NCT00272948

Brief Summary

The aim of this trial is to evaluate whether the prophylactic use of Defibrotide (DF) in pediatric patients (age less than 18 years) undergoing stem cell transplantation and who are at high risk of developing hepatic Veno-occlusive Disease (VOD) will have an impact on the incidence and severity of the disease. Patients will be randomly assigned to one of two treatment arms: Those allocated to the Prophylactic Arm will receive the study drug (Defibrotide) from the day of conditioning onwards. Patients allocated to the Control Arm will receive the study drug (Defibrotide) from the day that VOD is diagnosed.

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
360

participants targeted

Target at P75+ for phase_2

Timeline
Completed

Started Dec 2005

Typical duration for phase_2

Geographic Reach
10 countries

30 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

December 1, 2005

Completed
1 month until next milestone

First Submitted

Initial submission to the registry

January 4, 2006

Completed
5 days until next milestone

First Posted

Study publicly available on registry

January 9, 2006

Completed
3 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

January 1, 2009

Completed
6 months until next milestone

Study Completion

Last participant's last visit for all outcomes

July 1, 2009

Completed
Last Updated

June 9, 2011

Status Verified

June 1, 2011

Enrollment Period

3.1 years

First QC Date

January 4, 2006

Last Update Submit

June 8, 2011

Conditions

Keywords

Venoocclusive diseasePediatricmyeloablative conditioningstem cell transplant

Outcome Measures

Primary Outcomes (1)

  • The primary objective is to evaluate if prophylactic DF has an impact on the incidence of VOD

    Day + 30 post HSCT

Secondary Outcomes (1)

  • Occurrence of Multi-System Organ Failure and Survival (all causes of mortality)

    day +100 post HSCT

Study Arms (2)

Prophylaxis Arm

EXPERIMENTAL
Drug: Defibrotide

Control Arm

ACTIVE COMPARATOR
Drug: Defibrotide

Interventions

Defibrotide 25 mg/kg/d

Control ArmProphylaxis Arm

Eligibility Criteria

AgeUp to 18 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Age \<18 years
  • myeloablative conditioning and autologous or allogeneic stem cell transplantation with at least one of the following risk factors for VOD:
  • Pre-existing liver disease
  • Second myeloablative HSCT
  • History of treatment with gemtuzumab ozogamicin (MYLOTARGÒ, GO, CMA-676, Wyeth)
  • Allogeneic HSCT for leukemia beyond the second relapse
  • Osteopetrosis (OP)
  • Conditioning with busulfan and melphalan
  • Macrophage activating syndromes (MAS, like hemophagocytic lymphohistiocytosis, Griscelli, Chediak-Higashi
  • Adrenoleukodystrophy (ALD)

You may not qualify if:

  • Pregnant patients
  • Patients who are transplanted but do not fulfill any of the above mentioned criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (30)

University Hospital

Graz, Austria

Location

St Anna Kinderspital

Vienna, Austria

Location

Inst. Gustave Roussy

Villejuif, France

Location

University Hospital

Dresden, Germany

Location

Klinik Kinder-Onkologie

Düsseldorf, Germany

Location

Johann-Wolfgang Goethe Universität

Frankfurt, Germany

Location

Universitätsspital Eppendorf

Hamburg, Germany

Location

Medical School

Hanover, Germany

Location

University Hospital

Heidelberg, Germany

Location

Kinderklinik

Jena, Germany

Location

Christian-Albrecht -University

Kiel, Germany

Location

Kinderpoliklinik Uni

München, Germany

Location

Poliklinik Kinderheilkunde

Münster, Germany

Location

Universitätsspital

Tübingen, Germany

Location

Our Lady's Hospital for Sick Children

Dublin, Ireland

Location

Schneider Children's MC

Petah Tikva, Israel

Location

Institute G. Gaslini

Genova, Italy

Location

Ospedale S. Gerardo

Monza, Italy

Location

Clinica di Oncoematologia Pediatrica

Padua, Italy

Location

University Hospital

Utrecht, Netherlands

Location

Sahlgrenska University Hospital

Gothenburg, Sweden

Location

University Hospital

Huddinge, Sweden

Location

University Hospital

Lund, Sweden

Location

University Hospital

Uppsala, Sweden

Location

University Children Hospital

Basel, Switzerland

Location

Inselspital

Bern, Switzerland

Location

Hopital Cantonal Universitaire

Geneva, Switzerland

Location

University Hospital

Zurich, Switzerland

Location

Great Ormond Street Hospital

London, United Kingdom

Location

Children's Hospital

Manchester, United Kingdom

Location

Related Publications (2)

  • Corbacioglu S, Grupp SA, Richardson PG, Duarte R, Pagliuca A, Ruutu T, Mahadeo K, Carreras E. Prevention of veno-occlusive disease/sinusoidal obstruction syndrome: a never-ending story and no easy answer. Bone Marrow Transplant. 2023 Aug;58(8):839-841. doi: 10.1038/s41409-023-02007-2. Epub 2023 May 25. No abstract available.

  • Corbacioglu S, Cesaro S, Faraci M, Valteau-Couanet D, Gruhn B, Rovelli A, Boelens JJ, Hewitt A, Schrum J, Schulz AS, Muller I, Stein J, Wynn R, Greil J, Sykora KW, Matthes-Martin S, Fuhrer M, O'Meara A, Toporski J, Sedlacek P, Schlegel PG, Ehlert K, Fasth A, Winiarski J, Arvidson J, Mauz-Korholz C, Ozsahin H, Schrauder A, Bader P, Massaro J, D'Agostino R, Hoyle M, Iacobelli M, Debatin KM, Peters C, Dini G. Defibrotide for prophylaxis of hepatic veno-occlusive disease in paediatric haemopoietic stem-cell transplantation: an open-label, phase 3, randomised controlled trial. Lancet. 2012 Apr 7;379(9823):1301-9. doi: 10.1016/S0140-6736(11)61938-7. Epub 2012 Feb 23.

Related Links

MeSH Terms

Conditions

Hepatic Veno-Occlusive Disease

Interventions

defibrotide

Condition Hierarchy (Ancestors)

Liver DiseasesDigestive System DiseasesVascular DiseasesCardiovascular Diseases

Study Officials

  • Selim Corbacioglu, MD

    University of Ulm, Germany

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
NONE
Purpose
PREVENTION
Intervention Model
PARALLEL
Sponsor Type
NETWORK

Study Record Dates

First Submitted

January 4, 2006

First Posted

January 9, 2006

Study Start

December 1, 2005

Primary Completion

January 1, 2009

Study Completion

July 1, 2009

Last Updated

June 9, 2011

Record last verified: 2011-06

Locations