NCT02464891

Brief Summary

This study evaluates the effect of CCX168, a C5aR Antagonist, Oral Administration on Ex Vivo Thrombus Formation and Disease Activity in ten patients with diagnosis of Atypical Hemolytic Uremic Syndrome with or without genetic abnormalities in the complement system or thrombomodulin, on stable chronic extracorporeal or peritoneal dialysis therapy since at least 6 months.

Trial Health

57
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Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
6

participants targeted

Target at below P25 for phase_2

Timeline
Completed

Started Jun 2015

Geographic Reach
1 country

1 active site

Status
terminated

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

May 26, 2015

Completed
9 days until next milestone

Study Start

First participant enrolled

June 4, 2015

Completed
4 days until next milestone

First Posted

Study publicly available on registry

June 8, 2015

Completed
2.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 13, 2017

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

July 13, 2017

Completed
Last Updated

November 14, 2017

Status Verified

November 1, 2017

Enrollment Period

2.1 years

First QC Date

May 26, 2015

Last Update Submit

November 13, 2017

Conditions

Keywords

Atypical Hemolytic Uremic SyndromeCCX168dialysisC5aR antagonist

Outcome Measures

Primary Outcomes (1)

  • Ex vivo thrombogenesis.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

Secondary Outcomes (13)

  • Complement component 3 serum levels.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

  • Complement component 4 serum levels.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

  • Complement component 5 serum levels.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

  • Complement Factor H.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

  • Complement component 5a.

    Changes from baseline at day 2,14 (during CCX168 treatment), 16 and 21 (after treatment withdrawal).

  • +8 more secondary outcomes

Study Arms (1)

CCX168

EXPERIMENTAL

Study medication will be administered as hard gelatin capsules containing 10 mg CCX168. Patients will take 30 mg CCX168, given as 3 x 10 mg capsule, twice daily for 15 days.

Drug: CCX168

Interventions

CCX168DRUG
CCX168

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersYes
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Age \>18 years;
  • Diagnosis of aHUS with or without identified genetic abnormalities in the complement system or thrombomodulin;
  • Stable chronic extracorporeal or peritoneal dialysis therapy since at least 6 months;
  • Written informed consent.

You may not qualify if:

  • Women of childbearing potential or women who are breastfeeding;
  • Shiga toxin-associated HUS or secondary forms of thrombotic microangiopathy;
  • ADAMTS13 activity \<10 % or circulating anti ADAMTS13 autoantibodies consistent with the diagnosis of thrombotic thrombocytopenic purpura;
  • Need for specific intervention with plasma therapy and/or complement inhibitors as deemed clinically appropriate;
  • Plasma therapy or treatment with complement inhibitors or antiplatelet and antithrombotic agents over the last two weeks;
  • Liver function impairment (serum liver enzymes or bilirubin levels \>3 x upper limit of normal);
  • Neutrophil count \< 2000/μL or lymphocyte count \< 1000/μL;
  • Infection requiring antibiotic treatment within the previous 4 weeks prior to screening;
  • Participated in any clinical study of an investigational product within 30 days prior to screening or within 5 half-lives after taking the last dose;
  • History or presence of any medical condition or disease which, in the opinion of the Investigator may place the subject at unacceptable risk for study participation;
  • Inability to understand the potential risks and benefits of the study;
  • Legal incapacity.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

A.O. Papa Giovanni XXIII - U.O. Nefrologia e Dialisi/IRCCS IRFMN - Centro di Ricerche Cliniche per le Malattie Rare Aldo e Cele Daccò

Bergamo, Italy

Location

Related Publications (1)

  • Aiello S, Gastoldi S, Galbusera M, Ruggenenti P, Portalupi V, Rota S, Rubis N, Liguori L, Conti S, Tironi M, Gamba S, Santarsiero D, Benigni A, Remuzzi G, Noris M. C5a and C5aR1 are key drivers of microvascular platelet aggregation in clinical entities spanning from aHUS to COVID-19. Blood Adv. 2022 Jan 8;6(3):866-881. doi: 10.1182/bloodadvances.2021005246.

MeSH Terms

Conditions

Atypical Hemolytic Uremic Syndrome

Interventions

avacopan

Condition Hierarchy (Ancestors)

Hemolytic-Uremic SyndromeUremiaKidney DiseasesUrologic DiseasesFemale Urogenital DiseasesFemale Urogenital Diseases and Pregnancy ComplicationsUrogenital DiseasesMale Urogenital DiseasesAnemia, HemolyticAnemiaHematologic DiseasesHemic and Lymphatic DiseasesThrombotic MicroangiopathiesThrombocytopeniaBlood Platelet DisordersCytopenia

Study Officials

  • Giuseppe Remuzzi, MD

    IRCCS - Mario Negri Institute for Pharmacological Research/A.O. Papa Giovanni XXIII- BG

    STUDY CHAIR

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

May 26, 2015

First Posted

June 8, 2015

Study Start

June 4, 2015

Primary Completion

July 13, 2017

Study Completion

July 13, 2017

Last Updated

November 14, 2017

Record last verified: 2017-11

Locations