NCT04862221

Brief Summary

TReatment for ImmUne Mediated PathopHysiology (TRIUMPH) is a multi-center, three arm, randomized, controlled trial of immunosuppressive therapy for children with acute liver failure. The study will determine if suppressing inflammatory responses with either corticosteroids or equine anti-thymocyte globulin therapy improves survival for children with this rare, life-threatening condition.

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
163

participants targeted

Target at P75+ for phase_2

Timeline
9mo left

Started Feb 2022

Longer than P75 for phase_2

Geographic Reach
1 country

24 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress85%
Feb 2022Feb 2027

First Submitted

Initial submission to the registry

April 23, 2021

Completed
4 days until next milestone

First Posted

Study publicly available on registry

April 27, 2021

Completed
10 months until next milestone

Study Start

First participant enrolled

February 9, 2022

Completed
4.5 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

August 1, 2026

Expected
6 months until next milestone

Study Completion

Last participant's last visit for all outcomes

February 1, 2027

Last Updated

March 10, 2026

Status Verified

March 1, 2026

Enrollment Period

4.5 years

First QC Date

April 23, 2021

Last Update Submit

March 6, 2026

Conditions

Keywords

hepatic insufficiencyliver diseasesliver failureanti-thymocyte agents

Outcome Measures

Primary Outcomes (1)

  • Survival with native liver (SNL)

    Alive and without a liver transplant 21 days following randomization

    21 days

Secondary Outcomes (1)

  • Survival with native liver (SNL)

    180 days

Study Arms (4)

High-dose methylprednisolone

EXPERIMENTAL

Intravenous methylprednisolone at an initial dose of 10 mg/kg/day for 3 days, 5 mg/kg/day on day 4.

Drug: High-dose methylprednisoloneDrug: Prednisolone

Equine anti-thymocyte globulin

EXPERIMENTAL

Intravenous equine anti-thymocyte globulin at a dose of 40 mg/kg/day for 4 days.

Drug: Equine anti-thymocyte globulinDrug: PrednisoloneDrug: DiphenhydramineDrug: Methylprednisolone

Supportive care

PLACEBO COMPARATOR

Supportive care will be administered as determined by the clinical team at participating clinical sites in accordance with their local practices and standards.

Drug: Placebo for prednisoloneDrug: Placebo for infusions

Observational Cohort

NO INTERVENTION

This study includes a prospective observational cohort study of patients with Pediatric Acute Liver Failure who meet the randomized controlled trial eligibility criteria and are willing to provide longitudinal observational data. Patients who provide consent will receive the enrolling institution's standard of care and will be followed for up to 90-days for clinical (observational) assessments and biospecimen collection for the biorepository.

Interventions

Subjects in the high-dose methylprednisolone arm will receive an initial dose of methylprednisolone IV 10 mg/kg/day for 3 days and 5 mg/kg/day on Day 4. Normal saline will be used as placebo pre-medications and infusions given at the same volume and duration as the eATG infusions.

Also known as: Solu-Medrol
High-dose methylprednisolone

Subjects will receive eATG IV 40 mg/kg/day on Days 1- 4. Day 1 eATG infusion is run over 8 hours and Day 2-4 infusions are run over 4 hours.

Also known as: ATGAM
Equine anti-thymocyte globulin

Subjects will receive prednisolone 1 mg/kg on Days 5-13 followed by a gradual taper with discontinuation at 42 Days as indicated below. Days 5 - 13 Prednisolone PO 1 mg/kg/day (max 50 mg/day) Days 14- 20 Prednisolone PO 0.5 mg/kg/day (max 25 mg/day) Days 21 - 27 Prednisolone PO 0.3 mg/kg/day (max 15 mg/day) Days 28 - 34 Prednisolone PO 0.1 mg/kg/day (max 5 mg/day) Days 35 - 41 Prednisolone PO 0.1 mg/kg every OTHER day (max 5 mg every other day) Day 42 Discontinue

Also known as: 15 mg/mL oral solution National Drug Code: 0121-0885-08
Equine anti-thymocyte globulinHigh-dose methylprednisolone

Subjects will receive 1 mg/kg/day of oral placebo for prednisolone on days 5-13 followed by a gradual taper to discontinuation at 42 days as indicated below. Subjects receiving oral placebo will be given a solution that closely resembles the treatment drug. Days 5 - 13 Placebo for Prednisolone PO 1 mg/kg/day (max 50 mg/day) Days 14- 20 Placebo for Prednisolone PO 0.5 mg/kg/day (max 25 mg/day) Days 21 - 27 Placebo for Prednisolone PO 0.3 mg/kg/day (max 15 mg/day) Days 28 - 34 Placebo for Prednisolone PO 0.1 mg/kg/day (max 5 mg/day) Days 35 - 41 Placebo for Prednisolone PO 0.1 mg/kg every OTHER day (max 5 mg every other day) Day 42 Discontinue

Supportive care

Subjects randomized to the supportive care alone arm will receive normal saline in place of all study treatments (skin test, premedication and IV infusions) on Days 1-4 given at the same volume and duration as the eATG infusions.

Also known as: 0.9% Sodium chloride
Supportive care

Subjects in the eATG arm will receive pre-treatment medication diphenhydramine IV 1 mg/kg prior to start of eATG infusion.

Also known as: Benadryl
Equine anti-thymocyte globulin

Subjects in the eATG arm will receive pre-treatment medication methylprednisolone IV 1 mg/kg prior to start of eATG infusion.

Also known as: Solu-Medrol
Equine anti-thymocyte globulin

Eligibility Criteria

Age1 Year - 18 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64)

You may qualify if:

  • Patient with liver injury of ≤ 6 weeks duration resulting in an international normalization ratio (INR) of ≥ 1.5 or \< 2.0 (not corrected by vitamin K) with evidence of hepatic encephalopathy (HE), INR of ≥ 1.5 or \< 2.0 for at least 7 days duration without evidence of HE or INR ≥ 2.0 without evidence of HE.
  • Age is greater than or equal to 1 year and less than 18 years of age.
  • Patient or their legally authorized representative(s) (LAR) must consent (and assent, if applicable) to be in the study and must have signed and dated an approved informed consent form which conforms to federal and institutional guidelines.
  • Females of reproductive potential should not plan on conceiving children during the study and must agree to use a medically accepted form of contraception.

You may not qualify if:

  • Evidence of active infection with Hepatitis A, B, C, E or evidence of acute herpes simplex virus (HSV) or adenovirus infection
  • Travel within the past 3 months to an area highly endemic for Hepatitis E
  • Diagnosis of hemophagocytic lymphohistiocytosis (HLH) Note: Patients with a history of consanguinity and/or central nervous system (CNS) dysfunction that is exaggerated compared to the degree of liver dysfunction (as judged by the site investigator) will not be enrolled until results of rapid genetic testing are available. Turn-around time for genetic testing results is estimated to be 72-96 hours.
  • Aplastic anemia as defined by standardized criteria \[1\] diagnosed prior to enrollment
  • Diagnosis of autoimmune Hepatitis (AIH)
  • Diagnosis of acute Wilson disease
  • Diagnosis of acute drug or toxin-induced liver injury
  • History of recreational drug use within the past 4 weeks
  • Therapy with an immunosuppressive agent, including chemotherapy, biological therapies or an experimental drug or device within the past 6 weeks
  • Liver injury due to ischemia
  • Liver dysfunction diagnosed more than 6 weeks prior to screening
  • History of allergy to horse dander
  • Sepsis
  • Imminent risk of death as judged by the clinical site investigator, including but not limited to; signs of cerebral herniation at the time of enrollment and presence of intractable arterial hypotension
  • Solid organ or stem cell transplant recipient
  • +8 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (24)

Children's Hospital Los Angeles

Los Angeles, California, 90027, United States

RECRUITING

Lucile Packard Children's Hospital

Palo Alto, California, 94304, United States

RECRUITING

Rady Children's Hospital

San Diego, California, 92123, United States

RECRUITING

University of California San Francisco Benioff Children's Hospital

San Francisco, California, 94158, United States

WITHDRAWN

Children's Hospital Colorado

Aurora, Colorado, 80045, United States

RECRUITING

Yale New Haven Children's Hospital

New Haven, Connecticut, 06510, United States

WITHDRAWN

Children's Healthcare of Atlanta - Arthur M. Blank Hospital

Atlanta, Georgia, 30322, United States

WITHDRAWN

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, 60611, United States

RECRUITING

Riley Hospital for Children

Indianapolis, Indiana, 46202, United States

RECRUITING

Children's Hospital Boston

Boston, Massachusetts, 02115, United States

RECRUITING

The Children's Mercy Hospital

Kansas City, Missouri, 64108, United States

RECRUITING

St. Louis Children's Hospital

St Louis, Missouri, 63110, United States

RECRUITING

The Mount Sinai Medical Center

New York, New York, 10029, United States

WITHDRAWN

NYP Morgan Stanley Children's Hospital

New York, New York, 10032, United States

RECRUITING

Duke University Medical Center - Duke Children's

Durham, North Carolina, 27710, United States

WITHDRAWN

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, 45229, United States

RECRUITING

Cleveland Clinic Children's

Cleveland, Ohio, 44195, United States

RECRUITING

The Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

RECRUITING

Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, 15224, United States

RECRUITING

Children's Hospital Vanderbilt

Nashville, Tennessee, 37232, United States

RECRUITING

UT Southwestern Medical Center Children's Health

Dallas, Texas, 75235, United States

RECRUITING

Texas Children's Hospital

Houston, Texas, 77030, United States

RECRUITING

Primary Children's Medical Center

Salt Lake City, Utah, 84112, United States

WITHDRAWN

Seattle Children's Hospital

Seattle, Washington, 98105, United States

RECRUITING

MeSH Terms

Conditions

Liver Failure, AcuteHepatic EncephalopathyHepatic InsufficiencyLiver DiseasesLiver Failure

Interventions

MethylprednisoloneMethylprednisolone HemisuccinateAntilymphocyte SerumPrednisoloneSodium ChlorideDiphenhydramine

Condition Hierarchy (Ancestors)

Digestive System DiseasesBrain Diseases, MetabolicBrain DiseasesCentral Nervous System DiseasesNervous System DiseasesMetabolic DiseasesNutritional and Metabolic Diseases

Intervention Hierarchy (Ancestors)

PregnadienetriolsPregnadienesPregnanesSteroidsFused-Ring CompoundsPolycyclic CompoundsImmune SeraAntibodiesImmunoglobulinsImmunoproteinsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsSerum GlobulinsGlobulinsBiological ProductsComplex MixturesChloridesHydrochloric AcidChlorine CompoundsInorganic ChemicalsSodium CompoundsEthylaminesAminesOrganic ChemicalsBenzhydryl CompoundsBenzene DerivativesHydrocarbons, AromaticHydrocarbons, CyclicHydrocarbons

Study Officials

  • Estella M Alonso, MD

    Ann & Robert H Lurie Children's Hospital of Chicago

    PRINCIPAL INVESTIGATOR
  • Valerie L Durkalski-Mauldin, PhD

    Medical University of South Carolina

    PRINCIPAL INVESTIGATOR
  • Ed Doo, MD

    National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK)

    STUDY DIRECTOR
  • Averell Sherker, MD

    National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK)

    STUDY DIRECTOR

Central Study Contacts

Caitlin Schaffner, MPH

CONTACT

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
NIH
Responsible Party
SPONSOR

Study Record Dates

First Submitted

April 23, 2021

First Posted

April 27, 2021

Study Start

February 9, 2022

Primary Completion (Estimated)

August 1, 2026

Study Completion (Estimated)

February 1, 2027

Last Updated

March 10, 2026

Record last verified: 2026-03

Data Sharing

IPD Sharing
Will share

Data will be available at the National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK) Central Repository. The public use dataset, along with the study protocol, the data dictionary, annotated case report forms and a brief set of instructions ("Readme" file) will be provided.

Shared Documents
STUDY PROTOCOL
Time Frame
Release of the public use dataset will follow the NIDDK guidelines that study data analyzed for publications must be shared with the broader scientific community at the time of publication. Also, the study data analyzed for publications will be submitted to the NIDDK-CR when the manuscript is accepted for publication or at the time of publication.
More information

Locations