NCT03039686

Brief Summary

This is a multi-center, randomized, double-blind, placebo-controlled study to assess the efficacy, safety and tolerability of two different weekly doses of RO7239361 in ambulatory boys with Duchenne Muscular Dystrophy (DMD).

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
166

participants targeted

Target at P75+ for phase_2

Timeline
Completed

Started Jul 2017

Typical duration for phase_2

Geographic Reach
13 countries

44 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

January 27, 2017

Completed
5 days until next milestone

First Posted

Study publicly available on registry

February 1, 2017

Completed
5 months until next milestone

Study Start

First participant enrolled

July 6, 2017

Completed
2.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

April 28, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

April 28, 2020

Completed
8 months until next milestone

Results Posted

Study results publicly available

December 21, 2020

Completed
Last Updated

December 21, 2020

Status Verified

November 1, 2020

Enrollment Period

2.8 years

First QC Date

January 27, 2017

Results QC Date

October 21, 2020

Last Update Submit

November 25, 2020

Conditions

Keywords

muscular dystrophyDuchenne's Muscular DystrophyDMD

Outcome Measures

Primary Outcomes (2)

  • Baseline for the North Star Ambulatory Assessment (NSAA) Total Score

    The NSAA is a functional scale specifically designed for ambulant boys with Duchenne muscular dystrophy (DMD) that can provide information about motor function. The NSAA is a 17-item test of standing, ability to transition from lying to sitting, sitting to standing, and other mobility assessments. Each of the 17 items is evaluated on an ordinal scale of 0-2: 0 = unable to achieve independently, 1 = modified method but achieves goal independent of physical assistance from another, or 2 = normal with no obvious modification of activity. Total score range is 0 to 34. Higher scores reflect better performance.

    Baseline

  • Change From Baseline in the North Star Ambulatory Assessment (NSAA) Total Score at Week 48

    The NSAA is a functional scale specifically designed for ambulant boys with Duchenne muscular dystrophy (DMD) that can provide information about motor function. The NSAA is a 17-item test of standing, ability to transition from lying to sitting, sitting to standing, and other mobility assessments. Each of the 17 items is evaluated on an ordinal scale of 0-2: 0 = unable to achieve independently, 1 = modified method but achieves goal independent of physical assistance from another, or 2 = normal with no obvious modification of activity. Total score range is 0 to 34. Higher scores reflect better performance. A positive change from baseline indicates an improvement. Based on the mixed-effect model of repeated measures (MMRM).

    Baseline, Week 48

Secondary Outcomes (15)

  • Baseline Time for 4 Stair Climb

    Baseline

  • Change From Baseline at Week 48 in 4 Stair Climb Velocity (4SCV)

    Baseline, Week 48

  • Baseline for the Time to Stand From Supine

    Baseline

  • Change From Baseline at Week 48 in Stand From Supine Velocity

    Baseline, Week 48

  • Baseline Time for 10 Meter Walk/Run

    Baseline

  • +10 more secondary outcomes

Study Arms (3)

RO7239361 Low Dose

EXPERIMENTAL

Participants received low dose RO7239361 SC on specified days of the 48-week DB period. Following the DB period participants received low dose RO7239361 on specified days for up to 192 weeks during the open-label period followed by 24 weeks of follow-up.

Drug: RO7239361

RO7239361 High Dose

EXPERIMENTAL

Participants received high dose RO7239361 SC on specified days of the 48-week DB period. Following the DB period participants received high dose RO7239361 on specified days for up to 192 weeks during the open-label period followed by 24 weeks of follow-up.

Drug: RO7239361

Placebo

PLACEBO COMPARATOR

Participants received matching placebo solution subcutaneously (SC) on specified days of the 48-week double-blind (DB) period. Following the DB period participants received low dose or high dose RO7239361 on specified days for up to 192 weeks during the open-label period followed by 24 weeks of follow-up.

Drug: Placebo for RO7239361

Interventions

Take RO7239361 subcutaneously on specified days over a 48 week blinded period

RO7239361 High DoseRO7239361 Low Dose

Take placebo subcutaneously on specified days over a 48 week blinded period

Placebo

Eligibility Criteria

Age6 Years - 11 Years
Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17)

You may qualify if:

  • Diagnosed with DMD by confirmed medical history and genetic testing
  • Able to walk without assistance
  • Minimum North Star Ambulatory Assessment score of 15 at screening
  • Able to walk up 4 stairs in 8 seconds or less
  • Weigh at least 15 kg (33 lbs)
  • Taking corticosteroids for DMD

You may not qualify if:

  • Any behavior or mental issue that will affect the ability to complete the required study procedures
  • Previously or currently taking medications like androgens or human growth hormone
  • Use of a ventilator during the day
  • Unable to have blood samples collected or receive an injection under the skin
  • Concomitant or previous participation at any time in a gene therapy study

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (44)

Neuromuscular Research Center

Phoenix, Arizona, 85028, United States

Location

Stanford University

Palo Alto, California, 94304, United States

Location

University of California Davis Medical Center

Sacramento, California, 95817, United States

Location

Yale University School of Medicine ; Pulmonary & Critical Care

New Haven, Connecticut, 06510, United States

Location

University of Florida

Gainesville, Florida, 32607, United States

Location

Nemours Children's Hospital

Orlando, Florida, 32827, United States

Location

Rare Disease Research, LLC

Atlanta, Georgia, 30318, United States

Location

Rush University Medical Center - PPDS

Chicago, Illinois, 60612, United States

Location

University of Iowa

Iowa City, Iowa, 52242, United States

Location

University of Kansas Medical Center

Kansas City, Kansas, 66160, United States

Location

Kennedy Krieger Institute

Baltimore, Maryland, 21205, United States

Location

University of Massachusetts Memorial Childrens Medical Center; Department of Neurology

Worcester, Massachusetts, 01655, United States

Location

Saint Louis Children's Hospital

St Louis, Missouri, 63110, United States

Location

Las Vegas Clinic

Las Vegas, Nevada, 89145, United States

Location

Cincinnati Childrens Hospital Medical Center;Investigational Pharmacy

Cincinnati, Ohio, 45229, United States

Location

Nationwide Childrens Hospital; Research Institute at Nationwide Childrens Hospital

Columbus, Ohio, 43205, United States

Location

Seattle Children's Hospital

Seattle, Washington, 98105, United States

Location

Instituto centenario

Buenos Aires, C1204AAD, Argentina

Location

Children's Hospital Westmead; Paediatrics & Child Health

Westmead, New South Wales, 2145, Australia

Location

Lady Cilento Children's Hospital; Neurosciences Department

South Brisbane, Queensland, 4101, Australia

Location

Royal Children's Hospital

Parkville, Victoria, 3052, Australia

Location

UZ Gent

Ghent, 9000, Belgium

Location

London Health Sciences Centre; Children's Hospital; Pediatrics

London, Ontario, N6A 5W9, Canada

Location

Children'S Hospital of Eastern Ontario

Ottawa, Ontario, K1H 8L1, Canada

Location

Hospices Civils de Lyon

Lyon, 69004, France

Location

Hotel Dieu; Service Pharmacie Essais Cliniques

Nantes, 44093, France

Location

Hopital Armand Trousseau; centre reference Maladies Neuro-musculaires Est parisien Neuropediatrie

Paris, 75571, France

Location

Hopitaux Universitaires de Strasbourg

Strasbourg, 67091, France

Location

Universitatsklinikum Essen; Innere Klinik

Essen, 45122, Germany

Location

Fondazione Serena Onlus - CENTRO CLINICO NEMO

Milano, Emilia-Romagna, 20162, Italy

Location

Fondazione Policlinico Universitario A Gemelli; Servizio di Farmacia

Rome, Lazio, 00168, Italy

Location

Az. Osp. Universitaria Pol. G. Martino; Dip. Neuroscienze, Scienze Psichiatriche e Anest.

Messina, Sicily, 98125, Italy

Location

Hyogo College of Medicine Hospital

Hyōgo, 663-8501, Japan

Location

Miyagi Children's Hospital

Miyagi, 989-3126, Japan

Location

Shinshu University Hospital

Nagano, 390-8621, Japan

Location

National Hospital Organization Osaka Toneyama Medical Center

Osaka, 560-8552, Japan

Location

National Center of Neurology and Psychiatry

Tokyo, 187-8551, Japan

Location

Leids Universitair Medisch Centrum

Leiden, 2333 ZA, Netherlands

Location

Radboud University Nijmegen Medical Centre; Ophthalmology

Nijmegen, 6525 EX, Netherlands

Location

Hospital Sant Joan De Deu

Esplugues de Llobregas, Barcelona, 08950, Spain

Location

Hospital Universitari i Politecnic La Fe de Valencia; Servicio de Farmacia

Valencia, 46026, Spain

Location

Drottning Silvias Barn- och ungdomssjukhus; Kliniken for barnmedicin

Gothenburg, 41685, Sweden

Location

Alder Hey Children s Hospital; Department of Pediatrics

Liverpool, L12 2AP, United Kingdom

Location

UCL Institute of Child Health & Great Ormond Street Hospital for Children

London, WC1N 1EH, United Kingdom

Location

Related Publications (1)

  • Muntoni F, Byrne BJ, McMillan HJ, Ryan MM, Wong BL, Dukart J, Bansal A, Cosson V, Dreghici R, Guridi M, Rabbia M, Staunton H, Tirucherai GS, Yen K, Yuan X, Wagner KR; Taldefgrobep Alfa Study Group. The Clinical Development of Taldefgrobep Alfa: An Anti-Myostatin Adnectin for the Treatment of Duchenne Muscular Dystrophy. Neurol Ther. 2024 Feb;13(1):183-219. doi: 10.1007/s40120-023-00570-w. Epub 2024 Jan 8.

Related Links

MeSH Terms

Conditions

Muscular Dystrophy, DuchenneMuscular Dystrophies

Condition Hierarchy (Ancestors)

Muscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Results Point of Contact

Title
Medical Communications
Organization
Hoffmann-La Roche

Study Officials

  • Clinical Trials

    Hoffmann-La Roche

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
OTHER
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

January 27, 2017

First Posted

February 1, 2017

Study Start

July 6, 2017

Primary Completion

April 28, 2020

Study Completion

April 28, 2020

Last Updated

December 21, 2020

Results First Posted

December 21, 2020

Record last verified: 2020-11

Locations