NCT00561366

Brief Summary

Arimoclomol is a small molecule that upregulates "molecular chaperones" in cells under stress. Arimoclomol extends survival by five weeks when given both pre-symptomatically and at disease onset in a mutant superoxide dismutase (SOD1) transgenic mouse model of ALS. Furthermore, it has been demonstrated to have neuroprotective and neuroregenerative effects in other rat models of nerve damage. Molecular chaperone proteins are critical in the cellular response to stress and protein misfolding. Recent data suggest that the SOD1 mutation responsible for ALS in some patients with familial disease reduces the availability of a variety of molecular chaperones, and thus weakens their ability to respond to cellular stress. Protein misfolding and consequent aggregation may play a role in the pathogenesis of both the familial and sporadic forms of ALS. Therapeutic agents such as arimoclomol that improve cellular chaperone response to protein misfolding may be helpful in ALS.

Trial Health

40
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Geographic Reach
2 countries

35 active sites

Status
withdrawn

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

November 16, 2007

Completed
4 days until next milestone

First Posted

Study publicly available on registry

November 20, 2007

Completed
Last Updated

February 9, 2012

Status Verified

February 1, 2012

First QC Date

November 16, 2007

Last Update Submit

February 8, 2012

Conditions

Keywords

ALSLou Gehrig's disease

Outcome Measures

Primary Outcomes (1)

  • ALSFRS-R

    9 months

Secondary Outcomes (6)

  • ALSFRS-R

    18 months

  • Survival

    18 months

  • Muscle strength

    9 and 18 months

  • Pulmonary function

    9 and 18 months

  • MUNE

    9 and 18 months

  • +1 more secondary outcomes

Study Arms (2)

1

PLACEBO COMPARATOR
Drug: Placebo

2

EXPERIMENTAL
Drug: Arimoclomol

Interventions

Placebo t.i.d.

1

capsule, 400 mg t.i.d.

2

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Familial or sporadic ALS.
  • Diagnosed with laboratory-supported probable, probable or definite ALS according to the World Federation of Neurology El Escorial criteria for less than or equal to 36 months' duration prior to the Screening Visit.
  • Vital capacity (VC) equal to or greater than 70% predicted value for gender, height and age at the Screening Visit.
  • Geographic accessibility to the study site.
  • Ability to take oral medication at the Screening Visit, based on verbal report.
  • Fluency in English, Spanish or Canadian French.

You may not qualify if:

  • History of known sensitivity or intolerability to arimoclomol or to any other related compound.
  • Prior exposure to arimoclomol through a clinical trial or physician-sponsored IND.
  • Exposure to any investigational agent within 30 days of the Screening Visit.
  • Presence of any of the following clinical conditions:
  • Substance abuse within the past year
  • Unstable cardiac, pulmonary, renal, hepatic, endocrine, hematologic, or active malignancy or infectious disease
  • AIDS or AIDS-related complex
  • Unstable psychiatric illness defined as psychosis (hallucinations or delusions), untreated major depression within 90 days of the Screening Visit.
  • Laboratory values: Screening serum creatinine greater than or equal to 1.5 mg/dL, creatinine clearance less than 70 cc/min, alanine aminotransferase (ALT) greater than 3.0 times the upper limit of normal, total bilirubin greater than 1.5 times the upper limit of normal, white blood cell (WBC) count less than 3,500/mm3, platelet concentration of \<100,000/ul, hematocrit level of less than 33 % for female or less than 35 % for male, or coagulation tests (PT, PTT) greater than or equal to 1.5 times upper limit of normal.
  • Female volunteers who are breast-feeding.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (35)

University of California Los Angeles - Tier 2 Site

Pacific Palisades, California, 90272, United States

Location

University of California - San Francisco - Tier 2 Site

San Francisco, California, 94117, United States

Location

University of Colorado Health Sciences Center - Tier 2 Site

Denver, Colorado, 80262, United States

Location

University of Miami - Tier 2 Site

Miami, Florida, 33136, United States

Location

Emory University - Tier 2 site

Atlanta, Georgia, 30322, United States

Location

Northwestern University, Dept. of Neurology - Tier 2 Site

Chicago, Illinois, 60611, United States

Location

University of Kansas Medical Center - Tier 2 site

Kansas City, Kansas, 66160, United States

Location

John Hopkins University - Tier 2 Site

Baltimore, Maryland, 21287, United States

Location

Massachusetts General Hospital - Tier 1 Site

Boston, Massachusetts, 02114, United States

Location

Baystate Medical Center - Tier 2 Site

Springfield, Massachusetts, 01199, United States

Location

Saint Louis University, Neuromuscular Div. - Tier 2 Site

St Louis, Missouri, 63110, United States

Location

Washington University - Tier 2 Site

St Louis, Missouri, 63110, United States

Location

BryanLGH Medical Center - Tier 2 Site

Lincoln, Nebraska, 68506, United States

Location

Upstate Clinical Research, LLC - Tier 2 Site

Albany, New York, 12205, United States

Location

Mount Sinai School of Medicine - Tier 2 Site

New York, New York, 10029, United States

Location

Columbia University Medical Center - Tier 2 site

New York, New York, 10032, United States

Location

SUNY Downstate Medical Center - Tier 1 Site

Syracuse, New York, 13210, United States

Location

Duke University Medical Center - Tier 1 Site

Durham, North Carolina, 27705, United States

Location

Wake Forest University School of Medicine -Tier 2 Site

Winston-Salem, North Carolina, 27157, United States

Location

Cleveland Clinic Foundation -Tier 2 site

Cleveland, Ohio, 44195, United States

Location

Providence ALS Center - Tier 2 Site

Portland, Oregon, 97213, United States

Location

Pennsylvania State University School of Medicine - Tier 2 Site

Hershey, Pennsylvania, 17033, United States

Location

Drexel University College of Medicine - Tier 1 Site

Philadelphia, Pennsylvania, 19107, United States

Location

University of Pittsburgh Medical Center - Tier 2 Site

Pittsburgh, Pennsylvania, 15213, United States

Location

Vanderbilt University Medical Center - Tier 2

Nashville, Tennessee, 37232-2551, United States

Location

Texas Neurology, PA - Tier 2 Site

Dallas, Texas, 75214, United States

Location

University of Texas Health Science Center - Tier 2 Site

San Antonio, Texas, 78229-3900, United States

Location

University of Vermont, College of Medicine - Tier 2

Burlington, Vermont, 05405, United States

Location

University of Virginia - Tier 2 Sites

Charlottesville, Virginia, 22908, United States

Location

Virginia Mason Clinic - Tier 2 Site

Seattle, Washington, 98101, United States

Location

Medical College of Wisconsin - Tier 2 Site

Milwaukee, Wisconsin, 53226, United States

Location

University of British Columbia, Gordon and Leslie Diamond Health Care Centre - Tier 2 Site

Vancouver, British Columbia, V5Z 2G9, Canada

Location

London Health Science Center - Tier 2 Site

London, Ontario, N6A 5A5, Canada

Location

University of Toronto, Sunnybrook Health Sciences Centre - Tier 2 Site

Toronto, Ontario, M4N 3M5, Canada

Location

Montreal Neurological Institute - Tier 2

Montreal, Quebec, H3A 2B4, Canada

Location

MeSH Terms

Conditions

Amyotrophic Lateral Sclerosis

Interventions

arimoclomol

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesMotor Neuron DiseaseNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Study Officials

  • Merit Cudkowicz, MD, MSc

    Massachusetts General Hospital

    PRINCIPAL INVESTIGATOR
  • Jeremy Shefner, MD, PhD

    State University of New York - Upstate Medical University

    PRINCIPAL INVESTIGATOR
0

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

November 16, 2007

First Posted

November 20, 2007

Last Updated

February 9, 2012

Record last verified: 2012-02

Locations