NCT04580420

Brief Summary

The aim of this study is to evaluate DCR-PHXC in participants with PH1 and severe renal impairment, with or without dialysis.

Trial Health

88
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
28

participants targeted

Target at below P25 for phase_2

Timeline
69mo left

Started Apr 2021

Longer than P75 for phase_2

Geographic Reach
10 countries

18 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress47%
Apr 2021Jan 2032

First Submitted

Initial submission to the registry

September 24, 2020

Completed
14 days until next milestone

First Posted

Study publicly available on registry

October 8, 2020

Completed
6 months until next milestone

Study Start

First participant enrolled

April 15, 2021

Completed
10.7 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

December 30, 2031

Expected
1 month until next milestone

Study Completion

Last participant's last visit for all outcomes

January 30, 2032

Last Updated

December 24, 2025

Status Verified

December 1, 2025

Enrollment Period

10.7 years

First QC Date

September 24, 2020

Last Update Submit

December 23, 2025

Conditions

Keywords

PH1ESRD

Outcome Measures

Primary Outcomes (2)

  • Safety: Incidence of Events

    To assess the efficacy of DCR-PHXC in lowering Pox in participants with PH1 and severe renal impairment, with or without hemodialysis or peritoneal dialysis.

    180 days

  • Safety: Incidence of Events

    Characterize the safety of DCR-PHXC in participants with PH1 and severe renal impairment, with or without dialysis.

    180 days

Secondary Outcomes (8)

  • Change from Baseline in Plasma Oxalate Concentration

    180 Days

  • To characterize the PK of DCR PHXC in patients with PH by observing secondary parameters of the area under the curve.

    180 days

  • To characterize the PK of DCR PHXC in patients with PH by observing maximum observed concentration (Cmax).

    180 days

  • To characterize the PK of DCR PHXC in patients with PH by observing minimum concentration (Cmin).

    180 days

  • To characterize the PK of DCR PHXC in patients with PH by observing maximum concentration (Tmax).

    180 days

  • +3 more secondary outcomes

Other Outcomes (5)

  • Change from Baseline in the Short Form (36) Health Survey (SF-36®) in adults

    180 days

  • Change from Baseline in the EQ-5D-5L™ in adults

    180 days

  • Change from Baseline in the Pediatric Quality of Life Inventory (PedsQL™) in children

    180 days

  • +2 more other outcomes

Study Arms (1)

Open-Label DCR-PHXC

EXPERIMENTAL

Open-Label monthly subcutaneous injection of DCR-PHXC based on age and weight.

Drug: DCR-PHXC

Interventions

Monthly dosing throughout study period

Also known as: Nedosiran
Open-Label DCR-PHXC

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Four age groups of participants will be enrolled:
  • adults and adolescents (aged ≥ 12 years)
  • children 6 to 11 years of age
  • children 2 to 5 years of age
  • infants and newborns from birth to \< 2 years of age
  • Documented diagnosis of PH1, confirmed by genotyping
  • Estimated GFR at Screening \<30mL/min normalized to 1.73m\^2 BSA
  • Mean of 2 Plasma Oxalate \>20μmol/L during screening
  • For participants receiving hemodialysis or peritoneal dialysis total duration of hemodialysis or peritoneal dialysis must be less than 24 months and hemodialysis or peritoneal dialysis regimen must have been stable for at least 2 weeks prior to Screening.
  • Male or Female
  • Male participants:
  • A male participant with a female partner of childbearing potential must agree to use contraception during the treatment period and for at least 12 weeks after the last dose of study intervention and refrain from donating sperm during this period.
  • Female participants:
  • A female participant is eligible to participate if she is not pregnant, not breastfeeding, and at least one of the following conditions applies:
  • Not a woman of childbearing potential (WOCBP).
  • +6 more criteria

You may not qualify if:

  • Prior hepatic transplantation; or scheduled transplantation within 6 months of Day 1. Prior renal transplantation is allowed.
  • Documented evidence of clinical manifestations of severe systemic oxalosis (including preexisting retinal, heart, or skin calcifications, or history of severe bone pain, pathological fractures, or bone deformations)
  • Presence of any condition or comorbidities that would interfere with study compliance or data interpretation or potentially impact patient safety including, but not restricted to:
  • Severe intercurrent illness
  • Known causes of active liver disease/injury (e.g., alcoholic liver disease, nonalcoholic fatty liver disease/steatohepatitis)
  • Non-PH related conditions contributing to renal insufficiency
  • Physician concerns about intake of drugs of abuse or excessive alcohol intake, or history of excessive alcohol intake in the 2 years prior to enrollment (defined as ≥ 21 units of alcohol per week in men and ≥ 14 units of alcohol per week in women; where a "unit" of alcohol is equivalent to a 12-ounce beer, 4-ounce glass of wine, or 1ounce shot of hard liquor)
  • Use of an RNAi drug, other DCR-PHXC, within the last 6 months
  • History of one or more of the following reactions to an oligonucleotide-based therapy:
  • Severe thrombocytopenia (platelet count ≤ 100,000/µL)
  • Hepatotoxicity, defined as alanine transaminase (ALT) or aspartate transaminase (AST) \> 3 times the upper limit of normal (ULN) and total bilirubin \> 2 × ULN or international normalized ratio (INR) \>1.5
  • Severe flu-like symptoms leading to discontinuation of therapy
  • Localized skin reaction from the injection (graded severe) leading to discontinuation of therapy
  • Coagulopathy/clinically significant prolongation of clotting time
  • Participation in any clinical study in which they received an investigational medicinal product (IMP) other than DCR-PHXC within 4 months before Screening.
  • +4 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (18)

Clinical Trial Site

San Francisco, California, 94143, United States

ACTIVE NOT RECRUITING

Clinical Trial Site

Boston, Massachusetts, 02115, United States

ACTIVE NOT RECRUITING

Clinical Trial Site

Rochester, Minnesota, 55905, United States

RECRUITING

Clinical Trial Site

New York, New York, 10016, United States

ACTIVE NOT RECRUITING

Clinical Trial Site

Bron, 69677, France

WITHDRAWN

Clinical Trial Site

Paris, 75019, France

WITHDRAWN

Clinical Trial Site

Bonn, 53127, Germany

RECRUITING

Clinical Trial Site

Heidelberg, 69120, Germany

WITHDRAWN

Clinical Trial Site

Roma, 00165, Italy

WITHDRAWN

Clinical Trial Site

Beirut, 00001, Lebanon

RECRUITING

Clinical Trial Site

Casablanca, 2025, Morocco

WITHDRAWN

Clinical Trial Site

Oradea, 410469, Romania

WITHDRAWN

Clinical Trial Site

Oradea, 410562, Romania

WITHDRAWN

Clinical Trial Site

Barcelona, 08035, Spain

RECRUITING

Clinical Trial Site

Santa Cruz de Tenerife, 38320, Spain

WITHDRAWN

Clinical Trial Site

Dubai, +971, United Arab Emirates

RECRUITING

Clinical Trial Site

London, NWG 2Q3, United Kingdom

WITHDRAWN

Clinical Trial Site

London, WC1N3JH, United Kingdom

RECRUITING

Related Publications (1)

  • Cox JH, Boily MO, Caron A, Sheng T, Wu J, Ding J, Gaudreault S, Chong O, Surendradoss J, Gomez R, Lester J, Dumais V, Li X, Gumpena R, Hall MD, Waterson AG, Stott G, Flint AJ, Moore WJ, Lowther WT, Knight J, Percival MD, Tong V, Oballa R, Powell DA, King AJ. Characterization of CHK-336, A First-in-Class, Liver-Targeted, Small-Molecule Lactate Dehydrogenase Inhibitor for Hyperoxaluria Treatment. J Am Soc Nephrol. 2025 Apr 7;36(8):1535-1547. doi: 10.1681/ASN.0000000690.

MeSH Terms

Conditions

Primary hyperoxaluria type 1Kidney Failure, Chronic

Interventions

nedosiran

Condition Hierarchy (Ancestors)

Renal Insufficiency, ChronicRenal InsufficiencyKidney DiseasesUrologic DiseasesFemale Urogenital DiseasesFemale Urogenital Diseases and Pregnancy ComplicationsUrogenital DiseasesMale Urogenital DiseasesChronic DiseaseDisease AttributesPathologic ProcessesPathological Conditions, Signs and Symptoms

Study Officials

  • Clinical Transparency (dept. 2834)

    Novo Nordisk A/S

    STUDY DIRECTOR

Central Study Contacts

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SEQUENTIAL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

September 24, 2020

First Posted

October 8, 2020

Study Start

April 15, 2021

Primary Completion (Estimated)

December 30, 2031

Study Completion (Estimated)

January 30, 2032

Last Updated

December 24, 2025

Record last verified: 2025-12

Data Sharing

IPD Sharing
Will not share

Locations