NCT05312983

Brief Summary

Age-related hearing loss, or presbycusis, is caused by many genetic and environmental factors. Its prevalence poses a public health challenge of early identification and effective hearing aid treatment. However, the lack of screening and of a validated audiological test battery to diagnose an individual's needs and to guide hearing aid adjustments is a major obstacle. Furthermore, monogenic forms of hearing loss affect only one functional module of hearing. The audiological test(s) dependent on the function of this module are affected, in a progressive manner, but not the others. A previous study showed that in early onset presbycusis patients, a quarter of the subjects tested were affected by monogenic presbycusis. The collection of audiological and vestibular tests, carried out on proven monogenic presbycusis patients and compared to that of normal hearing patients, would constitute a battery of tests allowing a precision diagnosis, then developed to all forms of presbycusis in order to study if the identification of abnormal functional modules can usefully guide the diagnosis and the early fitting.

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
700

participants targeted

Target at P75+ for not_applicable

Timeline
57mo left

Started Jul 2022

Longer than P75 for not_applicable

Geographic Reach
1 country

2 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

Study Progress45%
Jul 2022Dec 2030

First Submitted

Initial submission to the registry

February 25, 2022

Completed
1 month until next milestone

First Posted

Study publicly available on registry

April 6, 2022

Completed
4 months until next milestone

Study Start

First participant enrolled

July 28, 2022

Completed
5.4 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 31, 2027

Expected
3 years until next milestone

Study Completion

Last participant's last visit for all outcomes

December 31, 2030

Last Updated

March 3, 2025

Status Verified

February 1, 2025

Enrollment Period

5.4 years

First QC Date

February 25, 2022

Last Update Submit

February 28, 2025

Conditions

Keywords

presbyacusisagingaudiologygenetic

Outcome Measures

Primary Outcomes (1)

  • Measurement of specificity and sensitivity of the audiological test battery in participants with early-onset presbycusis after identification of pathogenic variants by sequencing and division into subgroups.

    specifity and sensitivity will be calculated to identify which tests or combinations of audiological and vestibular tests will be the most discriminating in characterizing each functional module of hearing from participants with monogenic forms of presbycusis of anticipated onset, each affecting a determined functional module, in comparison with an age-matched control group.

    2 years

Secondary Outcomes (2)

  • Normative values for audiological and vestibular tests will be determined

    4 years and 6 months

  • Whole-exome sequencing of samples from participants with non-monogenic presbycusis

    4 years and 6 months

Study Arms (1)

people over the age of 18 who agree to participate in the research.

EXPERIMENTAL

They are either people who have a hearing loss about 20 years older than their age and wear a hearing aid (or come in for a hearing aid), or people over the age of 40 with normal hearing for their age.

Other: Audiological and vestibular testsOther: Blood samplingOther: neurocognitive self-questionnaire

Interventions

6h of audiological and vestibular tests divide in 3 sessions : * Session A : objective audiological tests * Session B ; subjective audiological tests * Session C : balance tests.

people over the age of 18 who agree to participate in the research.

A 10 mL blood sample will be collected during the study.

people over the age of 18 who agree to participate in the research.

Four self-questionnaires to fill out to measure sleep quality, memory and emotional state

people over the age of 18 who agree to participate in the research.

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersYes
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • For all participants:
  • Be over the age of 18,
  • Be affiliated to a social security system,
  • Have a good command of the French language (oral and written).
  • For the group of participants with anticipated presbycusis:
  • Over the age of 40, having a hearing aid recipient or coming for a first hearing aid recipient
  • Between 18 and 40, having a hearing aid recipient, coming for a first hearing aid recipient or declare a progressive genetic birth defect
  • For healthy volunteers:
  • \- Have no known hearing loss.

You may not qualify if:

  • Report having been chronically exposed to loud sounds.
  • Have a history of ototoxic substances,
  • To have sequelae of ear infections and/or a history of ENT disease that permanently affects hearing or balance,
  • Have an ethnic origin for which the Pasteur Institute does not have information on the frequency of variants of the genes studied.
  • Have type II diabetes,
  • Have a neurological or psychiatric condition that interferes with comprehension or ability to move,
  • Be under guardianship,
  • Be deprived of liberty by judicial or administrative decision, or be subject to legal protection,
  • Not being subject to a social security system,
  • Taking narcotic substances, alcohol or medication that diminishes cognitive abilities.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (2)

Laboratoire de correction auditive

Paris, 75001, France

NOT YET RECRUITING

CEntre de Recherche et d'Innovation en Audiologie Humaine

Paris, 75012, France

RECRUITING

MeSH Terms

Conditions

Presbycusis

Interventions

Blood Specimen Collection

Condition Hierarchy (Ancestors)

Hearing Loss, SensorineuralHearing LossHearing DisordersEar DiseasesOtorhinolaryngologic DiseasesSensation DisordersNeurologic ManifestationsNervous System DiseasesSigns and SymptomsPathological Conditions, Signs and Symptoms

Intervention Hierarchy (Ancestors)

Specimen HandlingClinical Laboratory TechniquesDiagnostic Techniques and ProceduresDiagnosisPuncturesSurgical Procedures, OperativeInvestigative Techniques

Study Officials

  • Paul Avan, MD

    CERIAH

    PRINCIPAL INVESTIGATOR

Central Study Contacts

Study Design

Study Type
interventional
Phase
not applicable
Allocation
NA
Masking
NONE
Purpose
DIAGNOSTIC
Intervention Model
SINGLE GROUP
Model Details: 2 groups : * 500 participants with early onset presbycusis * 200 participants with normal hearing for their age
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 25, 2022

First Posted

April 6, 2022

Study Start

July 28, 2022

Primary Completion (Estimated)

December 31, 2027

Study Completion (Estimated)

December 31, 2030

Last Updated

March 3, 2025

Record last verified: 2025-02

Locations