NCT01461837

Brief Summary

This study is being done to determine the safety and outcome (long-term control) of a high-dose chemotherapy regimen followed by an infusion of CD34 selected (immune cells) stem cells from a partially matched adult family member donor, called haploidentical stem cell transplantation, in high-risk sickle cell disease patients. Funding Source - FDA OOPD

Trial Health

75
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
21

participants targeted

Target at below P25 for phase_2

Timeline
7mo left

Started Jan 2012

Longer than P75 for phase_2

Geographic Reach
1 country

6 active sites

Status
active not recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress96%
Jan 2012Dec 2026

First Submitted

Initial submission to the registry

October 19, 2011

Completed
9 days until next milestone

First Posted

Study publicly available on registry

October 28, 2011

Completed
2 months until next milestone

Study Start

First participant enrolled

January 1, 2012

Completed
13.9 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 1, 2025

Completed
1 year until next milestone

Study Completion

Last participant's last visit for all outcomes

December 1, 2026

Expected
Last Updated

August 8, 2025

Status Verified

August 1, 2025

Enrollment Period

13.9 years

First QC Date

October 19, 2011

Last Update Submit

August 7, 2025

Conditions

Keywords

sickle cell diseasestem cell transplantationhaploidentical

Outcome Measures

Primary Outcomes (1)

  • Treatment related events

    Death, primary or late graft rejection, or recurrence of disease and acceptable rate of hematopoietic engraftment, acute and chronic graft-versus-host disease

    1 year

Secondary Outcomes (3)

  • neurological/neurocognitive status

    2 years

  • Pulmonary/pulmonary vascular status

    2 years

  • Health-related quality of life

    4 years

Study Arms (1)

Haplo Stem Cell Transplantation

EXPERIMENTAL

CD34 selected T-cell depleted allogeneic SCT

Drug: CD34 selected T-cell depleted allogeneic SCT

Interventions

Hydroxyurea (60 mg/kg/day) and azathioprine (3 mg/kg/day) day -59 to day -11; fludarabine (30 mg/m2) Days -17, -16, -15, -14, -13; busulfan (3.2 mg/kg/day) Days -12, -11, -10, -9; thiotepa (10 mg/kg IV) day -8; cyclophosphamide (50 mg/kg) Days -7, -6, -5, -4; TLI on day -3; rabbit ATG (2.0 mg/kg/day) day -5,-4,-3, and -2; Stem Cell infusion day 0

Also known as: Familial haploidentical, T-cell depleted, allogeneic stem cell transplantation, high risk Sickle Cell Disease
Haplo Stem Cell Transplantation

Eligibility Criteria

Age2 Years - 20 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Homozygous Hemoglobin S Disease, or Hemoglobin S Beta0/+ thalassemia
  • Patients must demonstrate one or more of the following Sickle Cell Disease Complications
  • Clinically significant neurologic event (stroke) or any neurologic deficit lasting \>24 hours that is accompanied by an infarct on cerebral MRI
  • Minimum of two episodes of acute chest syndrome.
  • Recurrent painful events (at least 3 in the 2 years prior to enrollment).
  • Abnormal TCD study requiring starting on chronic transfusion therapy.
  • At least one silent infarct lesion on a MRI scan of the head.
  • A familial haploidentical donor without homozygous sickle cell disease
  • Adequate organ function (renal, liver, cardiac and pulmonary function)
  • Karnofsky or Lansky (age appropriate) Performance Score ≥50%
  • Liver biopsy is optional to assess for iron overload in chronically transfused patients.

You may not qualify if:

  • Females who are pregnant or breast-feeding
  • SCD Patients with documented uncontrolled infection
  • SCD patients who have an unaffected HLA matched family donor willing to proceed to donation
  • Demonstrated lack of compliance with medical care.
  • Clinically significant fibrosis or cirrhosis of the liver
  • Previously received a HSCT

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (6)

University of California Los Angeles (UCLA)

Los Angeles, California, 90095, United States

Location

Children's Hospital and Research Center Oakland

Oakland, California, 94609, United States

Location

Lurie Children's Hospital

Chicago, Illinois, 60611-2605, United States

Location

Washington University/St. Louis Children's Hospital

St Louis, Missouri, 63110, United States

Location

New York Medical College

Valhalla, New York, 10595, United States

Location

Medical College of Wisconsin/Children's Hospital of Wisconsin

Milwaukee, Wisconsin, 53226, United States

Location

Related Publications (2)

  • Braniecki S, Vichinsky E, Walters MC, Shenoy S, Shi Q, Moore TB, Talano JA, Parsons SK, Flower A, Panarella A, Fabricatore S, Morris E, Mahanti H, Milner J, McKinstry RC, Duncan CN, van de Ven C, Cairo MS. Neurocognitive outcome in children with sickle cell disease after myeloimmunoablative conditioning and haploidentical hematopoietic stem cell transplantation: a non-randomized clinical trial. Front Neurol. 2024 May 22;15:1263373. doi: 10.3389/fneur.2024.1263373. eCollection 2024.

  • Parsons SK, Rodday AM, Weidner RA, Morris E, Braniecki S, Shenoy S, Talano JA, Moore TB, Panarella A, Flower A, Milner J, Fabricatore S, Mahanti H, van de Ven C, Shi Q, Cairo MS. Significant improvement of child physical and emotional functioning after familial haploidentical stem cell transplant. Bone Marrow Transplant. 2022 Apr;57(4):586-592. doi: 10.1038/s41409-022-01584-y. Epub 2022 Feb 2.

Related Links

MeSH Terms

Conditions

Anemia, Sickle Cell

Condition Hierarchy (Ancestors)

Anemia, Hemolytic, CongenitalAnemia, HemolyticAnemiaHematologic DiseasesHemic and Lymphatic DiseasesHemoglobinopathiesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Study Officials

  • Mitchell S Cairo, MD

    New York Medical College

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Principal Investigator

Study Record Dates

First Submitted

October 19, 2011

First Posted

October 28, 2011

Study Start

January 1, 2012

Primary Completion

December 1, 2025

Study Completion (Estimated)

December 1, 2026

Last Updated

August 8, 2025

Record last verified: 2025-08

Locations