NCT06957002

Brief Summary

The purpose of this study is to determine whether a treatment with 3 months of bosentan associated to standard therapy might be superior to glucocorticoids alone in term of failure free survival at 12 months

Trial Health

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Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
40

participants targeted

Target at P25-P50 for phase_2

Timeline
49mo left

Started Jun 2026

Typical duration for phase_2

Geographic Reach
1 country

1 active site

Status
not yet recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

March 24, 2025

Completed
1 month until next milestone

First Posted

Study publicly available on registry

May 4, 2025

Completed
1.1 years until next milestone

Study Start

First participant enrolled

June 1, 2026

Expected
3 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 1, 2029

1 year until next milestone

Study Completion

Last participant's last visit for all outcomes

June 1, 2030

Last Updated

May 6, 2026

Status Verified

April 1, 2026

Enrollment Period

3 years

First QC Date

March 24, 2025

Last Update Submit

April 30, 2026

Conditions

Keywords

Giant Cell ArteritisBosentan

Outcome Measures

Primary Outcomes (1)

  • Failure free survival at Week 52

    A failure is defined by the occurrence of a relapse or the impossibility to decrease Glucocorticoids according to the predefined scheduled Glucocorticoids scheme.

    12 months ( Week 52)

Secondary Outcomes (11)

  • Proportion of new ischemic event

    12 months (Week 52)

  • Proportion of patients in remission without prednisone

    12 months (Week 52)

  • Proportion of patients in remission with prednisone ≤5 mg/day

    12 months (Week 52)

  • Cumulative dose of prednisone

    12 months (Week 52)

  • Proportion of patient in remission

    2 years

  • +6 more secondary outcomes

Study Arms (2)

Bosentan + Glucocorticoids

EXPERIMENTAL

Bosentan : 62.5 mg bid for 4 weeks and 125 mg bid during 9 additional weeks Glucocorticoids : prespecified GC tapering schedule

Drug: Bosentan

Glucocorticoids

OTHER

prespecified GC tapering schedule

Drug: Glucocorticoids

Interventions

Bosentan : 62.5 mg twice a day for 4 weeks and 125 mg twice a day during 9 weeks (treatment length 3 months)

Bosentan + Glucocorticoids

prespecified GC tapering schedule

Glucocorticoids

Eligibility Criteria

Age50 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Patients having given their written informed consent prior to participation in the study
  • Patients affiliated with social security or CMU (profit or being entitled)
  • Diagnosis of GCA, as defined by the revised GCA diagnosis criteria. Patients must satisfy criteria 1-2-3 and 4 (irrespective of time):
  • Age ≥50 years at disease onset
  • History of erythrocyte sedimentation rate (ESR) ≥ 50 mm/h or CRP ≥ 20 mg/L (not mandatory if TAB is positive: see below)
  • At least one of the following:
  • unequivocal cranial symptoms of GCA (new onset headache, scalp tenderness, jaw claudication, temporal artery abnormality, ischemia-related vision loss)
  • unequivocal symptoms of polymyalgia rheumatica (PMR)
  • At least one of the following:
  • Temporal artery biopsy (TAB) compatible with the diagnosis of GCA (non-necrotizing vasculitis with a predominance of mononuclear cell infiltration or granulomatous inflammation, usually with multinucleated giant cells)
  • Evidence of large vessel vasculitis:
  • angio-CT or angio-MRI: thickened and/or contrast-enhanced arteries especially aorta (≥2mm) and epiaortic arteries (≥1mm) and contrast enhanced arteries in T1-weighted sequences
  • or PET scan: ≥ grade 2 (from 0 to 3) tracer uptake on large arteries
  • At least a sign of active GCA within the 2 weeks prior to randomisation. Active GCA is defined by ESR ≥30 mm/h or CRP ≥10 mg/L and at least one of the following:
  • unequivocal cranial symptoms of GCA (new onset localized headache, scalp or temporal artery tenderness, ischemia-related vision loss, or otherwise unexplained mouth or jaw pain upon mastication)
  • +2 more criteria

You may not qualify if:

  • Patients under maintenance of justice, wardship or legal guardianship
  • Patient unable to give written informed consent prior to participation in the study
  • Patients included in other investigational therapeutic study within the previous 3 months
  • Patients suspected not to be observant to the proposed treatments
  • Weight \<40 Kg or \> 100 Kg
  • Moderate to severe hepatic impairment, i.e., Child-Pugh class B or C. History of chronic alcohol abuse (consumption \> 20 g/day)
  • Severe chronic heart failure or severe systolic dysfunction
  • Recent (\< 3 months) or incoming surgery requiring a general anaesthesia
  • Hypersensitivity to bosentan or one of its excipients
  • Prior treatment with any of the following:
  • Cell-depleting agents (i.e., anti-CD20)
  • Alkylating agents including cyclophosphamide
  • Ongoing treatment with glibenclamide, fluconazole and rifampicin. Concomitant administration of both a CYP3A4 inhibitor or a CYP2C9 inhibitor
  • Long-course systemic glucocorticoid therapy for other conditions than GCA or PMR
  • Laboratory abnormalities: AST or ALT \>3 x upper limit of normal (ULN)
  • +3 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Unité de Recherche Clinique, Entrepôts de données et Pharmacologie GHU Paris Centre

Paris, 75005, France

Location

MeSH Terms

Conditions

Giant Cell Arteritis

Interventions

BosentanGlucocorticoids

Condition Hierarchy (Ancestors)

Vasculitis, Central Nervous SystemAutoimmune Diseases of the Nervous SystemNervous System DiseasesCerebrovascular DisordersBrain DiseasesCentral Nervous System DiseasesVascular DiseasesCardiovascular DiseasesArteritisVasculitisSkin Diseases, VascularSkin DiseasesSkin and Connective Tissue DiseasesAutoimmune DiseasesImmune System Diseases

Intervention Hierarchy (Ancestors)

BenzenesulfonamidesSulfonamidesAmidesOrganic ChemicalsBenzene DerivativesHydrocarbons, AromaticHydrocarbons, CyclicHydrocarbonsSulfonesSulfur CompoundsPyrimidinesHeterocyclic Compounds, 1-RingHeterocyclic CompoundsAdrenal Cortex HormonesHormonesHormones, Hormone Substitutes, and Hormone AntagonistsPhysiological Effects of DrugsPharmacologic ActionsChemical Actions and Uses

Study Officials

  • Luc MOUTHON, Pr

    Hôpital Cochin, Department of Internal Medicine - 75014, Paris

    STUDY DIRECTOR

Central Study Contacts

Alexis REGENT, Pr

CONTACT

Charly LARRIEU, Project advisor

CONTACT

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

March 24, 2025

First Posted

May 4, 2025

Study Start (Estimated)

June 1, 2026

Primary Completion (Estimated)

June 1, 2029

Study Completion (Estimated)

June 1, 2030

Last Updated

May 6, 2026

Record last verified: 2026-04

Data Sharing

IPD Sharing
Will not share

Locations