NCT05284929

Brief Summary

Pemphigus is a rare autoimmune life-threatening blistering condition affecting skin and mucous membranes. Pemphigus belongs to a family of polygenic disorders. Several different genes encoding molecules regulate pemphigus autoimmunity. Many trials focused on HLA investigation. Increased levels of certain HLA class II alleles frequencies in pemphigus have been reported in various populations. However, they were not investigated in the Russian population. The aim of our study is to investigate HLA class II alleles and haplotypes in Russian patients with pemphigus. Methods Patients and controls We are recruiting 120 patients with pemphigus. The diagnosis was based on clinical and histopathological findings and confirmed by immunofluorescent techniques (direct and indirect immunofluorescent tests). Before sampling, written consent was obtained from each subject. A single blood sample for HLA typing was obtained from all subjects. This study has been approved by the Ethics Committee of Sechenov University, Russia. Phenotypic and allelic frequencies were compared with healthy blood donors (n=100) registered in Sechenov University blood center.

Trial Health

43
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Enrollment
120

participants targeted

Target at P50-P75 for all trials

Timeline
Completed

Started May 2017

Longer than P75 for all trials

Geographic Reach
1 country

1 active site

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

Study Start

First participant enrolled

May 17, 2017

Completed
4.8 years until next milestone

First Submitted

Initial submission to the registry

March 10, 2022

Completed
7 days until next milestone

First Posted

Study publicly available on registry

March 17, 2022

Completed
8 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

November 17, 2022

Completed
4 months until next milestone

Study Completion

Last participant's last visit for all outcomes

March 17, 2023

Completed
Last Updated

March 17, 2022

Status Verified

March 1, 2022

Enrollment Period

5.5 years

First QC Date

March 10, 2022

Last Update Submit

March 10, 2022

Conditions

Outcome Measures

Primary Outcomes (1)

  • Estimation of HLA-DRB1 and HLA-DQB1 alleles frequencies in PV patients and controls

    The frequencies of HLA alleles will be counted directly from genotyping data, while the frequencies of haplotypes will be estimated with an expectation-maximization algorithm using the ARLEQUIN software package (version 3.11), leading to maximum-likelihood estimates of gene frequencies. To compare the differences between frequencies in the donor and patient groups the Fisher exact test will be performed.

    May 2017 - 2023

Study Arms (2)

Patients with pemphigus

Genetic: A single blood sample for HLA typing

Healthy controls

Genetic: A single blood sample for HLA typing

Interventions

Extracting of DNA from the blood sample using PCR-reaction

Healthy controlsPatients with pemphigus

Eligibility Criteria

Sexall
Healthy VolunteersYes
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

120 patients with confirmed diagnosis of pemphigus will be enrolled in the study Age \>18 years Sex: both females and males 100 healthy controls

You may qualify if:

  • Signed informed consent
  • Age of patients \>18 years
  • Confirmed diagnosis

You may not qualify if:

  • No as pemphigus is a life-threatening condition

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Sechenov University

Moscow, 119991, Russia

RECRUITING

MeSH Terms

Conditions

PemphigusPemphigoid, BullousStevens-Johnson Syndrome

Interventions

Histocompatibility Testing

Condition Hierarchy (Ancestors)

Skin Diseases, VesiculobullousSkin DiseasesSkin and Connective Tissue DiseasesAutoimmune DiseasesImmune System DiseasesStomatitisMouth DiseasesStomatognathic DiseasesDrug EruptionsDermatitisErythema MultiformeErythemaHypersensitivity, DelayedHypersensitivityDrug HypersensitivityDrug-Related Side Effects and Adverse ReactionsChemically-Induced Disorders

Intervention Hierarchy (Ancestors)

Immunologic TestsClinical Laboratory TechniquesDiagnostic Techniques and ProceduresDiagnosisInvestigative TechniquesImmunologic Techniques

Study Design

Study Type
observational
Observational Model
CASE CONTROL
Time Perspective
RETROSPECTIVE
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

March 10, 2022

First Posted

March 17, 2022

Study Start

May 17, 2017

Primary Completion

November 17, 2022

Study Completion

March 17, 2023

Last Updated

March 17, 2022

Record last verified: 2022-03

Locations