NCT02303626

Brief Summary

This study will evaluate the safety and efficacy of an oral treatment, BCX4161, in preventing acute attacks in participants with hereditary angioedema (HAE). Eligible participants will be randomized to receive one of two doses of BCX4161 or placebo for 12 weeks. The study will compare the number of acute attacks in each treatment group, as well as a number of other clinical outcomes, and the safety and tolerability of each dose of BCX4161 compared to placebo.

Trial Health

93
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
110

participants targeted

Target at P50-P75 for phase_2

Timeline
Completed

Started Dec 2014

Shorter than P25 for phase_2

Geographic Reach
8 countries

40 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

November 24, 2014

Completed
7 days until next milestone

First Posted

Study publicly available on registry

December 1, 2014

Completed
16 days until next milestone

Study Start

First participant enrolled

December 17, 2014

Completed
1 year until next milestone

Primary Completion

Last participant's last visit for primary outcome

January 1, 2016

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

January 1, 2016

Completed
9.9 years until next milestone

Results Posted

Study results publicly available

November 17, 2025

Completed
Last Updated

November 17, 2025

Status Verified

November 1, 2025

Enrollment Period

1 year

First QC Date

November 24, 2014

Results QC Date

January 31, 2017

Last Update Submit

November 3, 2025

Conditions

Keywords

BCX4161ProphylaxisPreventionHAEHereditary Angioedema

Outcome Measures

Primary Outcomes (1)

  • The Mean Acute Angioedema Attack Rate

    An angioedema attack was defined as swelling at any location reported by participant, which had no swelling earlier. Total number of confirmed attacks during the treatment period standardized to a weekly attack-rate to adjust for the total duration of treatment. The attack rate was derived for each participant by treatment period. The weekly attack rate was equal to the total number of confirmed attacks during a treatment period divided by the duration of the treatment (in days) times 7 days.

    12 weeks

Secondary Outcomes (6)

  • Number of Attack-free Days

    12 weeks

  • Number of Participants Who Are Attack-free

    12 weeks

  • Disease Activity, as Measured by the 84-day Angioedema Activity Score

    12 weeks

  • Change From Baseline at Week 12, in Quality of Life as Measured by the Angioedema Quality of Life Questionnaire

    Baseline (Day 1) and Week 12

  • Number of Participants With Treatment Emergent Adverse Events

    From first dose up to 14 weeks

  • +1 more secondary outcomes

Study Arms (3)

BCX4161 300 mg three times daily

EXPERIMENTAL

Three BCX4161 capsules (100 mg) and two placebo capsules to be taken three times daily by mouth

Drug: BCX4161Drug: Placebo

BCX4161 500 mg three times daily

EXPERIMENTAL

Five BCX4161 capsules (100 mg) to be taken three times daily by mouth

Drug: BCX4161

Placebo three times daily

PLACEBO COMPARATOR

Five placebo capsules to be taken three times daily by mouth

Drug: Placebo

Interventions

BCX4161 300 mg three times dailyBCX4161 500 mg three times daily
BCX4161 300 mg three times dailyPlacebo three times daily

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • A clinical diagnosis of HAE type I or II
  • Documented HAE attacks within a defined calendar period; in the absence of documented HAE attacks, participants will be required to enter a run-in period to document attacks
  • Access to acute attack medications
  • Sexually active women of child-bearing potential and sexually active men must utilize highly effective contraception

You may not qualify if:

  • Women who are pregnant or breast-feeding
  • Any clinical condition or medical history that would interfere with the subject's safety or ability to participate in the study
  • Use of C1INH or tranexamic acid for prophylaxis of HAE attacks
  • Current participation in any other investigational drug study or within the last 30 days
  • History of or current alcohol or drug abuse
  • Infection with hepatitis B, hepatitis C or HIV

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (40)

Unknown Facility

Birmingham, Alabama, 35209, United States

Location

Unknown Facility

Scottsdale, Arizona, 85251, United States

Location

Unknown Facility

Granada Hills, California, 91344, United States

Location

Unknown Facility

San Diego, California, 92093, United States

Location

Unknown Facility

San Diego, California, 92112, United States

Location

Unknown Facility

Walnut Creek, California, 94598, United States

Location

Unknown Facility

Colorado Springs, Colorado, 80907, United States

Location

Unknown Facility

Shreveport, Louisiana, 71106, United States

Location

Unknown Facility

Chevy Chase, Maryland, 20815, United States

Location

Unknown Facility

Boston, Massachusetts, 02114, United States

Location

Unknown Facility

Plymouth, Minnesota, 55446, United States

Location

Unknown Facility

St Louis, Missouri, 63141, United States

Location

Unknown Facility

New York, New York, 10029, United States

Location

Unknown Facility

Charlotte, North Carolina, 28277, United States

Location

Unknown Facility

Cincinnati, Ohio, 45267, United States

Location

Unknown Facility

Oklahoma City, Oklahoma, 73131, United States

Location

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Tulsa, Oklahoma, 74133, United States

Location

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Lake Oswego, Oregon, 97035, United States

Location

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Hershey, Pennsylvania, 17033, United States

Location

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Pittsburgh, Pennsylvania, 15241, United States

Location

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Dallas, Texas, 75231, United States

Location

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Galveston, Texas, 77555, United States

Location

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Fairfax, Virginia, 63141, United States

Location

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Spokane, Washington, 99204, United States

Location

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Tacoma, Washington, 98405, United States

Location

Unknown Facility

Leuven, Belgium

Location

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Ottawa, Canada

Location

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Grenoble, France

Location

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Lille, France

Location

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Paris, France

Location

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Berlin, Germany

Location

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Frankfurt, Germany

Location

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Mörfelden-Walldorf, Germany

Location

Unknown Facility

Budapest, Hungary

Location

Unknown Facility

Milan, Italy

Location

Unknown Facility

Birmingham, United Kingdom

Location

Unknown Facility

Bristol, United Kingdom

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Unknown Facility

Cardiff, United Kingdom

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Unknown Facility

London, United Kingdom

Location

Unknown Facility

Manchester, United Kingdom

Location

Related Publications (1)

  • Beard N, Frese M, Smertina E, Mere P, Katelaris C, Mills K. Interventions for the long-term prevention of hereditary angioedema attacks. Cochrane Database Syst Rev. 2022 Nov 3;11(11):CD013403. doi: 10.1002/14651858.CD013403.pub2.

MeSH Terms

Conditions

Angioedemas, Hereditary

Interventions

avoralstat

Condition Hierarchy (Ancestors)

AngioedemaVascular DiseasesCardiovascular DiseasesHereditary Complement Deficiency DiseasesPrimary Immunodeficiency DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesUrticariaSkin Diseases, VascularSkin DiseasesSkin and Connective Tissue DiseasesHypersensitivity, ImmediateHypersensitivityImmune System DiseasesImmunologic Deficiency Syndromes

Results Point of Contact

Title
VP Clinical Development
Organization
BioCryst Pharmaceuticals, Inc

Study Officials

  • Marc Riedl, MD MS

    UCSD

    PRINCIPAL INVESTIGATOR

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
No

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
PREVENTION
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 24, 2014

First Posted

December 1, 2014

Study Start

December 17, 2014

Primary Completion

January 1, 2016

Study Completion

January 1, 2016

Last Updated

November 17, 2025

Results First Posted

November 17, 2025

Record last verified: 2025-11

Locations