NCT03132337

Brief Summary

The goal of this is to learn more about stem cell transplant and complications that some people have after their transplants, in particular sinusoidal obstruction syndrome (SOS), also called veno-occlusive disease of the liver.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
80

participants targeted

Target at P50-P75 for all trials

Timeline
Completed

Started Apr 2017

Typical duration for all trials

Geographic Reach
1 country

4 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

April 1, 2017

Completed
23 days until next milestone

First Submitted

Initial submission to the registry

April 24, 2017

Completed
3 days until next milestone

First Posted

Study publicly available on registry

April 27, 2017

Completed
3.7 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

January 14, 2021

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

January 14, 2021

Completed
Last Updated

December 19, 2023

Status Verified

December 1, 2023

Enrollment Period

3.8 years

First QC Date

April 24, 2017

Last Update Submit

December 18, 2023

Conditions

Outcome Measures

Primary Outcomes (1)

  • SOS proteomic markers

    Measure for 3 SOS proteomic markers, L-Ficolin, HA, and ST2, as early predictors of SOS incidence through study completion.

    Until the end of the study evaluation, day 180

Study Arms (1)

Stem Cell Transplant

Serial Blood Draws

Other: Serial Blood Draws

Interventions

Day 0 and Day 3 blood draw for SOS biomarkers. If subject develops SOS blood draw prior to dose of Defibrotide, Day 14 after Defibrotide and Day 21 after Defibrotide.

Stem Cell Transplant

Eligibility Criteria

AgeUp to 25 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)
Sampling MethodProbability Sample
Study Population

Stem Cell Transplant patients

You may qualify if:

  • Age ≤ 25 years undergoing HCT for any reason who fulfill any ONE (1) of the following criteria:
  • History of hepatic disease as defined by:
  • Viral hepatitis (i.e., hepatitis C virus \[HCV\])
  • Liver tumor before HCT
  • Hepatic fibrosis or cirrhosis before HCT as proven by liver biopsy
  • High aspartate aminotransferase (AST) (\> 2x ULN) before HCT (pre-transplant evaluation)
  • High alanine transaminase (ALT) (\> 2x ULN) before HCT
  • High bilirubin (\> 1.2x ULN) before HCT
  • HCT high-risk features including:
  • a. Conditioning with high-risk modalities including: i. Busulfan (BU)-containing regimen particularly with oral BU + cyclophosphamide ii. TBI-containing regimen, particularly cyclophosphamide + total-body irradiation (TBI) b. ≥ 2 HCT c. Allo-HCT for leukemia \> or = second relapse d. Unrelated donor (URD) HCT e. Human leukocyte antigen (HLA) mismatch HCT (less than 10 of 10 for bone marrow/peripheral blood stem cell \[BM/PBSC\] or anything less than 6 of 6 for UCB) f. Use of sirolimus + tacrolimus prophylaxis for GVHD
  • High-risk disease states including:
  • Juvenile myelo-monocytic chronic leukemia (JMML)
  • Primary hemophagocytic lymphohistiocytosis (HLH)
  • Adrenoleukodystrophy
  • Osteopetrosis
  • +6 more criteria

You may not qualify if:

  • Patients who are transplanted but do not fulfill any of the above mentioned criteria.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (4)

Children's National Medical Center

Washington D.C., District of Columbia, 20010, United States

Location

Indiana University

Indianapolis, Indiana, 46202, United States

Location

University of Michigan

Ann Arbor, Michigan, 48109, United States

Location

Baylor College of Medicine

Houston, Texas, 77030, United States

Location

Related Publications (1)

  • Han Y, Bidgoli A, DePriest BP, Mendez A, Bijangi-Vishehsaraei K, Perez-Albuerne ED, Krance RA, Renbarger J, Skiles JL, Choi SW, Liu H, Paczesny S. Prospective assessment of risk biomarkers of sinusoidal obstruction syndrome after hematopoietic cell transplantation. JCI Insight. 2023 May 22;8(10):e168221. doi: 10.1172/jci.insight.168221.

Biospecimen

Retention: SAMPLES WITH DNA

Blood

MeSH Terms

Conditions

Hepatic Veno-Occlusive Disease

Condition Hierarchy (Ancestors)

Liver DiseasesDigestive System DiseasesVascular DiseasesCardiovascular Diseases

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
PROSPECTIVE
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Professor, Department of Pediatrics

Study Record Dates

First Submitted

April 24, 2017

First Posted

April 27, 2017

Study Start

April 1, 2017

Primary Completion

January 14, 2021

Study Completion

January 14, 2021

Last Updated

December 19, 2023

Record last verified: 2023-12

Data Sharing

IPD Sharing
Will not share

Locations