NCT07325591

Brief Summary

The objectives of this study are to examine the effects of tazbentetol on clinical measures of ALS, patient reported outcomes (PROs), long-term safety and tolerability.

Trial Health

65
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
430

participants targeted

Target at P75+ for phase_2

Timeline
22mo left

Started Mar 2026

Status
not yet recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress9%
Mar 2026Mar 2028

First Submitted

Initial submission to the registry

January 6, 2026

Completed
2 days until next milestone

First Posted

Study publicly available on registry

January 8, 2026

Completed
2 months until next milestone

Study Start

First participant enrolled

March 1, 2026

Completed
1.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 31, 2027

Expected
2 months until next milestone

Study Completion

Last participant's last visit for all outcomes

March 1, 2028

Last Updated

March 2, 2026

Status Verified

February 1, 2026

Enrollment Period

1.8 years

First QC Date

January 6, 2026

Last Update Submit

February 26, 2026

Conditions

Keywords

regenerativesynapseAmyotrophic Lateral Sclerosisplacebo-controlled

Outcome Measures

Primary Outcomes (3)

  • Phase 2: Absolute change from baseline in Amyotrophic Lateral Sclerosis Functional Rating Scale-revised (ALSFRS-R) total score

    Questionnaire administered by a clinician that measures participants' ability to function in certain daily activities. Each type of function is scored from 4 (normal) to 0 (no ability), with a maximum total score of 48 and a minimum total score of 0. Patients with higher scores have more physical function.

    36 weeks

  • Phase 3: Absolute change from baseline in Amyotrophic Lateral Sclerosis Functional Rating Scale-revised (ALSFRS-R) total score

    Questionnaire administered by a clinician that measures participants' ability to function in certain daily activities. Each type of function is scored from 4 (normal) to 0 (no ability), with a maximum total score of 48 and a minimum total score of 0. Patients with higher scores have more physical function.

    36 weeks

  • OLE: Absolute change from baseline in Amyotrophic Lateral Sclerosis Functional Rating Scale-revised (ALSFRS-R) total score

    Questionnaire administered by a clinician that measures participants' ability to function in certain daily activities. Each type of function is scored from 4 (normal) to 0 (no ability), with a maximum total score of 48 and a minimum total score of 0. Patients with higher scores have more physical function.

    36 weeks

Secondary Outcomes (21)

  • Phase 2: Combined Assessment of Function and Survival (CAFS) scores

    36 weeks

  • Phase 2: Change from baseline in Clinician Global Impression-Inhibitory (CGI-I)

    36 weeks

  • Phase 2: Change from baseline in Edinburgh Cognitive and Behavioural ALS Screen (ECAS)

    36 weeks

  • Phase 2: Change from baseline in ALS Assessment Questionnaire 40 items (ALSAQ-40)

    36 weeks

  • Phase 2: Change from baseline in Patient Global Impression (PGI) of Improvement

    36 weeks

  • +16 more secondary outcomes

Other Outcomes (7)

  • Phase 2: ALSFRS-R total score rate of decline

    36 weeks

  • Phase 2: Proportion of patients alive and survival time

    36 weeks

  • Phase 2 substudy: To compare electroencephalogram (EEG) outcomes of two dose levels of tazbentetol to placebo in participants with ALS

    36 weeks

  • +4 more other outcomes

Study Arms (2)

tazbentetol

EXPERIMENTAL

synthetic small molecule

Drug: Tazbentetol

Placebo

PLACEBO COMPARATOR

placebo

Drug: placebo

Interventions

Participants in both Phase 2B and Phase 3 will be randomized to received study drug tazbentetol or placebo tablets. Participants in the open-label extension phase will receive the dose determined from Phase 2.

Also known as: SPG302
tazbentetol

participants in double blind placebo controlled phase will be randomized to received placebo tablets

Placebo

Eligibility Criteria

Age18 Years - 80 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Age 18-80
  • ALS TRICALS risk score
  • Stable dose of standard of care treatment
  • Contraception use by men or women consistent with local regulations
  • Able and willing to provide written informed consent

You may not qualify if:

  • Underlying physical or psychological condition prohibiting study completion
  • Clinically significant cardiac disease
  • Active or history of malignancy in the past 5 years
  • Serious infection within 1 month of screening
  • Acute illness within 30 days of Day 1
  • History of suicidal behavior or suicidal ideation
  • Active cigarette smokers and users of nicotine-containing products
  • Neurodegenerative disease
  • External respiratory support or supplemental oxygen requirement
  • HIV, hepatitis B and hepatitis C positive
  • Vaccines within 14 days
  • Other investigational products within 30 days
  • Blood donation within 30 days
  • Plasma donation within 7 days
  • Pregnant or breastfeeding

Contact the study team to confirm eligibility.

Sponsors & Collaborators

MeSH Terms

Conditions

Amyotrophic Lateral Sclerosis

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesMotor Neuron DiseaseNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Central Study Contacts

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

January 6, 2026

First Posted

January 8, 2026

Study Start

March 1, 2026

Primary Completion (Estimated)

December 31, 2027

Study Completion (Estimated)

March 1, 2028

Last Updated

March 2, 2026

Record last verified: 2026-02

Data Sharing

IPD Sharing
Will not share