NCT03505021

Brief Summary

This study will evaluate whether prolonged oral levosimendan can preserve respiratory function more effectively than placebo, resulting in better patient functionality as measured by the ALSFRS-R scale. In this randomized, double-blind, placebo-controlled, parallel-group, multicenter study, subjects are allocated in a 2:1 ratio to receive either levosimendan (1 -2 mg daily) or placebo for 48 weeks. The primary endpoint is slow vital capacity (SVC) at 12 weeks, with the impact on patient function assessed through 48 weeks, adjusted for patient outcome, using ALSFRS-R (combined assessment of function and survival, CAFS). Other important efficacy measures include time to respiratory events, clinical global impression (CGI), assessment of dyspnea using the Borg scale and sleep scales (Pittsburgh sleep quality index and Epworth sleepiness scale). Patient safety is monitored using conventional methods including adverse events, safety laboratory tests, vital signs and 12-lead EKG. Following screening and baseline visits, patients attend the clinic at 2, 4, 8, 12, 24, 36 and 48 weeks, with telephone assessments conducted at weeks 18, 30 and 42. An end of study visit is performed 14-25 days after the last study treatment administration. The study will be monitored by an independent data and safety monitoring board. A long-term extension study will be available for patients completing the study.

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Strong global presence with extensive site network
Enrollment
496

participants targeted

Target at P50-P75 for phase_3

Timeline
Completed

Started Jun 2018

Geographic Reach
13 countries

101 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

April 16, 2018

Completed
4 days until next milestone

First Posted

Study publicly available on registry

April 20, 2018

Completed
2 months until next milestone

Study Start

First participant enrolled

June 21, 2018

Completed
2.1 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 23, 2020

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

July 23, 2020

Completed
1.1 years until next milestone

Results Posted

Study results publicly available

August 31, 2021

Completed
Last Updated

May 11, 2022

Status Verified

April 1, 2022

Enrollment Period

2.1 years

First QC Date

April 16, 2018

Results QC Date

July 1, 2021

Last Update Submit

April 22, 2022

Conditions

Outcome Measures

Primary Outcomes (1)

  • Supine Slow Vital Capacity (SVC)

    Change from baseline to 12 weeks, expressed as % of predicted normal.

    The change from baseline at 12 weeks

Secondary Outcomes (5)

  • Combined Assessment of Function and Survival Through 48 Weeks

    Mean rank at 48 weeks

  • Time to Respiratory Event Through 48 Weeks

    Time to event through 48 weeks

  • Change From the Baseline in Clinical Global Impression CGI at 48 Weeks

    The change from baseline at 48 weeks

  • Change From Baseline in Respiratory Function of ALSFRS-R at 48 Weeks

    Slope of decline at 48 weeks

  • Supine Borg Category Ratio 10 Scale at 12 Weeks

    Change from baseline at 12 weeks

Study Arms (2)

Levosimendan

EXPERIMENTAL

Levosimendan 1 mg capsules for oral administration, once to twice a day. The total duration of treatment 48 weeks

Drug: Levosimendan

Placebo for levosimendan

PLACEBO COMPARATOR

Placebo capsule for oral administration, once to twice a day. The total duration of treatment 48 weeks.

Drug: Placebo for levosimendan

Interventions

Levosimendan 1 mg capsule for oral administration

Also known as: ODM-109
Levosimendan

Placebo capsule for oral administration

Also known as: Placebo for ODM-109
Placebo for levosimendan

Eligibility Criteria

Age18 Years - 120 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Written or verbal informed consent (IC) for participation in the study
  • Male or female subjects with diagnosis of laboratory supported probable, probable or definite ALS according to El Escorial revised criteria. Full electromyogram (EMG) report available consistent with ALS (but not necessarily fulfilling the electrodiagnostic criteria for ALS) from an experienced neurophysiologist
  • Able to swallow study treatment capsules, and in the opinion of the investigator, is expected to continue to do so during the study
  • Sitting SVC between 60-90% of the predicted value for age, height and sex at screening visit
  • Disease duration from symptom onset (defined by first muscle weakness or dysarthria) 12-48 months at the time of visit 1 (baseline)
  • Able to perform supine SVC in an adequate and reliable way at screening and baseline visits as judged by the investigator
  • Subjects with or without riluzole and/or edaravone. If using riluzole (any daily dose up to 100 mg), the dose must have been stable for at least 4 weeks before the screening visit and should not be changed during the study. If using edaravone, the treatment should have been started at least 4 weeks before the screening visit (at least one 28-day treatment cycle as indicated) and should not be changed during the study. If not on riluzole and/or edaravone, the respective treatments should not be started during the study

You may not qualify if:

  • Subject in whom other causes of neuromuscular weakness have not been excluded
  • Subject with a diagnosis of another neurodegenerative disease (e.g. Parkinson's or Alzheimer's disease)
  • Assisted ventilation of any type within 3 months before the screening visit or at screening
  • Any use of a diaphragm pacing system (DPS) within 3 months before the screening visit
  • Any form of stem cell or gene therapy for the treatment of ALS
  • Known hypersensitivity to levosimendan
  • Administration of levosimendan within 3 months before the screening visit or previous participation in the present phase III study or earlier study with oral levosimendan in ALS patients (LEVALS)
  • Any use of tirasemtiv or reldesemtiv within 1 month before the screening visit.
  • Participation in a clinical trial with any experimental treatment within 30 days or within 5 half-lives of that treatment (whichever is longer) before the screening visit
  • Any botulinum toxin use within 3 months before the screening visit
  • Recorded diagnosis or evidence of major psychiatric diagnosis, significant cognitive impairment or clinically evident dementia that may interfere with the patient's ability to comply with study procedures
  • Pulmonary illness (e.g. asthma or COPD) requiring regular treatment
  • Haemodynamically significant uncorrected valve disease or hypertrophic cardiomyopathy or restrictive cardiomyopathy
  • Any cardiovascular event (e.g. myocardial infarction, HF, arrhythmia or stroke) requiring hospitalisation within 3 months before the screening visit
  • History of Torsades de Pointes (TdP) or diagnosed long QT-syndrome
  • +13 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (104)

Phoenix Neurological Associates

Phoenix, Arizona, 85006, United States

Location

Neuromuscular Research Center and Neuromuscular Clinic of Arizona

Phoenix, Arizona, 85028, United States

Location

University of California San Diego

La Jolla, California, 92037-0886, United States

Location

Cedars-Sinai Medical Center

Los Angeles, California, 90048, United States

Location

University of California Irvine

Orange, California, 92868, United States

Location

California Pacific Medical Center

San Francisco, California, 94115, United States

Location

Colorado Springs Neurological Associates

Colorado Springs, Colorado, 80907, United States

Location

Hospital for Special Care

New Britain, Connecticut, 06053, United States

Location

Georgetown University

Washington D.C., District of Columbia, 20007, United States

Location

The George Washington Medical Faculty Associates - Foggy Bottom North Pavilion

Washington D.C., District of Columbia, 20037, United States

Location

Providence Holy Cross Medical Center

Fort Lauderdale, Florida, 33308, United States

Location

University of Florida

Gainesville, Florida, 32611, United States

Location

University of Florida Health - Jacksonville

Jacksonville, Florida, 32209, United States

Location

Mayo Clinic - Jacksonville

Jacksonville, Florida, 32224, United States

Location

University of South Florida

Tampa, Florida, 33612, United States

Location

Emory University School of Medicine

Atlanta, Georgia, 30322, United States

Location

Augusta University

Augusta, Georgia, 30912, United States

Location

Northwestern University Feinberg School of Medicine

Chicago, Illinois, 60611, United States

Location

University of Chicago

Chicago, Illinois, 60637, United States

Location

University of Kentucky Chandler Medical Center

Lexington, Kentucky, 40536, United States

Location

Kentucky Neuroscience Research

Louisville, Kentucky, 40202, United States

Location

The Johns Hopkins Hospital

Baltimore, Maryland, 21205, United States

Location

Massachusetts General Hospital

Boston, Massachusetts, 02114, United States

Location

University of Michigan

Ann Arbor, Michigan, 49007, United States

Location

Mayo Clinic - Rochester

Rochester, Minnesota, 55905, United States

Location

HealthPartners Specialty Center

Saint Paul, Minnesota, 55130-5302, United States

Location

Washington University School of Medicine

St Louis, Missouri, 63110, United States

Location

Neurology Associates

Lincoln, Nebraska, 68506, United States

Location

Mount Sinai Beth Israel

New York, New York, 10003, United States

Location

Hospital for Special Surgery

New York, New York, 10021, United States

Location

Columbia Presbyterian Hospital

New York, New York, 10032, United States

Location

Neurosciences Institute - Neurology Charlotte

Charlotte, North Carolina, 28207, United States

Location

Duke University Medical Center

Durham, North Carolina, 27705, United States

Location

Wake Forest University Baptist Medical Center

Winston-Salem, North Carolina, 27157-1023, United States

Location

The Ohio State University

Columbus, Ohio, 43210, United States

Location

Oregon Health and Science University

Portland, Oregon, 97201-3098, United States

Location

Providence Brain and Spine Institute

Portland, Oregon, 97213, United States

Location

Hospital of the University of Pennsylvania

Philadelphia, Pennsylvania, 19107, United States

Location

Temple University School of Medicine

Philadelphia, Pennsylvania, 19140, United States

Location

Allegheny General Hospital

Pittsburgh, Pennsylvania, 15212, United States

Location

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, 15213, United States

Location

Texas Neurology

Dallas, Texas, 75214, United States

Location

Nerve and Muscle Center of Texas

Houston, Texas, 77030, United States

Location

University of Utah - Imaging & Neurosciences Center

Salt Lake City, Utah, 84108, United States

Location

University of Vermont Medical Center

Burlington, Vermont, 05401, United States

Location

Swedish Neuroscience Institute

Seattle, Washington, 98122, United States

Location

University of Washington Medical Center

Seattle, Washington, 98195, United States

Location

Froedtert Hospital

Milwaukee, Wisconsin, 53226, United States

Location

Brain and Mind Centre

Camperdown, New South Wales, 2050, Australia

Location

Royal Brisbane and Women's Hospital

Brisbane, Queensland, 4029, Australia

Location

Flinders Medical Centre

Bedford Park, South Australia, 5042, Australia

Location

Calvary Health Care Bethlehem

Caulfield South, Victoria, 3162, Australia

Location

Perron Institute for Neurological and Translational Science

Murdoch, Western Australia, 6150, Australia

Location

Universität Innsbruck

Innsbruck, Tyrol, 6020, Austria

Location

Salzkammergut-Klinikum Vöcklabruck

Vöcklabruck, Upper Austria, 4840, Austria

Location

Medizinische Universität Wien

Vienna, 1090, Austria

Location

Universitaire Ziekenhuis Leuven

Leuven, Flemish Brabant, 3000, Belgium

Location

Centre Hospitalier Régional de la Citadelle

Liège, Liege, 4000, Belgium

Location

Algemeen Ziekenhuis St. Lucas Gent

Ghent, Oost-Vlaanderen, 9000, Belgium

Location

Alberta Health Services - Neuromuscular Clinic

Calgary, Alberta, T3M 1M4, Canada

Location

University of Alberta

Edmonton, Alberta, T6G 2G3, Canada

Location

Stan Cassidy Centre for Rehabilitation

Fredericton, New Brunswick, E3B 0C7, Canada

Location

Moncton Hospital, Southeast Regional Health Authority

Moncton, New Brunswick, E1C 2Z3, Canada

Location

McMaster University Medical Centre

Hamilton, Ontario, L8N 3Z5, Canada

Location

Sunnybrook Health Sciences Centre

Toronto, Ontario, M4N 3M5, Canada

Location

Centre De Recherche Du Centre Hospitalier de l'Universite de Montreal - Hopital Notre-Dame

Montreal, Quebec, H2L 4M1, Canada

Location

Montreal Neurological Institute and Hospital

Montreal, Quebec, H3A 2B4, Canada

Location

Centre Hospitalier Affilie Universitaire de Quebec

Québec, Quebec, G1J 1Z4, Canada

Location

Neurologian Poliklinikka - Meilahden Tornisairaala 3

Helsinki, 00029, Finland

Location

Etelä-Karjalan keskussairaala

Lappeenranta, 53130, Finland

Location

Turku University Hospital

Turku, 20521, Finland

Location

Centre Hospitalier Universitaire de Limoges

Limoges, 87042, France

Location

Hôpital Gui de Chauliac

Montpellier, 34295, France

Location

Hôpital Pasteur

Nice, 06202, France

Location

Centre Hospitalier Régional et Universitaire de Tours Hôpital Bretonneau

Tours, 37044, France

Location

Universitätsklinikum Ulm

Ulm, Baden-Wurttemberg, 89081, Germany

Location

Deutsche Klinik für Diagnostik

Wiesbaden, Hesse, 65191, Germany

Location

Medizinische Hochschule Hannover

Hanover, Lower Saxony, 30625, Germany

Location

Universitätsmedizin Rostock

Rostock, Mecklenburg-western-pommerania, 18147, Germany

Location

Alfried Krupp Krankenhaus Rüttenscheid

Essen, North Rhine-Westphalia, 45131, Germany

Location

Universitätsklinikum Münster

Münster, North Rhine-Westphalia, 48149, Germany

Location

Universitätsklinikum Carl Gustav Carus

Dresden, Saxony, 01307, Germany

Location

Universitätsklinikum Jena

Jena, Thuringia, 07747, Germany

Location

Charité Universitätsmedizin Berlin - Campus Virchow-Klinikum

Berlin, 13353, Germany

Location

Beaumont Hospital - Ireland

Dublin, 9, Ireland

Location

Azienda Ospedaliera Universitaria San Martino

Genova, 16132, Italy

Location

Azienda Ospedaliera Universitaria-Maggiore della Carità di Novara

Novara, 28100, Italy

Location

ICS Maugeri Spa SB

Pavia, 27100, Italy

Location

Azienda Ospedaliero-Universitaria Pisana Ospedale Santa Chiara

Pisa, 56126, Italy

Location

Policlinico Umberto I di Roma

Roma, 0016, Italy

Location

Azienda Ospedaliera - Universitaria Città della Salute e della Scienza di Torino

Torino, 10126, Italy

Location

Academisch Medisch Centrum

Amsterdam, North Holland, 1105 AZ, Netherlands

Location

Universitair Medisch Centrum Utrecht - Rudolf Magnus Instituut voor Neurowetenschappen

Utrecht, 3584 CG, Netherlands

Location

Hospital de Basurto

Bilbao, Vizcaya, 48013, Spain

Location

Hospital Universitari de Bellvitge

Barcelona, 08207, Spain

Location

Hospital Universitario Reina Sofia

Córdoba, 14011, Spain

Location

Hospital San Rafael - Madrid

Madrid, 28016, Spain

Location

Hospital Universitario y Politécnico de La Fe

Valencia, 46026, Spain

Location

Norrlands Universitetssjukhus

Umeå, Västerbotten County, 90737, Sweden

Location

Centralsjukhuset Karlstad

Karlstad, 651 85, Sweden

Location

Karolinska Universitetssjukhuset

Stockholm, 14186, Sweden

Location

Barts Health NHS Trust

London, England, E1 1BB, United Kingdom

Location

King's College Hospital NHS Foundation Trust

London, England, SE5 9RS, United Kingdom

Location

The Walton Centre NHS Foundation Trust

Liverpool, L9 7LJ, United Kingdom

Location

Related Publications (1)

  • Cudkowicz M, Genge A, Maragakis N, Petri S, van den Berg L, Aho VV, Sarapohja T, Kuoppamaki M, Garratt C, Al-Chalabi A; REFALS investigators. Safety and efficacy of oral levosimendan in people with amyotrophic lateral sclerosis (the REFALS study): a randomised, double-blind, placebo-controlled phase 3 trial. Lancet Neurol. 2021 Oct;20(10):821-831. doi: 10.1016/S1474-4422(21)00242-8.

MeSH Terms

Conditions

Amyotrophic Lateral Sclerosis

Interventions

Simendan

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesMotor Neuron DiseaseNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Intervention Hierarchy (Ancestors)

HydrazonesHydrazinesOrganic ChemicalsPyridazinesHeterocyclic Compounds, 1-RingHeterocyclic Compounds

Results Point of Contact

Title
Director, Clinical Operations
Organization
Orion Corporation

Study Officials

  • Merja Mäkitalo, CSD

    Orion Corporation, Orion Pharma

    STUDY DIRECTOR

Publication Agreements

PI is Sponsor Employee
No
Restrictive Agreement
No

Study Design

Study Type
interventional
Phase
phase 3
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

April 16, 2018

First Posted

April 20, 2018

Study Start

June 21, 2018

Primary Completion

July 23, 2020

Study Completion

July 23, 2020

Last Updated

May 11, 2022

Results First Posted

August 31, 2021

Record last verified: 2022-04

Locations