NCT03224351

Brief Summary

This is a Phase 2, randomized, double-blind, placebo- and tezacaftor/ivacaftor (TEZ/IVA)-controlled, parallel-group, 3-part, multicenter study designed to evaluate the safety and efficacy of VX-659 in triple combination (TC) with TEZ and IVA in subjects with cystic fibrosis (CF) who are homozygous for the F508del mutation of the CF transmembrane conductance regulator (CFTR) gene (F/F genotype), or who are heterozygous for the F508del mutation and a minimal function (MF) CFTR mutation not likely to respond to TEZ, IVA, or TEZ/IVA (F/MF genotypes).

Trial Health

90
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
124

participants targeted

Target at P75+ for phase_2

Timeline
Completed

Started Aug 2017

Shorter than P25 for phase_2

Geographic Reach
4 countries

47 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

July 18, 2017

Completed
3 days until next milestone

First Posted

Study publicly available on registry

July 21, 2017

Completed
18 days until next milestone

Study Start

First participant enrolled

August 8, 2017

Completed
7 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

February 28, 2018

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

February 28, 2018

Completed
3.1 years until next milestone

Results Posted

Study results publicly available

April 22, 2021

Completed
Last Updated

April 22, 2021

Status Verified

February 1, 2021

Enrollment Period

7 months

First QC Date

July 18, 2017

Results QC Date

February 25, 2021

Last Update Submit

March 29, 2021

Conditions

Outcome Measures

Primary Outcomes (2)

  • Safety and Tolerability as Assessed by Number of Participants With Treatment Emergent Adverse Events (TEAEs) and Serious Adverse Events (SAEs)

    Day 1 Through Safety Follow-up (up to Day 61 for Part 1, Day 85 for Part 2 and Day 57 for Part 3)

  • Absolute Change in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1)

    FEV1 is the volume of air that can forcibly be blown out in one second, after full inspiration.

    From Baseline Through Day 29

Secondary Outcomes (4)

  • Absolute Change in Sweat Chloride Concentrations

    From Baseline Through Day 29

  • Relative Change in ppFEV1

    From Baseline Through Day 29

  • Absolute Change in Cystic Fibrosis Questionnaire-Revised (CFQ-R) Respiratory Domain Score

    From Baseline at Day 29

  • Observed Pre-dose Concentration (Ctrough) of VX-659, TEZ, M1-TEZ, IVA, M1-IVA, and VX-561

    Pre-dose at Day 15 and Day 29

Study Arms (8)

Part 1: Placebo

PLACEBO COMPARATOR

Participants received placebo matched to VX-659/TEZ/IVA in TC treatment period for 4 weeks and placebo matched TEZ/IVA in washout period for 4 days.

Drug: Placebo (matched to VX-659/TEZ/IVA)

Part 1: VX-659/TEZ/IVA TC - Low Dose

EXPERIMENTAL

Participants received VX-659 80 milligram (mg) once daily (qd)/TEZ 100 mg qd/IVA 150 mg every 12 hours (q12h) in TC treatment period for 4 weeks and TEZ 100 mg qd/IVA 150 mg q12h in washout period for 4 days.

Drug: VX-659Drug: TEZ/IVADrug: IVA

Part 1: VX-659/TEZ/IVA TC - Medium Dose

EXPERIMENTAL

Participants received VX-659 240 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in TC treatment period for 4 weeks and TEZ 100 mg qd/IVA 150 mg q12h in washout period for 4 days.

Drug: VX-659Drug: TEZ/IVADrug: IVA

Part 1: VX-659/TEZ/IVA TC - High Dose

EXPERIMENTAL

Participants received VX-659 400 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in TC treatment period for 4 weeks and TEZ 100 mg qd/IVA 150 mg q12h in washout period for 4 days.

Drug: VX-659Drug: TEZ/IVADrug: IVA

Part 2: TEZ/IVA

ACTIVE COMPARATOR

Following run-in period with TEZ 100 mg qd/IVA 150 mg q12h for 4 weeks, participants received TEZ 100 mg qd/IVA 150 mg q12h in TC treatment period for 4 weeks and TEZ 100 mg qd/IVA 150 mg q12h in washout period for 4 weeks.

Drug: TEZ/IVADrug: IVA

Part 2: VX-659/TEZ/IVA TC

EXPERIMENTAL

Following run-in period with TEZ 100 mg qd/IVA 150 mg q12h for 4 weeks, participants received VX-659 400 mg qd/TEZ 100 mg qd/IVA 150 mg q12h in TC treatment period for 4 weeks and TEZ 100 mg qd/IVA 150 mg q12h in washout period for 4 weeks.

Drug: VX-659Drug: TEZ/IVADrug: IVA

Part 3: Placebo

PLACEBO COMPARATOR

Participants received placebo matched to VX-659/TEZ/VX-561 in TC treatment period for 4 weeks.

Drug: Placebo (matched to VX-659/TEZ/VX-561)

Part 3: VX-659/TEZ/VX-561 TC

EXPERIMENTAL

Participants received VX-659 400 mg qd/TEZ 100 mg qd/VX-561 200 mg qd in TC treatment period for 4 weeks.

Drug: VX-659Drug: TEZDrug: VX-561

Interventions

VX-659DRUG

Tablet for oral administration.

Part 1: VX-659/TEZ/IVA TC - High DosePart 1: VX-659/TEZ/IVA TC - Low DosePart 1: VX-659/TEZ/IVA TC - Medium DosePart 2: VX-659/TEZ/IVA TCPart 3: VX-659/TEZ/VX-561 TC

TEZ/IVA fixed-dose combination tablet for oral administration.

Also known as: VX-661/VX-770, Tezacaftor/Ivacaftor
Part 1: VX-659/TEZ/IVA TC - High DosePart 1: VX-659/TEZ/IVA TC - Low DosePart 1: VX-659/TEZ/IVA TC - Medium DosePart 2: TEZ/IVAPart 2: VX-659/TEZ/IVA TC
IVADRUG

Tablet for oral administration.

Also known as: VX-770, Ivacaftor
Part 1: VX-659/TEZ/IVA TC - High DosePart 1: VX-659/TEZ/IVA TC - Low DosePart 1: VX-659/TEZ/IVA TC - Medium DosePart 2: TEZ/IVAPart 2: VX-659/TEZ/IVA TC

Placebo matched to VX-659 and TEZ/IVA.

Part 1: Placebo
TEZDRUG

Tablet for oral administration.

Also known as: VX-661, Tezacaftor
Part 3: VX-659/TEZ/VX-561 TC
VX-561DRUG

Tablet for oral administration.

Also known as: CTP-656
Part 3: VX-659/TEZ/VX-561 TC

Placebo matched to VX-659, TEZ and VX-561.

Part 3: Placebo

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Body weight ≥35 kg.
  • Subjects must have an eligibleCFTR genotype.
  • Part 1 and Part 3: Heterozygous for F508del and an MF mutation (F/MF)
  • Part 2: Homozygous for F508del (F/F)
  • FEV1 value ≥40% and ≤90% of predicted mean for age, sex, and height

You may not qualify if:

  • History of clinically significant cirrhosis with or without portal hypertension.
  • Glucose-6-phosphate dehydrogenase (G6PD) deficiency
  • Lung infection with organisms associated with a more rapid decline in pulmonary status.
  • History of solid organ or hematological transplantation.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (47)

Yale New Haven Hospital

New Haven, Connecticut, 06520, United States

Location

University of Miami/Miller School of Medicine

Miami, Florida, 33136, United States

Location

Advocate Children's Hospital - Park Ridge / North Suburban Pulmonary and Critical Care Consultants

Morton Grove, Illinois, 60053, United States

Location

Indiana University Health

Indianapolis, Indiana, 46202, United States

Location

The University of Iowa Hospitals and Clinics

Iowa City, Iowa, 52242, United States

Location

The Johns Hopkins Hospital/ Johns Hopkins Hospital, David Rubenstein Child Health Building

Baltimore, Maryland, 21287, United States

Location

Boston Children's Hospital

Boston, Massachusetts, 02155, United States

Location

University of Massachusetts Memorial Medical Center

Worcester, Massachusetts, 01655, United States

Location

University of Michigan Health System

Ann Arbor, Michigan, 48109, United States

Location

Helen DeVos Children's Hospital CF Center

Grand Rapids, Michigan, 49503, United States

Location

Children's Mercy Hospital

Kansas City, Missouri, 64108, United States

Location

Rutgers-Robert Wood Johnson Medical School/ Rutgers-Robert Wood Johnson Medical School, Clinical Research Center

New Brunswick, New Jersey, 08902, United States

Location

Albany Medical College

Albany, New York, 12208, United States

Location

Northwell Health, Long Island Jewish Medical Center

New Hyde Park, New York, 11040, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

SUNY Upstate Medical University

Syracuse, New York, 13210, United States

Location

Respiratory Diseases of Children & Adolescents

Oklahoma City, Oklahoma, 73112, United States

Location

Children's Hospital of Pittsburgh of University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, 15224, United States

Location

Sanford Research / USD

Sioux Falls, South Dakota, 57104, United States

Location

University of Tennessee Medical Center-Adult Cystic Fibrosis Clinic

Knoxville, Tennessee, 37920, United States

Location

Children's Foundation Research Center / Le Bonheur Children's Hospital

Memphis, Tennessee, 38103, United States

Location

Vanderbilt University Medical Center

Nashville, Tennessee, 37232, United States

Location

University of Utah / Primary Children's Medical Center

Salt Lake City, Utah, 84014, United States

Location

Seattle Children's Hospital

Seattle, Washington, 98105, United States

Location

Providence Pediatric Pulmonary & Allergy/Immunology Clinic

Spokane, Washington, 99204, United States

Location

Cork University Hospital

Cork, Ireland

Location

St. Vincent's University Hosptial

Dublin, Ireland

Location

Galway University Hospitals

Galway, Ireland

Location

University Hospital Limerick

Limerick, Ireland

Location

Carmel Medical Center

Haifa, Israel

Location

Ruth Children's Hospital Rambam Health Care Campus

Haifa, Israel

Location

Hadassah Medical Organization

Jerusalem, Israel

Location

The Chaim Sheba medical center

Ramat Gan, Israel

Location

Schneider Children's Medical Center

Tikvah, Israel

Location

Birmingham Heartlands Hospital

Birmingham, B95SS, United Kingdom

Location

Papworth Hospital NHS Foundation Trust, Papworth Everard

Cambridge, United Kingdom

Location

University Hospital Llandough in Cardiff

Cardiff, United Kingdom

Location

Royal Devon and Exeter NHS Foundation Trust, Royal Devon and Exeter Hospital

Devon, United Kingdom

Location

The Newcastle upon Tyne Hospitals NHS Foundation Trust, The Royal Victoria Infirmary

Fulham, United Kingdom

Location

Greater Glasgow and Clyde NHS Board, Glasgow Clinical Research Facility

Glasgow, United Kingdom

Location

Southampton University Hospitals NHS Foundation Trust

Hampshire, United Kingdom

Location

Regional Respiratory Centre Belfast City Hospital

London, United Kingdom

Location

Royal Brompton & Harefied NHS Foundation Trust

London, United Kingdom

Location

University Hospital of South Manchester NHS Trust, North West Lung Centre

Manchester, United Kingdom

Location

Liverpool Heart and Chest Hospital

Merseyside, United Kingdom

Location

Nottingham University Hospitals NHS Trust

Nottingham, United Kingdom

Location

Ruth Children's Hospital Rambam Health Care Campus

Nottingham, United Kingdom

Location

Related Publications (3)

  • Heneghan M, Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2023 Nov 20;11(11):CD010966. doi: 10.1002/14651858.CD010966.pub4.

  • Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2020 Dec 17;12(12):CD010966. doi: 10.1002/14651858.CD010966.pub3.

  • Davies JC, Moskowitz SM, Brown C, Horsley A, Mall MA, McKone EF, Plant BJ, Prais D, Ramsey BW, Taylor-Cousar JL, Tullis E, Uluer A, McKee CM, Robertson S, Shilling RA, Simard C, Van Goor F, Waltz D, Xuan F, Young T, Rowe SM; VX16-659-101 Study Group. VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles. N Engl J Med. 2018 Oct 25;379(17):1599-1611. doi: 10.1056/NEJMoa1807119. Epub 2018 Oct 18.

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

VX-659tezacaftor, ivacaftor drug combinationivacaftortezacaftor

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

July 18, 2017

First Posted

July 21, 2017

Study Start

August 8, 2017

Primary Completion

February 28, 2018

Study Completion

February 28, 2018

Last Updated

April 22, 2021

Results First Posted

April 22, 2021

Record last verified: 2021-02

Locations