NCT02971839

Brief Summary

This study will evaluate the efficacy and safety of CTP-656 in patients with cystic fibrosis (CF) who have a cystic fibrosis transmembrane conductance regulator (CFTR) gating mutation.

Trial Health

57
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
11

participants targeted

Target at below P25 for phase_2

Timeline
Completed

Started Dec 2016

Shorter than P25 for phase_2

Geographic Reach
1 country

14 active sites

Status
terminated

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

November 21, 2016

Completed
2 days until next milestone

First Posted

Study publicly available on registry

November 23, 2016

Completed
8 days until next milestone

Study Start

First participant enrolled

December 1, 2016

Completed
8 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

August 1, 2017

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

August 1, 2017

Completed
3.1 years until next milestone

Results Posted

Study results publicly available

August 26, 2020

Completed
Last Updated

August 26, 2020

Status Verified

August 1, 2020

Enrollment Period

8 months

First QC Date

November 21, 2016

Results QC Date

August 11, 2020

Last Update Submit

August 11, 2020

Conditions

Outcome Measures

Primary Outcomes (1)

  • Change From Baseline in Sweat Chloride at Day 28

    From baseline at Day 28

Secondary Outcomes (2)

  • Change From Baseline in Percent Predicted Forced Expiratory Volume in 1 Second (ppFEV1) at Day 28

    From baseline at Day 28

  • Change From Baseline in Cystic Fibrosis Questionnaire-Respiratory Domain (CFQ-R) at Day 28

    From baseline at Day 28

Study Arms (5)

VX-561 20 mg

EXPERIMENTAL
Drug: VX-561

VX-561 100 mg

EXPERIMENTAL
Drug: VX-561

VX-561 150 mg

EXPERIMENTAL
Drug: VX-561

Ivacaftor

ACTIVE COMPARATOR
Drug: IVA

Placebo

PLACEBO COMPARATOR
Drug: Placebo

Interventions

VX-561DRUG
Also known as: CTP-656
VX-561 100 mgVX-561 150 mgVX-561 20 mg
Placebo
IVADRUG
Also known as: ivacaftor; VX-770, Kalydeco
Ivacaftor

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • years of age or older
  • Has a confirmed diagnosis of CF with at least one allele of the following CFTR gating mutations: G551D, G1244E, G1349D, G178R, G551S, S1251N, S1255P, S549N, and S549R.
  • Has been stable on Kalydeco therapy for at least 3 months prior to screening
  • Has FEV1 ≥ 60% of predicted normal for age, sex, and height at screening and baseline (Day 1) assessments
  • Weighs at least 40 kg at screening
  • Patients of either gender and women of childbearing potential must be willing to use a medically highly effective form of birth control during the treatment period and 30 days after the last dose of study treatment.

You may not qualify if:

  • Acute upper respiratory infection or lower respiratory infection, pulmonary exacerbation, or changes in therapy within 4 weeks of study treatment
  • Uncontrolled type 2 diabetes, or uncontrolled CF-related diabetes
  • History of hepatitis C or chronic active hepatitis B infection
  • History of pulmonary tuberculosis, non-tuberculosis mycobacterial infections or allergic bronchopulmonary aspergillosis (ABPA) treated during screening or within 2 years prior to screening
  • Colonization with B. cenocepacia, B. dolosa, B. multivorans, and/or M. abcessus within 2 years prior to Screening
  • Abnormal liver function
  • History of abnormal renal function
  • History of prolonged QTcF \> 450 msec for males or QTcF \> 470 msec for females
  • History of solid organ or hematological transplantation
  • Using any inhibitor or inducer of cytochrome P450/3A during the study or within 30 days of screening
  • Women who are pregnant or lactating, or have plans to become pregnant during the study or within 1 month following the last dose

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (14)

University of Southern California

Los Angeles, California, United States

Location

Stanford Hospital

Palo Alto, California, United States

Location

Children's National Health

Washington D.C., District of Columbia, United States

Location

University of Miami

Miami, Florida, United States

Location

Rush University

Chicago, Illinois, United States

Location

Indiana University

Indianapolis, Indiana, United States

Location

Boston Children's Hospital

Boston, Massachusetts, United States

Location

University of Massachusetts

Worcester, Massachusetts, United States

Location

Washington University

St Louis, Missouri, United States

Location

Atlantic Health

Morristown, New Jersey, United States

Location

New York Medical College

Valhalla, New York, United States

Location

Cincinnati Children's Hospital

Cincinnati, Ohio, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Location

MeSH Terms

Conditions

Cystic Fibrosis

Interventions

ivacaftor

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Results Point of Contact

Title
Medical Monitor
Organization
Vertex Pharmaceuticals Incorporated

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 21, 2016

First Posted

November 23, 2016

Study Start

December 1, 2016

Primary Completion

August 1, 2017

Study Completion

August 1, 2017

Last Updated

August 26, 2020

Results First Posted

August 26, 2020

Record last verified: 2020-08

Data Sharing

IPD Sharing
Will not share

Locations