NCT03447262

Brief Summary

This study will evaluate the long-term safety and tolerability of VX-659 in triple combination (TC) with tezacaftor (TEZ) and ivacaftor (IVA) in subjects with cystic fibrosis (CF) who are homozygous or heterozygous for the F508del mutation.

Trial Health

68
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
484

participants targeted

Target at P50-P75 for phase_3

Timeline
Completed

Started Jul 2018

Geographic Reach
11 countries

100 active sites

Status
terminated

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

February 21, 2018

Completed
6 days until next milestone

First Posted

Study publicly available on registry

February 27, 2018

Completed
5 months until next milestone

Study Start

First participant enrolled

July 13, 2018

Completed
2.2 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

September 9, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

September 9, 2020

Completed
1.4 years until next milestone

Results Posted

Study results publicly available

January 25, 2022

Completed
Last Updated

January 25, 2022

Status Verified

December 1, 2021

Enrollment Period

2.2 years

First QC Date

February 21, 2018

Results QC Date

November 9, 2021

Last Update Submit

December 31, 2021

Conditions

Outcome Measures

Primary Outcomes (1)

  • Safety and Tolerability as Assessed by Number of Participants With Treatment-Emergent Adverse Events (AEs) and Serious Adverse Events (SAEs)

    From Day 1 up to 28 Days After Last Dose of Study Drug or to the Completion of Study Participation Date, Whichever Occurs First in the Current Study 659-105 (up to Week 100)

Secondary Outcomes (16)

  • Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1) for Participants From the Parent Study 659-102

    From Baseline at Week 72 (Study 659-105)

  • Absolute Change in ppFEV1 for Participants From the Parent Study 659-103

    From Baseline at Week 72 (Study 659-105)

  • Absolute Change in Sweat Chloride (SwCl) for Participants From the Parent Study 659-102

    From Baseline at Week 24 (Study 659-105)

  • Absolute Change in SwCl for Participants From the Parent Study 659-103

    From Baseline at Week 24 (Study 659-105)

  • Number of Pulmonary Exacerbations (PEx) for Participants From the Parent Study 659-102

    From Baseline up to Week 96 (Study 659-105)

  • +11 more secondary outcomes

Study Arms (1)

VX-659/TEZ/IVA TC

EXPERIMENTAL

Participants from parent studies VX17-659-102 (NCT03447249) or VX17-659-103 (NCT03460990) were administered VX-659 240 milligrams (mg) once daily (qd)/TEZ 100 mg qd/IVA 150 mg every 12 hours (q12h) in the TC treatment period for up to 96 weeks in the current study VX17-659-105.

Drug: VX-659/TEZ/IVADrug: IVA

Interventions

Fixed-dose combination tablets for oral administration qd in the morning.

Also known as: VX-659/VX-661/VX-770, VX-659/tezacaftor/ivacaftor
VX-659/TEZ/IVA TC
IVADRUG

IVA tablet qd in the evening.

Also known as: VX-770, ivacaftor
VX-659/TEZ/IVA TC

Eligibility Criteria

Age12 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Completed study drug treatment in a parent study; or had study drug interruption(s) in a parent study but completed study visits up to the last scheduled visit of the Treatment Period in the parent study.

You may not qualify if:

  • History of drug intolerance in a parent study that would pose an additional risk to the subject in the opinion of the investigator.
  • Current participation in an investigational drug trial (other than a parent study)

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (100)

University of Alabama at Birmingham

Birmingham, Alabama, 35233, United States

Location

Stanford University

Palo Alto, California, 94304, United States

Location

Children's Hospital Colorado

Aurora, Colorado, 80045, United States

Location

Hartford Hospital

Hartford, Connecticut, 06102, United States

Location

Yale New Haven Medical Center

New Haven, Connecticut, 06511, United States

Location

University of Miami Miller School of Medicine

Miami, Florida, 33136, United States

Location

Nicklaus Children's Hospital

Miami, Florida, 33155, United States

Location

Orlando Health, Inc.- Arnold Palmer Hospital for Children (APH)

Orlando, Florida, 32806, United States

Location

Johns Hopkins All Children's Hospital Outpatient Care Center

St. Petersburg, Florida, 33701, United States

Location

St. Luke's CF Center of Idaho

Boise, Idaho, 83712, United States

Location

Cystic Fibrosis Center of Chicago

Glenview, Illinois, 60025, United States

Location

Advocate Children's Hospital - Park Ridge / North Suburban Pulmonary and Critical Care Consultants

Niles, Illinois, 60714, United States

Location

Indiana Clinical Research Center, IU Health University Hospital

Indianapolis, Indiana, 46202, United States

Location

The University of Iowa Hospitals and Clinics

Iowa City, Iowa, 52242, United States

Location

University of Kentucky

Lexington, Kentucky, 40536, United States

Location

Kosair Charities Pediatric Clinical Research Unit

Louisville, Kentucky, 40202, United States

Location

Johns Hopkins Hospital

Baltimore, Maryland, 21287, United States

Location

Boston Children's Hospital

Boston, Massachusetts, 02115, United States

Location

UMass Memorial Medical Center

Worcester, Massachusetts, 01655, United States

Location

Michigan Medicine

Ann Arbor, Michigan, 48109-5212, United States

Location

Spectrum Health Medical Group Adult Cystic Fibrosis Care Center

Grand Rapids, Michigan, 49546, United States

Location

University of Minnesota

Minneapolis, Minnesota, 55455, United States

Location

University of Mississippi Medical Center

Jackson, Mississippi, 39216, United States

Location

The Children's Mercy Hospital

Kansas City, Missouri, 64108, United States

Location

Washington University School of Medicine/ St. Louis Children's Hospital

St Louis, Missouri, 63110, United States

Location

Dartmouth Hitchcock, Manchester

Manchester, New Hampshire, 03104, United States

Location

Rutgers-Robert Wood Johnson Medical School

New Brunswick, New Jersey, 08901, United States

Location

Albany Medical College

Albany, New York, 12208, United States

Location

CF Therapeutics Development Center of Western New York

Buffalo, New York, 14203, United States

Location

Northwell Health, Long Island Jewish Medical Center

New Hyde Park, New York, 11040, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

SUNY Upstate Medical University

Syracuse, New York, 13210, United States

Location

Clinical Research of Charlotte

Charlotte, North Carolina, 28277, United States

Location

Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

Cincinnati Children's Hospital

Cincinnati, Ohio, 45229, United States

Location

Santiago Reyes, M.D.

Oklahoma City, Oklahoma, 73112, United States

Location

Oregon Health & Science University

Portland, Oregon, 97239, United States

Location

Drexel University College of Medicine / Drexel Adult Cystic Fibrosis Center

Philadelphia, Pennsylvania, 19107, United States

Location

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, 15224, United States

Location

Sanford Children's Specialty Clinic

Sioux Falls, South Dakota, 57105, United States

Location

University of Tennessee Medical Center- Adult Cystic Fibrosis Clinic

Knoxville, Tennessee, 37920, United States

Location

Children's Foundation Research Center / Le Bonheur Children's Hospital

Memphis, Tennessee, 38103, United States

Location

Vanderbilt University Medical Center

Nashville, Tennessee, 37232, United States

Location

Cook Children's Medical Center

Fort Worth, Texas, 76104, United States

Location

Texas Children's Hospital

Houston, Texas, 77030, United States

Location

University of Utah/ Primary Children's Medical Center

Salt Lake City, Utah, 84132, United States

Location

Seattle Children's Hospital

Seattle, Washington, 98105, United States

Location

Providence Pediatric Pulmonary & Cystic Fibrosis Clinic

Spokane, Washington, 99204, United States

Location

Royal Adelaide Hospital

Adelaide, Australia

Location

The Prince Charles Hospital

Chermside, Australia

Location

Alfred Hospital

Melbourne, Australia

Location

Institute for Respiratory Health, Sir Charles Gairdner Hospital

Nedlands, Australia

Location

John Hunter Hospital & Hunter Medical Research Institute and John Hunter Children's Hospital

New Lambton, Australia

Location

Telethon Kids Institute

Perth, Australia

Location

Sydney Children's Hospital

Randwick, Australia

Location

Lady Cilento Children's Hospital

South Brisbane, Australia

Location

Stollery Children's Hospital

Edmonton, Canada

Location

Queen Elizabeth II Health Sciences Center

Halifax, Canada

Location

St. Michael's Hospital

Toronto, Canada

Location

Juliane Marie Center, Rigshospitalet

Copenhagen, Denmark

Location

Charite Paediatric Pulmonology Department

Berlin, Germany

Location

Universitaetsklinkum Koeln, CF-Studienzentrum

Cologne, Germany

Location

Ruhrlandklinik Westdeutsches Lungenzentrum am Klinikum Essen

Essen, Germany

Location

Clinic of J.W. Goethe University

Frankfurt, Germany

Location

Medizinische Hochschule Hannover

Hanover, Germany

Location

Mukeviszidose-Zentrum am Universitatsklinikum Jena, Klinik fuer Kinder- und Jugendmedizin

Jena, Germany

Location

Universitatsklinikum Schleswig-Holstein, Klinik für Kinder- und Jugendmedizin

Lübeck, Germany

Location

Klinikum Innenstadt, University of Munich

München, Germany

Location

Pneumologische Praxis Pasing

München, Germany

Location

Cork University Hospital

Cork, Ireland

Location

Beaumont Hospital

Dublin, Ireland

Location

Our Lady's Children's Hospital

Dublin, Ireland

Location

St. Vincent's University Hospital

Dublin, Ireland

Location

Temple Street Children's University Hospital

Dublin, Ireland

Location

University Hospital Galway

Galway, Ireland

Location

University Hospital Limerick

Limerick, Ireland

Location

Lady Davis Carmel Medical Center

Haifa, Israel

Location

Rambam Health Care Campus, Liver Unit

Haifa, Israel

Location

Pediatrics Hadassah Medical Center

Jerusalem, Israel

Location

Schneider Children's Medical Center

Petah Tikva, Israel

Location

Sheba Medical Center

Tel Litwinsky, Israel

Location

Klinika Mukowiscydozy IMD Oddozial Chorob Pluc Szpzoz IM. Dzieci WarszaWY

Łomianki, Poland

Location

Hospital Universitari Vall d Hebron

Barcelona, Spain

Location

Hospital Universitari Vall d´Hebron Servicio de Broncoscopia

Barcelona, Spain

Location

Hospital Universitario 12 de Octubre

Madrid, Spain

Location

Hospital Universitario Infantil La Paz

Madrid, Spain

Location

Parc Tauli Sabadell Hospital Universitari

Sabadell, Spain

Location

Hospital Universitario Virgen del Rocio

Seville, Spain

Location

Hospital Universitario y Politecnico La Fe

Valencia, Spain

Location

Lindenhofspital - Quartier Bleu

Bern, Switzerland

Location

Kinderspital Zuerich

Zurich, Switzerland

Location

Papworth Hospital NHS Foundation Trust, Papworth Everard

Cambridge, United Kingdom

Location

Clinical Research Facility, Queen Elizabeth University Hospital

Glasgow, United Kingdom

Location

St. James University Hospital

Leeds, United Kingdom

Location

Liverpool Head and Chest Hospital

Liverpool, United Kingdom

Location

Royal Brompton & Harefield NHS Foundation Trust, Royal Brompton Hospital

London, United Kingdom

Location

Wythenshaw e Hospital

Manchester, United Kingdom

Location

The Newcastle upon Tyne Hospitals NHS Foundation Trust, The Royal Victoria Infirmary

Newcastle upon Tyne, United Kingdom

Location

Wolfson Cystic Fibrosis Unit, City Campus

Nottingham, United Kingdom

Location

All Wales Adult Cystic Fibrosis Centre, University Hospital Llandough

Penarth, United Kingdom

Location

Related Publications (2)

  • Heneghan M, Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2023 Nov 20;11(11):CD010966. doi: 10.1002/14651858.CD010966.pub4.

  • Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2020 Dec 17;12(12):CD010966. doi: 10.1002/14651858.CD010966.pub3.

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

ivacaftor

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 3
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 21, 2018

First Posted

February 27, 2018

Study Start

July 13, 2018

Primary Completion

September 9, 2020

Study Completion

September 9, 2020

Last Updated

January 25, 2022

Results First Posted

January 25, 2022

Record last verified: 2021-12

Locations