NCT01099761

Brief Summary

The purpose of this study is to determine if ACE-031 is safe and well-tolerated in boys with Duchenne Muscular Dystrophy (DMD) and to select the optimal doses of ACE-031 in terms of safety and pharmacodynamic (PD) activity for designing future studies. \[Note: This study was terminated based on safety data\]

Trial Health

57
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
24

participants targeted

Target at below P25 for phase_2

Timeline
Completed

Started Apr 2010

Shorter than P25 for phase_2

Geographic Reach
1 country

5 active sites

Status
terminated

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

April 1, 2010

Completed
1 day until next milestone

First Submitted

Initial submission to the registry

April 2, 2010

Completed
6 days until next milestone

First Posted

Study publicly available on registry

April 8, 2010

Completed
1.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 1, 2011

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

June 1, 2011

Completed
5.4 years until next milestone

Results Posted

Study results publicly available

October 14, 2016

Completed
Last Updated

October 13, 2022

Status Verified

September 1, 2022

Enrollment Period

1.2 years

First QC Date

April 2, 2010

Results QC Date

May 10, 2016

Last Update Submit

September 14, 2022

Conditions

Outcome Measures

Primary Outcomes (2)

  • Number of Subjects With Adverse Reactions.

    Number of subjects in each cohort with a treatment-emergent adverse event considered at least possibly related to study drug

    From treatment initiation to End-of-Study Visit, approximately 24 weeks later

  • Number of Subjects With Clinical Laboratory Adverse Reactions.

    Number of subjects in each cohort with treatment-emergent adverse laboratory values judged to be at least possibly related to study drug

    Baseline to End-of-Study Visit, approximately 24 weeks later.

Secondary Outcomes (8)

  • Percent Change in Total Lean Body Mass by DXA Scan.

    Baseline to End-of-Study Visit, approximately 24 weeks later.

  • Percent Change in Lumbar Spine Bone Mineral Density by DXA Scan.

    Baseline to End-of-Study Visit, approximately 24 weeks later.

  • Percent Change in Muscle Strength Score by Hand-held Myometry.

    Baseline to End-of-Study Visit, approximately 24 weeks later.

  • Change in Distance Traveled in 6 Minutes (Standardized 6-Minute-Walk Test).

    Baseline to End-of-Study Visit, approximately 24 weeks later.

  • Change From Baseline in Time to Travel 10 Meters (Standardized 10-Meter-Walk/Run Test).

    Baseline to End-of-Study Visit, approximately 24 weeks later.

  • +3 more secondary outcomes

Study Arms (3)

ACE-031 0.5 mg/kg q4wk

EXPERIMENTAL
Biological: ACE-031 0.5 mg/kg q4wk

ACE-031 1.0 mg/kg q2wk

EXPERIMENTAL
Biological: ACE-031 1.0 mg/kg q2wk

Placebo

PLACEBO COMPARATOR
Other: Placebo

Interventions

ACE-031 0.5 mg/kg subcutaneously once every 4 weeks for 12 weeks.

ACE-031 0.5 mg/kg q4wk

ACE-031 1.0 mg/kg subcutaneously once every 2 weeks for 12 weeks.

ACE-031 1.0 mg/kg q2wk
PlaceboOTHER

Matching volume placebo subcutaneously every 2 or 4 weeks for 12 weeks.

Placebo

Eligibility Criteria

Age4 Years+
Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Diagnosis of DMD confirmed
  • Ambulant
  • Corticosteroid therapy for at least one year prior to study day 1 and on a stable dose and schedule for at least 6 months prior to study day 1
  • Evidence of muscle weakness by clinical assessment

You may not qualify if:

  • Any previous treatment with another investigational product within 6 months prior to study day 1
  • Any clinically significant cardiac, endocrine, hematologic, hepatic, immunologic, metabolic, urologic, pulmonary, neurologic, dermatologic, psychiatric, renal, and/or other major disease that is not related to DMD
  • Inability to perform a whole body dual x-ray absorptiometry (DXA) scan

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (5)

Acceleron Investigative Site

Calgary, Alberta, Canada

Location

Acceleron Investigative Site

Vancouver, British Columbia, Canada

Location

Acceleron Investigative Site

Hamilton, Ontario, Canada

Location

Acceleron Investigative Site

London, Ontario, Canada

Location

Acceleron Investigative Site

Ottawa, Ontario, Canada

Location

MeSH Terms

Conditions

Muscular Dystrophy, Duchenne

Condition Hierarchy (Ancestors)

Muscular DystrophiesMuscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Results Point of Contact

Title
Senior Vice President, Global Clinical Development
Organization
Merck Sharp & Dohme LLC

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
No

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

April 2, 2010

First Posted

April 8, 2010

Study Start

April 1, 2010

Primary Completion

June 1, 2011

Study Completion

June 1, 2011

Last Updated

October 13, 2022

Results First Posted

October 14, 2016

Record last verified: 2022-09

Data Sharing

IPD Sharing
Will not share

Abstract summarizing trial data has been published online in Muscle \& Nerve 23-Dec-2016 https://www.ncbi.nlm.nih.gov/pubmed/27462804 The Sponor currently has no plans to make IPD available for a number of reasons; (i) the study was terminated by the Sponsor prematurely based upon concerns for potential adverse drug reactions following long-term use, which were identified in chronic toxicity studies in animals, (ii) the study population was one with a rare disease, in a groups of subjects with a relatively narrow age range, across a small number of study sites. The Sponsor believes that these factors, taken together, make patient anonymity a significant challenge.

Locations