NCT01359670

Brief Summary

This study, supported by Parent Project Muscular Dystrophy, will determine if tadalafil or sildenafil can improve muscle blood flow during exercise in boys with Duchenne muscular dystrophy.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
30

participants targeted

Target at P50-P75 for early_phase_1

Timeline
Completed

Started May 2011

Geographic Reach
1 country

1 active site

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

May 1, 2011

Completed
22 days until next milestone

First Submitted

Initial submission to the registry

May 23, 2011

Completed
2 days until next milestone

First Posted

Study publicly available on registry

May 25, 2011

Completed
1.9 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

May 1, 2013

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

May 1, 2013

Completed
Last Updated

January 14, 2020

Status Verified

April 1, 2018

Enrollment Period

2 years

First QC Date

May 23, 2011

Last Update Submit

January 10, 2020

Conditions

Keywords

Duchennemuscular dystrophytadalafilsildenafilmuscle ischemiaexercise

Outcome Measures

Primary Outcomes (1)

  • Functional muscle ischemia

    Measured by the decrease in muscle tissue oxygenation (near infrared spectroscopy) and blood flow (Doppler ultrasound) evoked by reflex sympathetic activation in exercising forearm muscle.

    For 5 study visits

Secondary Outcomes (5)

  • Cardiac Function

    For 5 study visits

  • EKG Monitoring

    5 times over about 6 weeks

  • 6 Minute Walk Test

    For 5 study visits

  • Physical Activity

    5 times over about 6-weeks

  • Quality of Life

    For 5 study visits

Study Arms (2)

Tadalafil

EXPERIMENTAL
Drug: Tadalafil

Sildenafil

EXPERIMENTAL
Drug: Sildenafil

Interventions

Escalating dose (0.25 mg/kg, 0.5 mg/kg, 1.0 mg/kg; once daily) over 2 weeks

Also known as: Cialis, Adcirca
Tadalafil

Escalating dose (0.25 mg/kg, 0.5 mg/kg, 1.0 mg/kg; four times daily) over 2 weeks

Also known as: Viagra, Revatio
Sildenafil

Eligibility Criteria

Age7 Years - 15 Years
Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17)

You may qualify if:

  • Diagnosis of DMD confirmed by muscle biopsy or DNA analysis
  • Age 7-15y
  • Ambulatory
  • No clinical evidence of heart failure

You may not qualify if:

  • Hypertension, diabetes, or heart failure by standard clinical criteria
  • Elevated BNP level (\>100 pg/ml)
  • LVEF \< 50%
  • Wheelchair bound
  • Cardiac rhythm disorder, specifically: rhythm other than sinus, SVT, atrial fibrillation, ventricular tachycardia
  • Continuous ventilatory support
  • Liver disease
  • Renal impairment
  • Contraindications to tadalafil or sildenafil (use of nitrates, alpha-blockers, CYP3A inhibitors, amlodipine, or other PDE5A inhibitors)

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Cedars-Sinai Medical Center

Los Angeles, California, 90048, United States

Location

MeSH Terms

Conditions

Muscular Dystrophy, DuchenneMuscular DystrophiesMotor Activity

Interventions

TadalafilSildenafil Citrate

Condition Hierarchy (Ancestors)

Muscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesBehavior

Intervention Hierarchy (Ancestors)

CarbolinesPyridinesHeterocyclic Compounds, 1-RingHeterocyclic CompoundsIndole AlkaloidsIndolesHeterocyclic Compounds, 2-RingHeterocyclic Compounds, Fused-RingHeterocyclic Compounds, 3-RingSulfonamidesAmidesOrganic ChemicalsSulfonesSulfur CompoundsPiperazinesPurines

Study Officials

  • Ronald Victor, MD

    Cedars-Sinai Medical Center

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
early phase 1
Allocation
RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
CROSSOVER
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

May 23, 2011

First Posted

May 25, 2011

Study Start

May 1, 2011

Primary Completion

May 1, 2013

Study Completion

May 1, 2013

Last Updated

January 14, 2020

Record last verified: 2018-04

Locations