NCT05066217

Brief Summary

This is a multicenter, Phase 3, randomized, double-blind, placebo-controlled study designed to evaluate the efficacy and safety of clemizole HCL (EPX-100) as adjunctive therapy in children and adult participants with Lennox-Gastaut syndrome (LGS).

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
260

participants targeted

Target at P50-P75 for phase_3

Timeline
43mo left

Started Apr 2025

Longer than P75 for phase_3

Geographic Reach
1 country

20 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress24%
Apr 2025Nov 2029

First Submitted

Initial submission to the registry

September 23, 2021

Completed
11 days until next milestone

First Posted

Study publicly available on registry

October 4, 2021

Completed
3.5 years until next milestone

Study Start

First participant enrolled

April 9, 2025

Completed
1.6 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

November 1, 2026

Expected
3 years until next milestone

Study Completion

Last participant's last visit for all outcomes

November 1, 2029

Last Updated

April 15, 2026

Status Verified

April 1, 2026

Enrollment Period

1.6 years

First QC Date

September 23, 2021

Last Update Submit

April 13, 2026

Conditions

Keywords

Lennox Gastaut SyndromeLennox-Gastaut SyndromeLGSClemizole HClSeizure

Outcome Measures

Primary Outcomes (1)

  • Percent Change in CMMS-28

    Percent change in CMMS-28 from the Baseline Period through the end of the DB Period

    From Baseline Period up to 16 weeks

Secondary Outcomes (10)

  • Proportion of Participants with ≥50% Reduction in CMMS-28

    From Baseline Period up to 16 weeks

  • Percent Change in CMMS-28 Seizure-free Days

    From Baseline Period up to 16 weeks

  • Clinical Global Impression of Change (CGI-C) Score

    Week 16

  • Caregiver Global Impression of Change (CaGI-C) Score

    Week 16

  • Caregiver Global Impression of Change in Seizure Intensity/Duration (CaGI-CSID) Score

    Week 16

  • +5 more secondary outcomes

Study Arms (3)

Placebo

PLACEBO COMPARATOR

Participants will receive their first dose of study drug following randomization.

Drug: Placebo

Double-blind clemizole HCl

EXPERIMENTAL

Participants will receive their first dose of study drug following randomization.

Drug: Clemizole HCl

Open-label clemizole HCl

EXPERIMENTAL

Eligible participants who complete the DB Period will have the option to continue in the OLE Period, during which they will receive clemizole HCl for up to 3 years.

Drug: Clemizole HClDrug: Placebo

Interventions

Clemizole HCl will be administered as an oral solution.

Also known as: EPX-100
Double-blind clemizole HClOpen-label clemizole HCl

Placebo will be administered as an oral solution.

Open-label clemizole HClPlacebo

Eligibility Criteria

Age2 Years - 55 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Males or females, ages ≥2 to ≤55 years, at the time of Screening.
  • Participant/parent/legal authorized representative (LAR) willing and able to give written informed consent/assent.
  • Diagnosis of LGS, including:
  • Evidence of at least one type of countable major motor seizure.
  • History of electroencephalogram (EEG) consistent with LGS (abnormal background activity, and one of the following: 1) slow spike-wave discharges \[\<2.5 Hz\], or 2) paroxysmal fast activity during sleep).
  • Abnormal cognitive development.
  • Onset of seizures at 11 years of age or younger.

You may not qualify if:

  • Known sensitivity, allergy, or previous exposure to clemizole HCl.
  • Known history of long QT syndrome or any significant history of a serious abnormality of the electrocardiogram (ECG) (e.g., recent myocardial infarction, clinically significant arrhythmia).
  • Family history of sudden cardiac death, unexplained death, or death from a primary dysrhythmia potentially associated with QT prolongation in any family member.
  • Seizures secondary to illicit drug or alcohol use, infection, neoplasm, demyelinating disease, degenerative neurological disease, or progressive central nervous system disease, metabolic illness, recent anoxic episode within the last 6 months requiring resuscitation, or progressive degenerative disease or any other condition, which in the opinion of the investigator, could affect seizure control.
  • Epilepsy surgery planned during the study or epilepsy surgery within 6 months prior to Screening.
  • Concomitant use of fenfluramine.
  • Prior or concomitant use of lorcaserin.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (20)

Arkansas Children's Hospital

Little Rock, Arkansas, 72202, United States

ACTIVE NOT RECRUITING

UC Irvine Medical Center

Orange, California, 92868, United States

ACTIVE NOT RECRUITING

UCI Center for Innovative Health Therapies

Orange, California, 92868, United States

RECRUITING

Nemours Children's Health

Wilmington, Delaware, 19803, United States

NOT YET RECRUITING

Rare Disease Research

Kissimmee, Florida, 34746, United States

SUSPENDED

University of Miami Miller School of Medicine

Miami, Florida, 33136, United States

RECRUITING

Pediatric Neurology and Epilepsy Specialists

Winter Park, Florida, 32789, United States

ACTIVE NOT RECRUITING

Re:Cognition Health

Chicago, Illinois, 60611, United States

RECRUITING

Norton Children's Medical Center

Louisville, Kentucky, 40202, United States

ACTIVE NOT RECRUITING

Henry Ford Hospital

Detroit, Michigan, 48202, United States

ACTIVE NOT RECRUITING

Minnesota Epilepsy Group, P.A.

Roseville, Minnesota, 55102, United States

ACTIVE NOT RECRUITING

Children's Nebraska

Omaha, Nebraska, 68114, United States

ACTIVE NOT RECRUITING

Neurology Center for Epilepsy and Seizures

Marlboro, New Jersey, 07746, United States

RECRUITING

Tekton Research

Marlboro, New Jersey, 07746, United States

RECRUITING

Weill Cornell Medicine/New York Presbyterian Hospital

New York, New York, 10021, United States

RECRUITING

Atrium Health STRIVE Research

Charlotte, North Carolina, 28207, United States

ACTIVE NOT RECRUITING

On-Site Clinical Solution

Charlotte, North Carolina, 28211, United States

ACTIVE NOT RECRUITING

Duke University Medical Center

Durham, North Carolina, 27705, United States

RECRUITING

PPD Virtual-Science 37, Inc.

Morrisville, North Carolina, 27560, United States

ACTIVE NOT RECRUITING

UTHealth Houston

Houston, Texas, 77030, United States

ACTIVE NOT RECRUITING

MeSH Terms

Conditions

Lennox Gastaut SyndromeSeizures

Condition Hierarchy (Ancestors)

Epileptic SyndromesEpilepsyBrain DiseasesCentral Nervous System DiseasesNervous System DiseasesGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesNeurologic ManifestationsSigns and SymptomsPathological Conditions, Signs and Symptoms

Study Officials

  • Amit Ray, MD

    Harmony Biosciences Management, Inc.

    STUDY DIRECTOR

Central Study Contacts

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
TRIPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Model Details: Patients are randomized 1:1 to clemizole HCl (EPX-100) or placebo.
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

September 23, 2021

First Posted

October 4, 2021

Study Start

April 9, 2025

Primary Completion (Estimated)

November 1, 2026

Study Completion (Estimated)

November 1, 2029

Last Updated

April 15, 2026

Record last verified: 2026-04

Data Sharing

IPD Sharing
Will not share

Locations