NCT01051076

Brief Summary

The purpose of this study is to evaluate whether a concentrate containing both FVIII and von Willebrand Factor (VWF) given at a high dose will induce immune tolerance in subjects who have already experienced and failed ITI with VWF-free FVIII concentrates. The treatment on this study is expected to last up to 33 months.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
3

participants targeted

Target at below P25 for not_applicable

Timeline
Completed

Started Nov 2009

Longer than P75 for not_applicable

Geographic Reach
1 country

1 active site

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

November 3, 2009

Completed
2 months until next milestone

First Submitted

Initial submission to the registry

January 15, 2010

Completed
3 days until next milestone

First Posted

Study publicly available on registry

January 18, 2010

Completed
10.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

October 21, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

October 21, 2020

Completed
Last Updated

August 23, 2021

Status Verified

December 1, 2020

Enrollment Period

11 years

First QC Date

January 15, 2010

Last Update Submit

August 18, 2021

Conditions

Keywords

ITIHaemophilia AInhibitorsFailed ITIVWF/FVIII concentrates

Outcome Measures

Primary Outcomes (1)

  • Achievement of an inhibitor titer of <0.6 BU/failure to achieve an inhibitor titer of <0.6 BU within 33 months, or failure to decrease inhibitor titer by at least 20% compared to titer in prior 6 months, beginning at 3 months after starting ITI

    Primary end point is the achievement of an inhibitor titer of less than 0.6 BU or failure to achieve an inhibitor titer of less than 0.6 BU within 33 months of treatment, or failure to decrease the inhibitor titer by at least 20% compared to the titer in the prior 6 months, beginning at 3 months after starting ITI

    3 years

Secondary Outcomes (3)

  • Time to achieve success- either partial or complete.

    33 months

  • Safety - assessment of adverse events through treatment and compliance with prolonged regimen.

    33 months

  • Cost of care.

    Up to 45 months

Study Arms (1)

Factor VIII and von Willebrand Factor

EXPERIMENTAL
Drug: VWF/FVIII concentrates

Interventions

200 IU/Kg by one or two bolus injections daily. After successful confirmation the dose will be tailed off progressively until discontinuation. Patients will be treated with a VWF/FVIII concentrates according to physician/patients preference.

Also known as: Koate-DVI, Emoclot DI, Factane, 8Y, Optivate, Alphanate, Fahndi, Haemate P, Humate P, Haemoctine SDH, Octanate, Wilate
Factor VIII and von Willebrand Factor

Eligibility Criteria

Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • severe hemophilia A (FVIII\<1%) with high responding inhibitors (peak levels \>5 BU)
  • male, any age;
  • any inhibitor level at study enrollment;
  • ability and willingness to participate to the study;
  • previous ITI course of at least 9 months with a VWF-free FVIII concentrate at any dosage, such as recombinant FVIII and/or monoclonally purified FVIII.

You may not qualify if:

  • concomitant systemic treatment with immunosuppressive drugs;
  • concomitant experimental treatment;
  • previous history of myocardial infarction and/or cerebral stroke

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

City of Hope Medical Center

Duarte, California, 91010, United States

Location

Related Publications (3)

  • Berntorp E, Ekman M, Gunnarsson M, Nilsson IM. Variation in factor VIII inhibitor reactivity with different commercial factor VIII preparations. Haemophilia. 1996 Apr;2(2):95-9. doi: 10.1111/j.1365-2516.1996.tb00022.x.

    PMID: 27214015BACKGROUND
  • Kreuz W, Steiner J, Auerswald G, Beeg T, Becker S. Successful immunetolerance therapy of FVIII-inhibitor in chldren after changing from high to intermediate purity FVIII concentrate. Ann Hematol 1996; 72 (suppl 1).

    BACKGROUND
  • Gringeri A, Musso R, Mazzucconi MG, Piseddu G, Schiavoni M, Pignoloni P, Mannucci PM; RITS-FITNHES Study Group. Immune tolerance induction with a high purity von Willebrand factor/VIII complex concentrate in haemophilia A patients with inhibitors at high risk of a poor response. Haemophilia. 2007 Jul;13(4):373-9. doi: 10.1111/j.1365-2516.2007.01484.x.

    PMID: 17610550BACKGROUND

Related Links

MeSH Terms

Conditions

Hemophilia A

Interventions

Factor VIIIoptivatefactor VIII, von Willebrand factor drug combinationvon Willebrand Factor

Condition Hierarchy (Ancestors)

Blood Coagulation Disorders, InheritedBlood Coagulation DisordersHematologic DiseasesHemic and Lymphatic DiseasesCoagulation Protein DisordersHemorrhagic DisordersGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Intervention Hierarchy (Ancestors)

Blood Coagulation FactorsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsProtein PrecursorsBiological Factors

Study Officials

  • Nadia P. Ewing, MD

    Clinical Professor of Pediatrics, City of Hope National Medical Center, Dept. of Pediatrics, 1500 E. Duarte Rd. Duarte, CA 91010

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
not applicable
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

January 15, 2010

First Posted

January 18, 2010

Study Start

November 3, 2009

Primary Completion

October 21, 2020

Study Completion

October 21, 2020

Last Updated

August 23, 2021

Record last verified: 2020-12

Locations