NCT04138485

Brief Summary

This randomized, multicenter, double-blind (DB), placebo controlled, phase 2 study will evaluate the efficacy and safety of IgPro10. The DB Treatment Period will be followed by a 24-week Open-label (OL) Treatment Period. Eligible subjects will be randomized at Baseline in a 2:1 ratio of treatment IgPro10 or placebo in the DB Treatment Period. All subjects who enter OL Treatment Period will receive IgPro10.

Trial Health

42
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Timeline
Completed

Started Dec 2019

Shorter than P25 for phase_2

Geographic Reach
13 countries

77 active sites

Status
withdrawn

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

October 14, 2019

Completed
10 days until next milestone

First Posted

Study publicly available on registry

October 24, 2019

Completed
2 months until next milestone

Study Start

First participant enrolled

December 20, 2019

Completed
9 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

September 16, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

September 16, 2020

Completed
Last Updated

November 17, 2020

Status Verified

November 1, 2020

Enrollment Period

9 months

First QC Date

October 14, 2019

Last Update Submit

November 16, 2020

Conditions

Outcome Measures

Primary Outcomes (1)

  • Response on American College of Rheumatology Combined Response Index in Diffuse Systemic Sclerosis (ACR CRISS) score in IgPro10 vs Placebo

    Over 48 weeks

Secondary Outcomes (28)

  • Proportion of subjects meeting cardiopulmonary or renal failure criteria in ACR CRISS Step 1 events

    Over 48 weeks

  • Proportion of responders (ACR CRISS > 0.6)

    Over 48 weeks

  • Mean change from Baseline in Modified Rodnan Skin Score (mRSS)

    Baseline and over48 weeks

  • Mean change from Baseline in Health Assessment Questionnaire - Disability Index (HAQ-DI)

    Baseline and over 48 weeks

  • Mean change from Baseline in Forced Vital Capacity (FVC)% predicted

    Baseline and over 48 weeks

  • +23 more secondary outcomes

Study Arms (2)

IgPro10

EXPERIMENTAL

10% liquid formulation of human immunoglobulin for intravenous use

Biological: IgPro10

Placebo

PLACEBO COMPARATOR

0.5% human albumin solution stabilized with 250 mmol/L L-proline

Biological: Placebo

Interventions

IgPro10BIOLOGICAL

10% liquid formulation of human immunoglobulin for IVIG

Also known as: Human normal immunoglobulin
IgPro10
PlaceboBIOLOGICAL

0.5% human albumin solution stabilized with 250 mmol/L L-proline

Also known as: Albumin
Placebo

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • \. Age ≥18 years (male or female) at time of providing written informed consent
  • Documented diagnosis of SSc according to ACR / EULAR criteria 2013
  • mRSS ≥ 15 and ≤ 45
  • Disease duration ≤ 5 years defined as the time from the first non-Raynaud's phenomenon manifestation
  • Subjects within first 18 months of disease duration from first non-Raynaud's phenomenon manifestation.

You may not qualify if:

  • Primary rheumatic autoimmune disease other than dcSSc, including but not limited to rheumatoid arthritis, systemic lupus erythematosus, mixed connective tissue disorder, polymyositis, and dermatomyositis, as determined by the investigator Note: Subjects with fibromyalgia, secondary Sjogren's syndrome, and scleroderma-associated myopathy or myositis at Screening are not excluded
  • Positive anti-centromere autoantibodies at Screening
  • Evidence of severe chronic kidney disease with estimated glomerular filtration rate \< 45 mL/min/1.73 m2 (as calculated by the Chronic Kidney Disease Epidemiology Collaboration equation) or receiving dialysis. Additionally, subjects with current confirmed diagnosis of diabetes mellitus and requiring medication, with eGFR \< 90 mL/min/1.73m2 will be excluded from the study.
  • Documented thrombophilic abnormalities including blood hyperviscosity, protein S or protein C deficiency, anti-thrombin-3 deficiency, plasminogen deficiency, antiphospholipid syndrome, Factor V Leiden mutation, dysfibrinogenemia, or prothrombin G20210A mutation
  • Greater than 3 specified current risk factors for TEEs (documented and currents conditions): atrial fibrillation, coronary disease, diabetes mellitus, dyslipidemia, hypertension, obesity (Body Mass Index ≥ 30 kg/m2), recent significant trauma, and immobility (wheelchair-bound or bedridden)
  • Ongoing active serious infection at Screening (including, but not limited to, pneumonia, bacteremia/septicemia, osteomyelitis/septic arthritis, bacterial meningitis, or visceral abscess)
  • Malignancy in the past 2 years, except for non-melanoma skin cancer, cervical carcinoma in situ, or other in situ cancer if it has been excised and treated within in the past year
  • Known hypoalbuminemia, protein-losing enteropathies, and any proteinuria (defined by total urine protein concentration \> 0.2 g/L)
  • Known IgA deficiency or serum IgA level \< 5% lower limit of normal

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (77)

Mayo Clinic Arizona - Scottsdale

Scottsdale, Arizona, 85259, United States

Location

Pacific Arthritis Care Center

Los Angeles, California, 90045, United States

Location

University of California

Los Angeles, California, 90095, United States

Location

Stanford University Medical Center

Palo Alto, California, 94304, United States

Location

University of Colorado

Aurora, Colorado, 80045, United States

Location

Lombardi Cancer Center-Georgetown University

Washington D.C., District of Columbia, 20007, United States

Location

Alliance for Multispecialty Research

Wichita, Kansas, 67207, United States

Location

Heartland Research Associates, LLC

Wichita, Kansas, 67207, United States

Location

Louisiana State University Health Sciences Center

Shreveport, Louisiana, 71103, United States

Location

John Hopkins Bayview Medical Center

Baltimore, Maryland, 21287, United States

Location

Boston University Amyloidosis Center

Boston, Massachusetts, 02118, United States

Location

University of Michigan Health System

Ann Arbor, Michigan, 48108, United States

Location

Rutgers Clinical Research Center

New Brunswick, New Jersey, 08901, United States

Location

Northwell Health

Great Neck, New York, 11021, United States

Location

Hospital For Special Surgery

New York, New York, 10021, United States

Location

Cleveland Clinic - Taussig Cancer Center

Cleveland, Ohio, 44195, United States

Location

Altoona Center For Research

Duncansville, Pennsylvania, 16635, United States

Location

University of Pennsylvania - Perelman Center

Philadelphia, Pennsylvania, 19104, United States

Location

Medical University of South Carolina

Charleston, South Carolina, 29425, United States

Location

The University Of Texas Medical School At Houston (Utms)

Houston, Texas, 77030, United States

Location

APRILLUS Asistencia e Investigacion Clinica

Buenos Aires, C1194AAO, Argentina

Location

Hospital Militar Central

Buenos Aires, C1426AAL, Argentina

Location

Hospital Italiano de Buenos Aires

Buenos Aires, S2000SDV, Argentina

Location

Sanatorio Parque S.A y Consultorios Externos Asociados

Rosario, C1181ACH, Argentina

Location

John Hunter Hospital / Autoimmune Resource and Research Centre

New Lambton Heights, New South Wales, 2305, Australia

Location

PARC Clinical Research

Adelaide, South Australia, 5005, Australia

Location

UZ Gent

Ghent, 9000, Belgium

Location

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, 3000, Belgium

Location

Mount Sinai Hospital, The Rebecca Macdonald Centre For Arthritis

Toronto, M5T 3L9, Canada

Location

CHU de Caen

Caen, 14000, France

Location

CHRU de Lille Hopital Huriez

Lille, 59037, France

Location

Internal Medicine, Nantes University Hospital

Nantes, 44000, France

Location

Assistance Publique - Hopitaux de Paris (AP-HP)

Paris, 75014, France

Location

CHU de Rennes-Hopital Sud

Rennes, 35203, France

Location

Centre Hospitalier Universitaire de Rouen-Hopital

Rouen, 76000, France

Location

CHU Hautepierre

Strasbourg, 67098, France

Location

Kerckhoff Klinik GmbH, Abteilung für Rheumatologie und Klinische Immunologie Rheumatologie

Bad Nauheim, 61231, Germany

Location

Charite - Universitaetsmedizin Berlin - Campus Charite Mitte

Berlin, 10117, Germany

Location

Universitaetsmedizin Berlin - Campus Charite Mitte (CCM)

Berlin, 10117, Germany

Location

University Hospital of Cologne

Cologne, 50937, Germany

Location

Universitaetsklinikum Freiburg- Klinik fuer Rheumatologie und Klinische Immunologie

Freiburg im Breisgau, 79106, Germany

Location

Universitaetsmedizin der Johannes Gutenberg

Mainz, 55131, Germany

Location

University Hospital Of Tuebingen

Tübingen, 72076, Germany

Location

Universitaetsklinikum Ulm

Ulm, 89081, Germany

Location

Hospital St. Josef

Wuppertal, 42105, Germany

Location

Universita degli Study di Ancona

Ancona, 60121, Italy

Location

Universita Degli Studi Di Bari Aldo Moro

Bari, 70121, Italy

Location

Universita degli Studi Di Brescia

Brescia, 25123, Italy

Location

Universita degli Studi Firenze

Florence, 50139, Italy

Location

UOC Immunoreumatologia

L’Aquila, 67100, Italy

Location

Azienda Ospedaliera Gaetano Pini

Milan, 20122, Italy

Location

Modena University

Modena, 41121, Italy

Location

Universita degli Studi di Napoli Federico II

Napoli, 80138, Italy

Location

IRCCS Policlinico San Matteo

Pavia, 27100, Italy

Location

Dip.to Med. Sperimentale -Polic.Umberto I -Univ. La Sapienza

Rome, 00161, Italy

Location

Centro Integral en Reumatologia, SA de CV

Guadalajara, 44160, Mexico

Location

Centro De Estudios De Investigation Basica Y Clinica S.C

Jalisco, 44690, Mexico

Location

Cliditer, S.A. DE C.V.

Mexico City, 06700, Mexico

Location

Centro de Investigacion y Tratamiento Reumatologico S.C.

Mexico City, 11850, Mexico

Location

Instituto Nacional De Ciencias Medicas Y Nutricion

México, 14080, Mexico

Location

Centro de Alta Especialidad en Reumatologia

San Luis Potosí City, 78213, Mexico

Location

Uniwersytecki Szpital Kliniczny W Bialymstoku

Bialystok, 15-369, Poland

Location

University Clinical Centre, Medical University of Gdansk

Gdansk, 80-211, Poland

Location

Samodzielny Publiczny Szpital Kliniczny

Katowice, 40-635, Poland

Location

Klinika Dermatologii Szpital im. Dzieciątka Jezus

Warsaw, 00-001, Poland

Location

Klinika i Poliklinika Układowych Chorób Tkanki Łącznej Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji

Warsaw, 02-637, Poland

Location

Complejo Hospitalario Universitario A Coruna

A Coruña, 15006, Spain

Location

Hospital Universitari Materno Infantil Vall Dhebron

Barcelona, 08035, Spain

Location

Hospital de la Santa Creu i Sant Pau

Barcelona, 08041, Spain

Location

Hospital General Universitario Gregorio Maranon

Madrid, 28009, Spain

Location

Hospital Univ 12 de Octubre

Madrid, 28041, Spain

Location

Hospital Infanta Luisa Quirónsalud

Seville, 41010, Spain

Location

Hospital Universitari Dr.Peset

Valencia, 46017, Spain

Location

Cantonal Hospital St. Gallen - Klinik fuer Rheumatologie

Sankt Gallen, 9007, Switzerland

Location

Countess of Chester Hospital

Chester, CH2 1UL, United Kingdom

Location

Chapel Allerton Hospital

Leeds, LS7 4SA, United Kingdom

Location

Royal Free Hospital-Royal Free London NHS Foundation Trust

London, NW3 2QG, United Kingdom

Location

MeSH Terms

Conditions

Scleroderma, Diffuse

Interventions

gamma-GlobulinsAlbumins

Condition Hierarchy (Ancestors)

Scleroderma, SystemicConnective Tissue DiseasesSkin and Connective Tissue DiseasesSkin Diseases

Intervention Hierarchy (Ancestors)

ImmunoglobulinsImmunoproteinsBlood ProteinsProteinsAmino Acids, Peptides, and ProteinsSerum GlobulinsGlobulins

Study Officials

  • Study Director

    CSL Behring

    STUDY DIRECTOR
0

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

October 14, 2019

First Posted

October 24, 2019

Study Start

December 20, 2019

Primary Completion

September 16, 2020

Study Completion

September 16, 2020

Last Updated

November 17, 2020

Record last verified: 2020-11

Data Sharing

IPD Sharing
Will share

CSL will consider requests to share Individual Patient Data (IPD) from systemic review groups or bona-fide researchers. For information on the process and requirements for submitting a voluntary data sharing request for IPD, please contact CSL at clinicaltrials@cslbehring.com. Applicable country specific privacy and other laws and regulations will be considered and may prevent sharing of IPD. If the request is approved and the researcher has executed an appropriate data sharing agreement, IPD that has been appropriately anonymized will be available.

Shared Documents
STUDY PROTOCOL, SAP
Time Frame
IPD requests may be submitted to CSL no earlier than 12 months after publication of the results of this study via an article made available on a public website.
Access Criteria
Requests may only be made by systematic review groups or bona-fide researchers whose proposed use of the IPD is non-commercial in nature and has been approved by an internal review committee. An IPD request will not be considered by CSL unless the proposed research question seeks to answer a significant and unknown medical science or patient care question as determined by CSL's internal review committee. The requesting party must execute an appropriate data sharing agreement before IPD will be made available.

Locations