NCT06915766

Brief Summary

The purpose of this expanded access program (EAP) protocol is to provide investigational bezuclastinib to patients with a diagnosis of nonadvanced systemic mastocytosis (NonAdvSM) or advanced systemic mastocytosis (AdvSM) who have received and failed or been intolerant to at least one standard approved therapy and/or have no comparable or satisfactory alternative therapy options.

Trial Health

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Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Geographic Reach
1 country

18 active sites

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

March 31, 2025

Completed
8 days until next milestone

First Posted

Study publicly available on registry

April 8, 2025

Completed
Last Updated

March 9, 2026

Status Verified

March 1, 2026

First QC Date

March 31, 2025

Last Update Submit

March 6, 2026

Conditions

Keywords

Systemic MastocytosisNonAdvanced Systemic MastocytosisAdvanced Systemic MastocytosisSystemic Mastocytosis with an associated hematologic neoplasm (SM-AHN)Aggressive Systemic Mastocytosis (ASM)Mast Cell Leukemia (MCL)Bone Marrow Mastocytosis (BMM)

Interventions

Drug: Bezuclastinib Tablets

Also known as: CGT9486

Eligibility Criteria

Age18 Years+
Sexall
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Able to provide written informed consent and commit to EAP assessments.
  • ≥18 years of age.
  • Able to swallow tablets.
  • Diagnosed with ASM, SM-AHN, MCL, BMM, ISM, or SSM according to the 2022 WHO Classification for SM
  • Not receiving adequate disease control on current therapy(ies).
  • Have clinically acceptable laboratory screening results.

You may not qualify if:

  • Patients who are eligible for and/or enrolled in an on-going bezuclastinib clinical trial.
  • Patients who discontinued investigational use of bezuclastinib in previous clinical trials due to toxicity or withdrawal of consent.
  • Pregnant or currently breastfeeding.
  • Prior or ongoing clinically significant illness or medical or physical condition
  • Other protocol-defined criteria apply.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (18)

Orso Health/Modena Asthma Allergy

La Jolla, California, 92037, United States

AVAILABLE

Scripps Green Hospital

La Jolla, California, 92037, United States

AVAILABLE

UCLA Ronald Reagan Medical Center

Los Angeles, California, 90095, United States

AVAILABLE

Sneeze Wheeze & Itch Associates LLC Clinical Research Center

Normal, Illinois, 61761, United States

AVAILABLE

Indiana University Health

Indianapolis, Indiana, 46202, United States

AVAILABLE

Walter Reed

Bethesda, Maryland, 20889, United States

AVAILABLE

AllerVie Health

Glenn Dale, Maryland, 20769, United States

AVAILABLE

Boston Specialists

Boston, Massachusetts, 02111, United States

AVAILABLE

Dana Farber Cancer Institute

Boston, Massachusetts, 02215, United States

AVAILABLE

Michigan Medicine- University of Michigan

Ann Arbor, Michigan, 48109, United States

AVAILABLE

Mayo Clinic

Rochester, Minnesota, 55905, United States

AVAILABLE

Dartmouth-Hitchcock Medical Center

Lebanon, New Hampshire, 03756, United States

AVAILABLE

Memorial Sloan Kettering Cancer Center

New York, New York, 10065, United States

AVAILABLE

Duke Blood Cancer Center

Durham, North Carolina, 27705, United States

AVAILABLE

The Ohio State University Wexner Medical Center

Columbus, Ohio, 43210, United States

AVAILABLE

AIR Care

Dallas, Texas, 75231, United States

AVAILABLE

Texas Children's Hospital

Houston, Texas, 77030, United States

AVAILABLE

The University of Texas, MD Anderson Cancer Center

Houston, Texas, 77030, United States

AVAILABLE

MeSH Terms

Conditions

Mastocytosis, SystemicLeukemia, Mast-Cell

Condition Hierarchy (Ancestors)

MastocytosisNeoplasms, Connective TissueNeoplasms, Connective and Soft TissueNeoplasms by Histologic TypeNeoplasmsMast Cell Activation DisordersImmune System DiseasesLeukemiaLeukemia, Myeloid, AcuteLeukemia, MyeloidHematologic DiseasesHemic and Lymphatic Diseases

Study Officials

  • Rachael Easton, MD, PhD

    Cogent Biosciences, Inc.

    STUDY DIRECTOR

Central Study Contacts

Alexandra Malinowski, PharmD

CONTACT

Study Design

Study Type
expanded access
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

March 31, 2025

First Posted

April 8, 2025

Last Updated

March 9, 2026

Record last verified: 2026-03

Locations