NCT04918251

Brief Summary

The purpose of this observational study is to improve understanding of the biology of why ALS, MS and FTD have different effects on different people and facilitate better measurement of the disease in future drug testing. To do this, brain and spinal cord neural network functionality will be measured over time, in addition to profiling of movement and non-movement symptoms, in large groups of patients, as well as in a population-based sample of the healthy population. Patterns of dysfunction which relate to patients' diagnosis and coinciding and future symptoms which align with categories of patients with similar prognoses will be investigated and their ability to predict incident patients' symptoms in future will be measured.

Trial Health

43
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Enrollment
400

participants targeted

Target at P75+ for all trials

Timeline
Completed

Started Sep 2012

Longer than P75 for all trials

Geographic Reach
1 country

1 active site

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

September 1, 2012

Completed
8.6 years until next milestone

First Submitted

Initial submission to the registry

April 1, 2021

Completed
2 months until next milestone

First Posted

Study publicly available on registry

June 8, 2021

Completed
1.7 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

February 1, 2023

Completed
2 months until next milestone

Study Completion

Last participant's last visit for all outcomes

April 1, 2023

Completed
Last Updated

June 8, 2021

Status Verified

June 1, 2021

Enrollment Period

10.4 years

First QC Date

April 1, 2021

Last Update Submit

June 2, 2021

Conditions

Keywords

EEGTMSNeurodegenerationNetworkElectrophysiologyBiomarkersCognitiveBehaviouralMotor

Outcome Measures

Primary Outcomes (4)

  • Diagnosis-related difference in EEG or TMS measurements

    Differences in single or paired pulse TMS measures or time and/or frequency domain EEG characteristics between those within each patient cohort and controls

    Baseline recording

  • Prognosis-related EEG or TMS measurements

    Patient cohort single or paired pulse TMS measures or time and/or frequency domain EEG characteristics which show significant correlation to cognitive, behavioural, motor and/or sensory task performance, to disease duration or to survival time

    Baseline recording

  • Diagnosis-related changes in EEG or TMS measurements

    Differences in rate of change (slope) across time of single or paired pulse TMS measures or time and/or frequency domain EEG characteristics between those within each patient cohort relative to controls

    Baseline to final visit assessed up to 2 years after baseline

  • Prognosis-related changes in EEG or TMS measurements

    Rates of change (slope) across time of patient cohort single or paired pulse TMS measures or time and/or frequency domain EEG characteristics which show significant correlation to cognitive, behavioural, motor and/or sensory task performance, to disease duration or to survival time

    Baseline to final visit assessed up to 2 years after baseline

Secondary Outcomes (2)

  • Diagnosis-specific changes in EEG or TMS measurements

    Baseline to final visit assessed up to 2 years after baseline

  • Diagnosis-specific difference in EEG or TMS measurements

    Baseline recording

Study Arms (4)

Controls

Individuals from the Irish population with no psychiatric, psychological, neurological or muscular disease diagnosis

Procedure: 128 electrode electroencephalography (EEG)Procedure: Transcranial magnetic stimulation (TMS)

Amyotrophic lateral sclerosis patients

Procedure: 128 electrode electroencephalography (EEG)Procedure: Transcranial magnetic stimulation (TMS)

Multiple sclerosis patients

Procedure: 128 electrode electroencephalography (EEG)Procedure: Transcranial magnetic stimulation (TMS)

Frontotemporal dementia patients

Procedure: 128 electrode electroencephalography (EEG)Procedure: Transcranial magnetic stimulation (TMS)

Interventions

128 electrode EEG will be non-invasively recorded from electrodes placed in a montage over the scalp while the participant is resting or performing tasks designed to engage specific cortical motor networks of interest (cognitive, behavioural, motor and sensory)

Amyotrophic lateral sclerosis patientsControlsFrontotemporal dementia patientsMultiple sclerosis patients

Single and paired pulse TMS protocol will be delivered while surface bipolar EMG is recorded over hand muscles to interrogate corticospinal tract function and cortical motor network component functions

Amyotrophic lateral sclerosis patientsControlsFrontotemporal dementia patientsMultiple sclerosis patients

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersYes
Age GroupsAdult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Healthy controls and patients diagnosed with ALS, FTD or MS

You may qualify if:

  • Age \>18 years and able to give informed written or verbal (in the presence of two witnesses) consent.
  • In the case of non-control subjects, a clinical diagnosis of:
  • (i) Probable frontotemporal dementia (FTD) including behavioural variant FTD, semantic dementia or primary progressive aphasia) with supportive brain imaging or known FTD causing genetic mutation (ii) Multiple sclerosis (MS) according to the McDonald criteria (Polman et al., 2011) or (iii) Possible, probable or definite amyotrophic lateral sclerosis (ALS) according to the El Escorial Criteria Revised (Brooks et al. 2000)

You may not qualify if:

  • Any diagnosed neurological/muscular disease other than ALS, MS or FTD
  • Use of neuro- or myo-modulatory medications except riluzole
  • Inability to participate due to disease-related motor symptoms (e.g. inability to sit for the required time or click the mouse to respond)
  • Upper body metallic implants
  • History of seizure disorders in the participant or immediate family members
  • Anxiety-induced fainting
  • Regular migraine
  • Evidence of significant respiratory insufficiency
  • Sleep time \>2 hours below normal and/or alcohol consumption the night before data collection (in which case, recording session will be rescheduled).

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Academic Unit of Neurology, Trinity College Dublin, The University of Dublin

Dublin, Leinster, Dublin 2, Ireland

RECRUITING

Related Publications (7)

  • McMackin R, Dukic S, Broderick M, Iyer PM, Pinto-Grau M, Mohr K, Chipika R, Coffey A, Buxo T, Schuster C, Gavin B, Heverin M, Bede P, Pender N, Lalor EC, Muthuraman M, Hardiman O, Nasseroleslami B. Dysfunction of attention switching networks in amyotrophic lateral sclerosis. Neuroimage Clin. 2019;22:101707. doi: 10.1016/j.nicl.2019.101707. Epub 2019 Feb 2.

  • Dukic S, McMackin R, Buxo T, Fasano A, Chipika R, Pinto-Grau M, Costello E, Schuster C, Hammond M, Heverin M, Coffey A, Broderick M, Iyer PM, Mohr K, Gavin B, Pender N, Bede P, Muthuraman M, Lalor EC, Hardiman O, Nasseroleslami B. Patterned functional network disruption in amyotrophic lateral sclerosis. Hum Brain Mapp. 2019 Nov 1;40(16):4827-4842. doi: 10.1002/hbm.24740. Epub 2019 Jul 26.

  • McMackin R, Dukic S, Costello E, Pinto-Grau M, Fasano A, Buxo T, Heverin M, Reilly R, Muthuraman M, Pender N, Hardiman O, Nasseroleslami B. Localization of Brain Networks Engaged by the Sustained Attention to Response Task Provides Quantitative Markers of Executive Impairment in Amyotrophic Lateral Sclerosis. Cereb Cortex. 2020 Jul 30;30(9):4834-4846. doi: 10.1093/cercor/bhaa076.

  • McMackin R, Dukic S, Costello E, Pinto-Grau M, Keenan O, Fasano A, Buxo T, Heverin M, Reilly R, Pender N, Hardiman O, Nasseroleslami B. Sustained attention to response task-related beta oscillations relate to performance and provide a functional biomarker in ALS. J Neural Eng. 2021 Feb 25;18(2). doi: 10.1088/1741-2552/abd829.

  • Iyer PM, Mohr K, Broderick M, Gavin B, Burke T, Bede P, Pinto-Grau M, Pender NP, McLaughlin R, Vajda A, Heverin M, Lalor EC, Hardiman O, Nasseroleslami B. Mismatch Negativity as an Indicator of Cognitive Sub-Domain Dysfunction in Amyotrophic Lateral Sclerosis. Front Neurol. 2017 Aug 15;8:395. doi: 10.3389/fneur.2017.00395. eCollection 2017.

  • Nasseroleslami B, Dukic S, Broderick M, Mohr K, Schuster C, Gavin B, McLaughlin R, Heverin M, Vajda A, Iyer PM, Pender N, Bede P, Lalor EC, Hardiman O. Characteristic Increases in EEG Connectivity Correlate With Changes of Structural MRI in Amyotrophic Lateral Sclerosis. Cereb Cortex. 2019 Jan 1;29(1):27-41. doi: 10.1093/cercor/bhx301.

  • Iyer PM, Egan C, Pinto-Grau M, Burke T, Elamin M, Nasseroleslami B, Pender N, Lalor EC, Hardiman O. Functional Connectivity Changes in Resting-State EEG as Potential Biomarker for Amyotrophic Lateral Sclerosis. PLoS One. 2015 Jun 19;10(6):e0128682. doi: 10.1371/journal.pone.0128682. eCollection 2015.

MeSH Terms

Conditions

Amyotrophic Lateral SclerosisFrontotemporal DementiaMultiple SclerosisNerve Degeneration

Interventions

Transcranial Magnetic Stimulation

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesMotor Neuron DiseaseNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic DiseasesFrontotemporal Lobar DegenerationDementiaBrain DiseasesNeurocognitive DisordersMental DisordersDemyelinating Autoimmune Diseases, CNSAutoimmune Diseases of the Nervous SystemDemyelinating DiseasesAutoimmune DiseasesImmune System DiseasesPathologic ProcessesPathological Conditions, Signs and Symptoms

Intervention Hierarchy (Ancestors)

Magnetic Field TherapyTherapeutics

Study Officials

  • Orla Hardiman, BSc MB BCh BAO MD FRCPI FAAN

    Academic Unit of Neurology, Trinity College Dublin, The University of Dublin

    PRINCIPAL INVESTIGATOR

Central Study Contacts

Orla Hardiman, BSc MB BCh BAO MD FRCPI FAAN

CONTACT

Roisin McMackin, BA PhD

CONTACT

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
PROSPECTIVE
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Professor of Neurology

Study Record Dates

First Submitted

April 1, 2021

First Posted

June 8, 2021

Study Start

September 1, 2012

Primary Completion

February 1, 2023

Study Completion

April 1, 2023

Last Updated

June 8, 2021

Record last verified: 2021-06

Data Sharing

IPD Sharing
Will share

Raw data from this study may be made available in anonymized form upon request from qualified investigators subject to the approval by the Data Protection Office (DPO) and Office of Corporate Partnership and Knowledge Exchanges (OCPKE) in Trinity College Dublin, the University of Dublin.

Shared Documents
STUDY PROTOCOL, SAP, ICF
Time Frame
Due to ethical constraint and the time required for data quality checks, data will only be made available in fully anonymised format following publication of results.

Locations