NCT03591094

Brief Summary

The study population is comprised of adult subjects with cystic fibrosis (CF) who are homozygous for the F508del mutation and are currently receiving background treatment with tezacaftor/ivacaftor for a minimum of 1 month prior to Day 1. The planned sample size is approximately 40 subjects. 20 subjects will be assigned to PTI-428 dose level 1 or placebo and 20 subjects will be assigned to PTI-428 dose level 2 or placebo. At each dose level, subjects will be randomized at a 3:1 randomization ratio. Subjects will receive once daily oral doses of PTI-428 or placebo for 28 days, while the subjects continue to receive background treatment with tezacaftor/ivacaftor per product label. The study drug administration period will be followed by a 14-day safety follow-up period.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
40

participants targeted

Target at P25-P50 for phase_2

Timeline
Completed

Started Aug 2018

Shorter than P25 for phase_2

Geographic Reach
1 country

26 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

July 6, 2018

Completed
12 days until next milestone

First Posted

Study publicly available on registry

July 18, 2018

Completed
1 month until next milestone

Study Start

First participant enrolled

August 21, 2018

Completed
6 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

February 18, 2019

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

February 18, 2019

Completed
Last Updated

February 27, 2020

Status Verified

February 1, 2020

Enrollment Period

6 months

First QC Date

July 6, 2018

Last Update Submit

February 25, 2020

Conditions

Outcome Measures

Primary Outcomes (1)

  • Number of subjects with treatment-emergent adverse events (TEAEs)

    Safety and tolerability will be assessed by adverse events (AEs), safety labs, electrocardiograms (ECGs), physical examinations and vital signs.

    Baseline through Day 42

Secondary Outcomes (5)

  • Maximum plasma concentration (Cmax)

    28 days

  • Time of Cmax (Tmax)

    28 days

  • Area under the concentration time curve from time 0 to time of last measurable concentration (AUC0-t)

    28 days

  • Change in FEV1 over time

    Baseline through Day 42

  • Change in sweat chloride over time

    Baseline through Day 42

Other Outcomes (5)

  • Change in nasal epithelial CFTR mRNA and protein expression over time

    Baseline through Day 42

  • Change in CFQ-R over time

    Baseline through Day 42

  • Cmax of PTI-428 metabolites, if applicable

    28 days

  • +2 more other outcomes

Study Arms (3)

PTI-428 dose level 1

ACTIVE COMPARATOR
Drug: PTI-428

PTI-428 dose level 2

ACTIVE COMPARATOR
Drug: PTI-428

Placebo PTI-428

PLACEBO COMPARATOR
Drug: Placebo

Interventions

Active

PTI-428 dose level 1PTI-428 dose level 2

Placebo

Placebo PTI-428

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Confirmed diagnosis of CF with the F508del/F508del genotype on record
  • On tezacaftor/ivacaftor dosing for both label indication and per label dosing for a minimum of 1 month on Day 1
  • Forced expiratory volume in 1 second (FEV1) 40-90% predicted, inclusive
  • Clinically stable with no significant changes in health status within 14 days of Day 1
  • Non-smoker and non-tobacco user for a minimum of 28 days prior to screening and for the duration of the study

You may not qualify if:

  • Participation in another clinical trial or treatment with an investigational agent within 28 days or 5 half-lives, whichever is longer, prior to Study Day 1
  • History of cancer within the past 5 years (excluding cervical cancer in situ with curative therapy for at least one year prior to screening and non-melanoma skin cancer)
  • History of organ transplantation
  • Hospitalization, sinopulmonary infection, CF exacerbation, or other clinically significant infection or illness (as determined by the investigator) requiring an increase or addition of medication, such as antibiotics or corticosteroids, within 14 days of Day 1
  • Initiation of any new chronic therapy (e.g., ibuprofen, hypertonic saline, azithromycin, Pulmozyme®, Cayston®, TOBI®)) or any change in chronic therapy (excluding pancreatic enzyme replacement therapy) within 28 days prior to Day 1
  • History or current evidence of alcohol or drug abuse or dependence within 12 months of screening as determined by the investigator
  • Pregnant or nursing women

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (26)

University of Alabama at Birmingham

Birmingham, Alabama, 35233, United States

Location

University of Arizona

Tucson, Arizona, 85724, United States

Location

Stanford University

Stanford, California, 94305, United States

Location

National Jewish Health

Denver, Colorado, 80206, United States

Location

Central Florida Pulmonary Group

Altamonte Springs, Florida, 32701, United States

Location

Northwestern University

Chicago, Illinois, 60611, United States

Location

Cystic Fibrosis Center, Children's Hospital of Illinois at OSF Saint Francis Medical Center

Peoria, Illinois, 61637, United States

Location

University of Iowa, Roy J and Lucille A Carver College of Medicine

Iowa City, Iowa, 52242, United States

Location

Universitey of Louisville, Kosair Charities Pediatric Clinical Research Unit

Louisville, Kentucky, 40202, United States

Location

Maine Medical Center

Portland, Maine, 04102, United States

Location

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

Location

Boston Children's Hospital

Boston, Massachusetts, 02115, United States

Location

Michigan Medicine, University of Michigan

Ann Arbor, Michigan, 48109, United States

Location

University of Minnesota

Minneapolis, Minnesota, 55455, United States

Location

Children's Mercy Hospital

Kansas City, Missouri, 64108, United States

Location

Dartmouth Hitchcock Medical Center

Manchester, New Hampshire, 03104, United States

Location

Mount Sinai Beth Israel

New York, New York, 10003, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

New York Medical College

Valhalla, New York, 10595, United States

Location

Duke University Medical Center

Durham, North Carolina, 27710, United States

Location

Akron Children's Hospital

Akron, Ohio, 44308, United States

Location

Nationwide Children's Hospital

Columbus, Ohio, 43205, United States

Location

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, 15224, United States

Location

Medical University of South Carolina

Charleston, South Carolina, 29425, United States

Location

The University of Texas Health Science Center at Tyler - Center for Clinical Research

Tyler, Texas, 75708, United States

Location

University of Utah

Salt Lake City, Utah, 84132, United States

Location

MeSH Terms

Conditions

Cystic Fibrosis

Condition Hierarchy (Ancestors)

Pancreatic DiseasesDigestive System DiseasesLung DiseasesRespiratory Tract DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesInfant, Newborn, Diseases

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

July 6, 2018

First Posted

July 18, 2018

Study Start

August 21, 2018

Primary Completion

February 18, 2019

Study Completion

February 18, 2019

Last Updated

February 27, 2020

Record last verified: 2020-02

Data Sharing

IPD Sharing
Will not share

Locations