 3, 2018

Primary Completion

December 28, 2018

Study Completion

December 28, 2018

Last Updated

January 27, 2020

Results First Posted

January 27, 2020

Record last verified: 2020-01

Locations