NCT05135663

Brief Summary

This is the extension study of NS-089/NCNP-02 (Study NCNP/DMT02), which is designed to assess the safety, tolerability and efficacy of NS-089/NCNP-02 in patients with Duchenne muscular dystrophy (DMD).

Trial Health

75
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
6

participants targeted

Target at below P25 for phase_2

Timeline
12mo left

Started Jun 2021

Longer than P75 for phase_2

Geographic Reach
1 country

2 active sites

Status
active not recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress83%
Jun 2021Apr 2027

Study Start

First participant enrolled

June 23, 2021

Completed
3 months until next milestone

First Submitted

Initial submission to the registry

October 5, 2021

Completed
2 months until next milestone

First Posted

Study publicly available on registry

November 26, 2021

Completed
5.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 30, 2027

Expected
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

April 30, 2027

Last Updated

July 20, 2025

Status Verified

July 1, 2025

Enrollment Period

5.9 years

First QC Date

October 5, 2021

Last Update Submit

July 16, 2025

Conditions

Outcome Measures

Primary Outcomes (1)

  • Incidence of adverse events

    Up to Week 319

Secondary Outcomes (10)

  • Expression of dystrophin protein (Western blot)

    Week 99

  • Percentage of exon 44-skipped mRNA of dystrophin

    Week 99

  • North Star Ambulatory Assessment (NSAA)

    Up to Week 315

  • Time to stand test

    Up to Week 315

  • Time to run/walk 10 meters test

    Up to Week 315

  • +5 more secondary outcomes

Study Arms (2)

NS-089/NCNP-02 40 mg/kg

EXPERIMENTAL
Drug: NS-089/NCNP-02

NS-089/NCNP-02 80 mg/kg

EXPERIMENTAL
Drug: NS-089/NCNP-02

Interventions

The same dose administered in as Part 2 of Study NCNP/DMT02 (40 mg/kg) will be administered once weekly for 288 weeks (The total treatment period is 312 weeks including Part2 of Study NCNP/DMT02).

Also known as: Brogidirsen
NS-089/NCNP-02 40 mg/kg

Eligibility Criteria

Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Patient completed Study NCNP/DMT02

You may not qualify if:

  • Patient had any serious adverse events in Study NCNP/DMT02 that, in the opinion of the Investigator and/or Sponsor, was probably or definitely related to NS-089/NCNP-02 use and precludes safe use of NS-089/NCNP-02 for the patient in this study.
  • Patient had a treatment which was made for the purpose of dystrophin or dystrophin-related protein induction after completion of Study NCNP/DMT02.
  • Patient took any other investigational drugs after completion of Study NCNP/DMT02.
  • Patient was judged by the investigator and/or the Sponsor that it was not appropriate to participate in the extension study for other reasons.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (2)

Kagoshima University Hospital

Kagoshima, Japan

Location

National Center of Neurology and Psychiatry

Tokyo, Japan

Location

MeSH Terms

Conditions

Muscular Dystrophy, Duchenne

Condition Hierarchy (Ancestors)

Muscular DystrophiesMuscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

October 5, 2021

First Posted

November 26, 2021

Study Start

June 23, 2021

Primary Completion (Estimated)

April 30, 2027

Study Completion (Estimated)

April 30, 2027

Last Updated

July 20, 2025

Record last verified: 2025-07

Locations