NCT04920812

Brief Summary

MITOMICS aims to determine which RNA-Seq results (from muscle or fibroblasts) are the most informative for the interpretation of VUS identified by WES for patients suspected of mitochondrial myopathy. Analysis of RNA-Seq and WES results will performed with a computational approach using an autoencoder-based method

Trial Health

57
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Enrollment
66

participants targeted

Target at P25-P50 for all trials

Timeline
Completed

Started Mar 2022

Typical duration for all trials

Geographic Reach
1 country

9 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

June 4, 2021

Completed
6 days until next milestone

First Posted

Study publicly available on registry

June 10, 2021

Completed
9 months until next milestone

Study Start

First participant enrolled

March 7, 2022

Completed
Same day until next milestone

Primary Completion

Last participant's last visit for primary outcome

March 7, 2022

Completed
3.5 years until next milestone

Study Completion

Last participant's last visit for all outcomes

September 7, 2025

Completed
Last Updated

February 25, 2025

Status Verified

February 1, 2025

Enrollment Period

Same day

First QC Date

June 4, 2021

Last Update Submit

February 21, 2025

Conditions

Outcome Measures

Primary Outcomes (1)

  • number of variations interpreted as responsible for the Mitochondrial diseases

    • Comparison of the number of variations (splicing variant, expression level) or VUS, identified in WES, interpreted as responsible for the disease (class 4 or 5 variants) thanks to the RNA-Seq carried out at from a muscle biopsy or RNA-Seq performed from fibroblasts

    baseline

Secondary Outcomes (3)

  • RNA in mitochondiral deseases

    baseline

  • variation of RNA in mitochondiral deseases

    baseline

  • specific molecular signatures of mitochondiral deseases

    baseline

Study Arms (1)

Mitochondrial diseases

annalysing with methology of multi-OMICS integration we will determined which RNA-Seq data (from muscle or fibroblasts) are the most informative for the interpretation of VUS identified by WES for patients suspected of mitochondrial myopathy.

Genetic: diagnosis of mitochondrial myopathy

Interventions

• Determination of the presence of specific molecular signatures at the RNA level in muscles and fibroblasts from patients

Mitochondrial diseases

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Patients are seen in consultation by the genetic doctors of the different centers as part of the usual management of their mitochondrial disease.

You may qualify if:

  • Patients suspected of a mitochondrial disease with muscular signs (clinical, histological or biochemical)
  • Patients with negative mtDNA and WES NGS in trio
  • Patients with routine muscle and skin biopsies available
  • Blood samples from parents and / or relatives available for segregation studies
  • Informed consent of the study signed by the patient or the legal representatives of the minor patient or under guardianship
  • Patients affiliated to social security

You may not qualify if:

  • Patients with suspected mitochondrial disease without muscle involvement
  • Patients for whom the mtDNA NGS and WES have not been performed
  • Patients with suspected mitochondrial disease with causal variant identified
  • Refusal to sign the informed consent for the study
  • Insufficient amount of frozen material or culture failure for fibroblasts

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (9)

CHU de Nice

Nice, CHU de NICE, 06003, France

RECRUITING

C.H.R.U. Brest

Brest, France, France

NOT YET RECRUITING

Chu de Nantes

Nantes, France, France

RECRUITING

chu Angers

Angers, France

RECRUITING

Chu Brest

Brest, France

NOT YET RECRUITING

APHM

Marseille, France

RECRUITING

APHM

Marseille, France

RECRUITING

Chu Montpellier

Montpellier, France

RECRUITING

CHU Nantes

Nantes, France

NOT YET RECRUITING

MeSH Terms

Conditions

Mitochondrial Diseases

Condition Hierarchy (Ancestors)

Metabolic DiseasesNutritional and Metabolic Diseases

Study Officials

  • SYLVIE BANNWARTH

    Centre Hospitalier Universitaire de Nice

    PRINCIPAL INVESTIGATOR

Central Study Contacts

SYLVIE BANNWARTH

CONTACT

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
OTHER
Sponsor Type
OTHER
Responsible Party
SPONSOR

Study Record Dates

First Submitted

June 4, 2021

First Posted

June 10, 2021

Study Start

March 7, 2022

Primary Completion

March 7, 2022

Study Completion

September 7, 2025

Last Updated

February 25, 2025

Record last verified: 2025-02

Data Sharing

IPD Sharing
Will not share

Locations