NCT00628498

Brief Summary

Single arm, open-label study to provide Defibrotide to patients diagnosed with VOD. Defibrotide is no longer available though the Emergency Use IND mechanism (also known as compassionate use, or single patient named use). This protocol is the only mechanism by which Defibrotide can be made available to patients in the U.S.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
1,206

participants targeted

Target at P75+ for phase_3

Timeline
Completed

Started Dec 2007

Longer than P75 for phase_3

Geographic Reach
1 country

125 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

December 1, 2007

Completed
3 months until next milestone

First Submitted

Initial submission to the registry

February 25, 2008

Completed
9 days until next milestone

First Posted

Study publicly available on registry

March 5, 2008

Completed
8.3 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 1, 2016

Completed
2 months until next milestone

Study Completion

Last participant's last visit for all outcomes

September 1, 2016

Completed
1.2 years until next milestone

Results Posted

Study results publicly available

November 30, 2017

Completed
Last Updated

November 30, 2017

Status Verified

November 1, 2017

Enrollment Period

8.6 years

First QC Date

February 25, 2008

Results QC Date

November 2, 2017

Last Update Submit

November 2, 2017

Conditions

Keywords

VOD

Outcome Measures

Primary Outcomes (1)

  • Survival by Day+100 Post Stem Cell Transplant or Chemotherapy

    Day +100 from HSCT or 100 days from start of chemotherapy

Study Arms (1)

Defibrotide

EXPERIMENTAL

Defibrotide 25 mg/kg day given in 4 divided doses approximately every 6 hours

Drug: Defibrotide

Interventions

Defibrotide is a single-stranded polydeoxyribonucleotide derived from porcine intestinal mucosa by controlled depolymerisation. Defibrotide has a complex mechanism of action with antithrombotic, anti-ischemic, anti-inflammatory, anti-adhesive and thrombolytic properties but no significant systemic anti-coagulant effects. Defibrotide is dose intravenously as a 2-hour infusion every 6 hours at a dose of 25 mg/kg/day. Recommended duration of therapy is 21 days.

Defibrotide

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Entry criteria include the following:
  • Clinical diagnosis of VOD, made by Baltimore Criteria, Modified Seattle Criteria, or biopsy proven:
  • Baltimore Criteria- Bilirubin ≥2 mg/dL and at least 2 of the following clinical findings:
  • Ascites (radiographic or physical exam)
  • Weight gain of ≥5% compared to the day of conditioning-- if this value is not available, the weight on the date of admission to the SCT unit may be used)
  • Hepatomegaly; increased over baseline.
  • Modified Seattle Criteria: At least two of the following
  • Bilirubin ≥2 mg/dL
  • Ascites (radiographic or physical exam) and/or weight gain ≥5% above baseline weight (defined as weight on the first day of conditioning- if this value is not available, the weight on the date of admission to the SCT unit may be used)
  • hepatomegaly increased over baseline
  • Patients that do not meet the Baltimore Criteria or Modified Seattle Criteria and have biopsy proven VOD are eligible.
  • Patient must also provide written informed consent.

You may not qualify if:

  • Use of any medication which increases the risk of hemorrhage is disallowed. Use of heparin or other anticoagulants is disallowed within 12 hours unless being used for routine central venous line management, fibrinolytic instillation for central venous line occlusion, intermittent dialysis or ultrafiltration of CVVH.
  • Clinically significant uncontrolled acute bleeding, defined as hemorrhage requiring \> 15 cc/kg of packed red blood cells (e.g., a pediatric patient weighing 20 kg and requiring \> 300cc of packed red blood cells/24 hours, or an adult patient weighing 70 kg and requiring \>3 units of packed red blood cells/24 hours) to replace blood loss, OR bleeding from a site which in the Investigator's opinion constitutes a potential life-threatening source (e.g. pulmonary hemorrhage or CNS bleeding), irrespective of amount of blood loss, at any point from the date of SCT through the date of severe VOD diagnosis.
  • Hemodynamic instability as defined by a requirement for multiple pressors, or inability to maintain mean arterial pressure (for children: to maintain mean arterial pressure within 1 standard deviation of age-adjusted levels) with single pressor support.
  • Woman who are pregnant.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (125)

Children's Hospital of Alabama

Birmingham, Alabama, 35233, United States

Location

Phoenix Children's Hospital

Phoenix, Arizona, 85016, United States

Location

Mayo Clinic Cancer Center

Phoenix, Arizona, 85054, United States

Location

Arizona Oncology

Scottsdale, Arizona, 85258, United States

Location

University Medical Center

Tucson, Arizona, 85724, United States

Location

University of Arkansas for Medical Services

Little Rock, Arkansas, 72205, United States

Location

City of Hope Medical Center

Duarte, California, 91010, United States

Location

The University of California, San Diego

La Jolla, California, 92037, United States

Location

Loma Linda University

Loma Linda, California, 92354, United States

Location

Long Beach Memorial Medical Center

Long Beach, California, 90806, United States

Location

Children's Hospital of Los Angeles

Los Angeles, California, 90027, United States

Location

Children's Hospital & Research Center Oakland

Oakland, California, 94609, United States

Location

Children's Hospital of Orange County (CHOC)

Orange, California, 92868, United States

Location

Sutter Institute for Medical Research

Sacramento, California, 95816, United States

Location

University of California Davis Health System

Sacramento, California, 95817, United States

Location

Rady's Children's Hospital - San Diego

San Diego, California, 92123, United States

Location

University of California San Francisco Medical Center

San Francisco, California, 94143, United States

Location

Stanford University Medical Center

Stanford, California, 94305, United States

Location

Children's Hospital Colorado

Aurora, Colorado, 80045, United States

Location

US Oncology - Denver

Denver, Colorado, 80218, United States

Location

Yale - New Haven Hospital

New Haven, Connecticut, 06520, United States

Location

Nemours-Al duPont Hospital for Children

Wilmington, Delaware, 19803, United States

Location

Georgetown University Hospital

Washington D.C., District of Columbia, 20007, United States

Location

Children's National Medical Center

Washington D.C., District of Columbia, 20010, United States

Location

UF Health Shands Hospital

Gainesville, Florida, 32610, United States

Location

Jackson Memorial- University of Miami Health System- Pediatrics

Miami, Florida, 33136, United States

Location

Nicklaus Children's Hospital (Miami Children's Hospital)

Miami, Florida, 33155, United States

Location

Florida Hospital

Orlando, Florida, 42803, United States

Location

All Children's Hospital Specialty Physicians

St. Petersburg, Florida, 33701, United States

Location

H. Lee Moffitt Cancer Center & Research Institute

Tampa, Florida, 33612, United States

Location

Childrens Healthcare of Atlanta

Atlanta, Georgia, 30322, United States

Location

Emory University Hospital

Atlanta, Georgia, 30322, United States

Location

Northside Hospital

Atlanta, Georgia, 30342, United States

Location

Kapi'olani Medical Center for Women and Children

Honolulu, Hawaii, 96826, United States

Location

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, 60611, United States

Location

Northwest Memorial Hospital

Chicago, Illinois, 60611, United States

Location

Rush University Medical Center

Chicago, Illinois, 60612, United States

Location

Pediatric Hematology/Oncology MC4060 - University of Chicago

Chicago, Illinois, 60637, United States

Location

Cardinal Bernardin Cancer-Loyola University Medical Center

Maywood, Illinois, 60153, United States

Location

Riley Hospital for Children

Indianapolis, Indiana, 46202, United States

Location

Indiana Blood and Marrow Transplantation Clinical Lab LLC/St. Francis Hospital

Indianapolis, Indiana, 46237, United States

Location

University of Iowa Hospitals & Clinics

Iowa City, Iowa, 52242, United States

Location

University of Kansas Cancer Center

Kansas City, Kansas, 66160, United States

Location

Pediatric Blood and Cancer Disorders Clinic

Louisville, Kentucky, 40202, United States

Location

University of Louisville Research Foundation

Louisville, Kentucky, 40202, United States

Location

Tulane University Hospital & Clinic (Tuhc) - Tulane Cancer Center Comprehensive Clinic (Tcccc)

New Orleans, Louisiana, 70112, United States

Location

Children's Hospital

New Orleans, Louisiana, 70118, United States

Location

University of Maryland - Greenebaum Cancer Center

Baltimore, Maryland, 21201, United States

Location

Johns Hopkins University

Baltimore, Maryland, 21287, United States

Location

National Institutes of Health

Bethesda, Maryland, 20892, United States

Location

Tufts Medical Center

Boston, Massachusetts, 02111, United States

Location

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

Location

Boston Children's Hospital DFCI/CHB-Pediatrics

Boston, Massachusetts, 02115, United States

Location

Dana-Farber Cancer Institute

Boston, Massachusetts, 02115, United States

Location

Beth Israel Deaconess Medical Center

Boston, Massachusetts, 02215, United States

Location

University of Michigan Health System

Ann Arbor, Michigan, 48109, United States

Location

Wayne State University/Children's Hospital of Michigan

Detroit, Michigan, 48201, United States

Location

Henry Ford Hospital

Detroit, Michigan, 48202, United States

Location

Helen DeVos Children's Hospital - Spectrum Health

Grand Rapids, Michigan, 49503, United States

Location

Children's Hospitals and Clinics of Minnesota and Minneapolis

Minneapolis, Minnesota, 55404, United States

Location

University of Minnesota Medical Center

Minneapolis, Minnesota, 55455, United States

Location

Mayo Clinic

Rochester, Minnesota, 55905, United States

Location

University of Mississippi Medical Center

Jackson, Mississippi, 39216, United States

Location

Children's Mercy Hospital and Clinics - Infectious Diseases

Kansas City, Missouri, 64108, United States

Location

Cardinal Glennon Children's Medical Center/St. Louis University Department of Pediatrics

St Louis, Missouri, 63104, United States

Location

Washington University/St. Louis Children's Hospital

St Louis, Missouri, 63110, United States

Location

University of Nebraska Medical Center

Omaha, Nebraska, 68198, United States

Location

Hackensack University Medical Center - Joseph M. Sanzari Childrens Hospital

Hackensack, New Jersey, 07601, United States

Location

Rutgers Cancer Institute of New Jersey

New Brunswick, New Jersey, 08903, United States

Location

Presbyterian Hospital

Albuquerque, New Mexico, 87106, United States

Location

Roswell Park Cancer Institute

Buffalo, New York, 14263, United States

Location

Steven and Alexandra Cohen Children's Medical Center

New Hyde Park, New York, 11040, United States

Location

New York University School of Medicine

New York, New York, 10016, United States

Location

Memorial Sloan Kettering Cancer Center

New York, New York, 10021, United States

Location

Mount Sinai Hospital - BMT Program

New York, New York, 10029, United States

Location

Mount Sinai Medical Center

New York, New York, 10029, United States

Location

Morgan Stanley Children's Hospital - Columbia University Medical Center

New York, New York, 10032, United States

Location

Weill Cornell Medical College - New York Presbyterian Hospital

New York, New York, 10065, United States

Location

University of Rochester Medical Center, Strong Memorial Hospital

Rochester, New York, 14642, United States

Location

Stony Brook University Hospital

Stony Brook, New York, 11794, United States

Location

Montefiore Medical Center

The Bronx, New York, 10467, United States

Location

New York Medical College

Valhalla, New York, 10595, United States

Location

The University of North Carolina at Chapel Hill

Chapel Hill, North Carolina, 27599, United States

Location

Levine Children's Hospital

Charlotte, North Carolina, 28203, United States

Location

Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

Wake Forest Baptist Health

Winston-Salem, North Carolina, 27157, United States

Location

Children's Hospital Medical

Akron, Ohio, 44308, United States

Location

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, 45229, United States

Location

The Jewish Hospital

Cincinnati, Ohio, 45236, United States

Location

Case Western Reserve University (Cwru) - University Hospitals of Cleveland (Uhc)

Cleveland, Ohio, 44106, United States

Location

Robert J Tomsich Pathology & Laboratory Medicine Institute

Cleveland, Ohio, 44195, United States

Location

Nationwide Children's Hospital - Ohio State University College of Medicine (OSUCOM)

Columbus, Ohio, 43205, United States

Location

The Ohio State University, James Cancer Hospital

Columbus, Ohio, 43210, United States

Location

The University of Oklahoma Health Science Center

Oklahoma City, Oklahoma, 73104, United States

Location

Doernbecher Children's Hospital - Oregon Health and Science University

Portland, Oregon, 97239, United States

Location

Oregon Health and Science University

Portland, Oregon, 97239, United States

Location

Geisinger Medical Center

Danville, Pennsylvania, 17822, United States

Location

Milton S. Hershey Medical Center

Hershey, Pennsylvania, 17033, United States

Location

The Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, 15219, United States

Location

West Penn Allegheny Health System

Pittsburgh, Pennsylvania, 15224, United States

Location

Medical University of South Carolina

Charleston, South Carolina, 29425, United States

Location

Greenville Health System Cancer Institute

Greenville, South Carolina, 29605, United States

Location

Avera Cancer Institute

Sioux Falls, South Dakota, 57105, United States

Location

Methodist University Hospital

Memphis, Tennessee, 38104, United States

Location

St. Jude Children's Research Hospital - Department of Bone Marrow Transplantation and Cellular Therapy

Memphis, Tennessee, 38105, United States

Location

The Children's Hospital at TriStar Centennial

Nashville, Tennessee, 37203, United States

Location

Vanderbilt Ingram Cancer Center

Nashville, Tennessee, 37232, United States

Location

Children's Medical Center of Dallas

Dallas, Texas, 75235, United States

Location

San Antonio Military Medical Center

Fort Sam Houston, Texas, 78234, United States

Location

Cook Children's Health Care Hospital

Fort Worth, Texas, 76104, United States

Location

Baylor College of Medicine

Houston, Texas, 77030, United States

Location

Texas Children's Hospital

Houston, Texas, 77030, United States

Location

The University of Texas - MD Anderson Cancer Center

Houston, Texas, 77030, United States

Location

University of Texas MD Anderson Cancer Center

Houston, Texas, 77030, United States

Location

Methodist Healthcare System of San Antonio

San Antonio, Texas, 78229, United States

Location

University of Utah

Salt Lake City, Utah, 84132, United States

Location

University of Virginia Health System

Charlottesville, Virginia, 22908, United States

Location

Children's Hospital of the King's Daughter

Norfolk, Virginia, 23507, United States

Location

Virginia Commonwealth University

Richmond, Virginia, 23298, United States

Location

Fred Hutchinson Cancer Research Center/Seattle Children Hospital

Seattle, Washington, 98109, United States

Location

Providence Sacred Heart Medical Center and Children's Hospital

Spokane, Washington, 99204, United States

Location

Mary Babb Randolph Cancer Center - West Virginia University Hospital

Morgantown, West Virginia, 26505, United States

Location

University of Wisconsin, American Family Children's Hospital, Medical School

Madison, Wisconsin, 53792, United States

Location

Medical College of Wisconsin/ Children's Hospitalof Wisconsin

Milwaukee, Wisconsin, 53226, United States

Location

Related Publications (3)

  • Richardson PG, Murakami C, Jin Z, Warren D, Momtaz P, Hoppensteadt D, Elias AD, Antin JH, Soiffer R, Spitzer T, Avigan D, Bearman SI, Martin PL, Kurtzberg J, Vredenburgh J, Chen AR, Arai S, Vogelsang G, McDonald GB, Guinan EC. Multi-institutional use of defibrotide in 88 patients after stem cell transplantation with severe veno-occlusive disease and multisystem organ failure: response without significant toxicity in a high-risk population and factors predictive of outcome. Blood. 2002 Dec 15;100(13):4337-43. doi: 10.1182/blood-2002-04-1216. Epub 2002 Aug 1.

  • Richardson PG, Smith AR, Kernan NA, Lehmann L, Ryan RJ, Grupp SA. Analysis of Time to Complete Response after Defibrotide Initiation in Patients with Hepatic Veno-Occlusive Disease/Sinusoidal Obstruction Syndrome after Hematopoietic Cell Transplantation. Transplant Cell Ther. 2021 Jan;27(1):88.e1-88.e6. doi: 10.1016/j.bbmt.2020.09.008. Epub 2020 Sep 17.

  • Kernan NA, Grupp S, Smith AR, Arai S, Triplett B, Antin JH, Lehmann L, Shore T, Ho VT, Bunin N, Iacobelli M, Liang W, Hume R, Tappe W, Soiffer R, Richardson P. Final results from a defibrotide treatment-IND study for patients with hepatic veno-occlusive disease/sinusoidal obstruction syndrome. Br J Haematol. 2018 Jun;181(6):816-827. doi: 10.1111/bjh.15267. Epub 2018 May 16.

MeSH Terms

Conditions

Hepatic Veno-Occlusive Disease

Interventions

defibrotide

Condition Hierarchy (Ancestors)

Liver DiseasesDigestive System DiseasesVascular DiseasesCardiovascular Diseases

Results Point of Contact

Title
Associate Director, Clinical Trial Disclosure & Transparency
Organization
Jazz Pharmaceuticals

Study Officials

  • William Tappe, M.D.

    Jazz Pharmaceuticals

    STUDY CHAIR
  • Paul Richardson, M.D.

    Dana-Farber Cancer Institute

    PRINCIPAL INVESTIGATOR

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
No

Study Design

Study Type
interventional
Phase
phase 3
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 25, 2008

First Posted

March 5, 2008

Study Start

December 1, 2007

Primary Completion

July 1, 2016

Study Completion

September 1, 2016

Last Updated

November 30, 2017

Results First Posted

November 30, 2017

Record last verified: 2017-11

Locations