NCT01540409

Brief Summary

The primary objective of this study is to assess the ongoing efficacy, safety, and tolerability of an additional 212 weeks of treatment with eteplirsen injection in Duchenne muscular dystrophy (DMD) subjects who have successfully completed the 28 week eteplirsen study: Study 4658-us-201. This study will also evaluate the correlation between biomarkers for DMD and the clinical status of participating DMD subjects.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
12

participants targeted

Target at below P25 for phase_2

Timeline
Completed

Started Feb 2012

Longer than P75 for phase_2

Geographic Reach
1 country

11 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

February 23, 2012

Completed
4 days until next milestone

Study Start

First participant enrolled

February 27, 2012

Completed
1 day until next milestone

First Posted

Study publicly available on registry

February 28, 2012

Completed
4.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 15, 2016

Completed
1.3 years until next milestone

Study Completion

Last participant's last visit for all outcomes

August 16, 2017

Completed
1.9 years until next milestone

Results Posted

Study results publicly available

July 10, 2019

Completed
Last Updated

March 30, 2020

Status Verified

March 1, 2020

Enrollment Period

4.1 years

First QC Date

February 23, 2012

Results QC Date

June 20, 2019

Last Update Submit

March 26, 2020

Conditions

Keywords

DMD, Duchenne, Eteplirsen, dystrophy, dystrophin, exon 51

Outcome Measures

Primary Outcomes (2)

  • Change From Baseline in the 6 Minute Walk Test (6MWT) at Week 240

    This study used a modified version of the 6MWT test procedure described in American Thoracic Society (ATS) 2002 guidelines, specifically adapted for patients with Duchenne muscular dystrophy. The participant was asked to walk a set course of 25 meters for 6 minutes (timed) and the distance walked in meters was recorded. Increases from baseline in 6MWT distance are indicative of improvement and decreases from baseline indicate worsening. Baseline here corresponds to the baseline in the parent study (4658-us-201, NCT01396239).

    Parent Baseline and Week 240

  • Change From Baseline in the Percentage of Dystrophin Positive Fibers (PDPF) at Week 48

    Dystrophin expression as assessed by percent dystrophin positive fibers was measured by immunohistochemistry (IHC) technique using primary anti-dystrophin antibody. Percent change from baseline is the arithmetic difference of the treatment time point minus baseline divided by baseline calculated for individual subjects. Baseline here corresponds to the baseline in the parent study (4658-us-201, NCT01396239).

    Parent Baseline and Week 48

Study Arms (1)

AVI-4658 (Eteplirsen)

EXPERIMENTAL

Multiple-Dose Extension Study

Drug: AVI-4658 (Eteplirsen)

Interventions

Eteplirsen will be administered once weekly via an IV infusion. There are two treatment groups, 30 mg/kg and 50 mg/kg.

Also known as: EXONDYS 51
AVI-4658 (Eteplirsen)

Eligibility Criteria

Age7 Years - 13 Years
Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17)

You may qualify if:

  • A subject must meet all of the following criteria to be eligible for this study.
  • The subject and/or their parent/legal guardian are willing and able to provide signed informed consent.
  • The subject has successfully completed 28 weeks of treatment in Study 4658-US-201.
  • The subject has a parent(s) or legal guardian(s) who is able to understand and comply with all of the study procedure requirements.

You may not qualify if:

  • A subject who meets any of the following criteria will be excluded from this study.
  • \. The subject has a prior or ongoing medical condition that, in the Investigator's opinion, could adversely affect the safety of the subject or make it unlikely that the course of treatment or follow-up would be completed or impair the assessment of study results.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (11)

Miller Children's Hospital

Long Beach, California, 90806, United States

Location

University of Florida Clinical Research Center

Gainesville, Florida, 32610, United States

Location

Rush University Medical Center

Chicago, Illinois, 60612, United States

Location

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

Location

Washington University Medical School

St Louis, Missouri, 63110, United States

Location

Summerwood Pediatrics/Infusacare Medical Services

Liverpool, New York, 13088, United States

Location

Levine Children's Hospital

Charlotte, North Carolina, 28203, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, 43205, United States

Location

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, 15224, United States

Location

Children's Specialty Group, Pediatric Neurology

Norfolk, Virginia, 23510, United States

Location

Osceola Medical Center

Osceola, Wisconsin, 54020, United States

Location

Related Publications (1)

  • Mendell JR, Goemans N, Lowes LP, Alfano LN, Berry K, Shao J, Kaye EM, Mercuri E; Eteplirsen Study Group and Telethon Foundation DMD Italian Network. Longitudinal effect of eteplirsen versus historical control on ambulation in Duchenne muscular dystrophy. Ann Neurol. 2016 Feb;79(2):257-71. doi: 10.1002/ana.24555. Epub 2016 Jan 8.

Related Links

MeSH Terms

Conditions

Muscular Dystrophy, Duchenne

Interventions

eteplirsen

Condition Hierarchy (Ancestors)

Muscular DystrophiesMuscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Results Point of Contact

Title
Medical Director
Organization
Sarepta Therapeutics, Inc.

Study Officials

  • Medical Director

    Sarepta Therapeutics, Inc.

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 23, 2012

First Posted

February 28, 2012

Study Start

February 27, 2012

Primary Completion

April 15, 2016

Study Completion

August 16, 2017

Last Updated

March 30, 2020

Results First Posted

July 10, 2019

Record last verified: 2020-03

Locations