NCT01051544

Brief Summary

This is a prospective, controlled, randomized, open label study, aimed at comparing FVIII/VWF concentrates with FVIII concentrates at 200 IU/kg daily in their ability to induce immune tolerance in Haemophilia A patients with high responding inhibitors and poor prognosis for success.

Trial Health

15
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Timeline
Completed

Started Sep 2009

Longer than P75 for not_applicable

Status
withdrawn

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

September 25, 2009

Completed
4 months until next milestone

First Submitted

Initial submission to the registry

January 15, 2010

Completed
3 days until next milestone

First Posted

Study publicly available on registry

January 18, 2010

Completed
10.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 25, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

June 25, 2020

Completed
Last Updated

December 17, 2020

Status Verified

December 1, 2020

Enrollment Period

10.8 years

First QC Date

January 15, 2010

Last Update Submit

December 15, 2020

Conditions

Keywords

ITIHAEMOPHILIA AINHIBITORSVWF/FVIII Concentrates

Outcome Measures

Primary Outcomes (1)

  • Primary end point is the success in inducing immune tolerance, defined as: the abolition of the inhibitor to < 0.6 BU within 33 months of ITI with a factor VIII recovery ≥ 66% and half-life ≥ 6 hrs, and measured after a 72-hour washout period.

    33 months

Secondary Outcomes (4)

  • Absence of relapse, up to 12 months after achievement of Immune Tolerance

    12 months

  • Time to achieve partial or complete success as defined in the protocol.

    33 months

  • Safety Compliance to treatment

    33 months

  • Cost of Care

    12 months

Study Arms (2)

von Willebrand factor-free FVIII concentrates

ACTIVE COMPARATOR

Patients treated with FVIII concentrates

Drug: FVIII Concentrates

FVIII/VWF concentrates

ACTIVE COMPARATOR

Patients treated with FVIII/VWF concentrates

Drug: FVIII/VWF concentrates

Interventions

Patients will be centrally randomized to receive a von Willebrand factor-free FVIII concentrate (recombinant or plasma-derived, monoclonally-purified). The choice of product brand will be based on physician / patients preferences.

Also known as: Including but not limited to:, Advate, Beriate P, Hemofil M, Helixate, Kogenate, Kogenate SF, Monarch M, Monoclate, Recombinate, Refacto, Replenate, Xyntha
von Willebrand factor-free FVIII concentrates

Patients will be centrally randomized to receive a FVIII/VWF concentrate of 200 IU/Kg by one or two bolus injections daily.The choice of product brand will be based on physician / patients preferences.

Also known as: Including but not limited to:, Koate-DVI, 8Y, Optivate, Alphanate, Fahndi, Haemate P, Humate P, Haemoctine SDH, Octanate, Wilate, Emoclot DI, Factane
FVIII/VWF concentrates

Eligibility Criteria

Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • severe hemophilia A (FVIII\<1%);
  • male, any age;
  • high responders (peak inhibitor levels \> 5 BU);
  • any inhibitor level at study enrolment;
  • ability and willingness to participate in the study;
  • at least one of the following risk factors for ITI failure:
  • peak inhibitor titer \> 200 BU
  • titer at ITI start \> 10 BU
  • age \> 7 years
  • time between inhibitor occurrence and ITI \> 2 years
  • absence of high risk of cardiovascular, cerebrovascular or other thromboembolic events as deemed by the treating clinician.

You may not qualify if:

  • concomitant systemic treatment with immunosuppressive drugs;
  • concomitant experimental treatment;
  • previous ITI attempt;
  • previous history of myocardial infarction and/or cerebral stroke.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Related Publications (3)

  • Berntorp E, Ekman M, Gunnarsson M, Nilsson IM. Variation in factor VIII inhibitor reactivity with different commercial factor VIII preparations. Haemophilia. 1996 Apr;2(2):95-9. doi: 10.1111/j.1365-2516.1996.tb00022.x.

    PMID: 27214015BACKGROUND
  • Kreutz W: Immune tolerance induction (ITI) in Haemophilia A-patients with inhibitors - the choice of concentrate affecting success. Haematologica2001; 86 (S4):16-20

    BACKGROUND
  • Gringeri A, Musso R, Mazzucconi MG, Piseddu G, Schiavoni M, Pignoloni P, Mannucci PM; RITS-FITNHES Study Group. Immune tolerance induction with a high purity von Willebrand factor/VIII complex concentrate in haemophilia A patients with inhibitors at high risk of a poor response. Haemophilia. 2007 Jul;13(4):373-9. doi: 10.1111/j.1365-2516.2007.01484.x.

    PMID: 17610550BACKGROUND

Related Links

MeSH Terms

Conditions

Hemophilia A

Interventions

Factor VIIIF8 protein, humanrecombinant factor VIII SQoptivatefactor VIII, von Willebrand factor drug combinationvon Willebrand Factor

Condition Hierarchy (Ancestors)

Blood Coagulation Disorders, InheritedBlood Coagulation DisordersHematologic DiseasesHemic and Lymphatic DiseasesCoagulation Protein DisordersHemorrhagic DisordersGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Intervention Hierarchy (Ancestors)

Blood Coagulation FactorsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsProtein PrecursorsBiological Factors

Study Officials

  • Nadia P Ewing, MD

    Clinical Professor of Pediatrics, City of Hope National Medical Center, Dept. of Pediatrics, 1500 E. Duarte Rd. Duarte, CA 91010

    PRINCIPAL INVESTIGATOR
0

Study Design

Study Type
interventional
Phase
not applicable
Allocation
RANDOMIZED
Masking
NONE
Purpose
PREVENTION
Intervention Model
PARALLEL
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

January 15, 2010

First Posted

January 18, 2010

Study Start

September 25, 2009

Primary Completion

June 25, 2020

Study Completion

June 25, 2020

Last Updated

December 17, 2020

Record last verified: 2020-12