NCT03433807

Brief Summary

The primary objective of this Expanded Access Program is to provide idebenone as a treatment for eligible participants with Duchenne Muscular Dystrophy before it is commercially available in the United States (U.S.) for the indication of DMD.

Trial Health

55
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Geographic Reach
1 country

12 active sites

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

February 8, 2018

Completed
7 days until next milestone

First Posted

Study publicly available on registry

February 15, 2018

Completed
Last Updated

April 21, 2023

Status Verified

April 1, 2023

First QC Date

February 8, 2018

Last Update Submit

April 20, 2023

Conditions

Keywords

idebenone, DMD, Duchenne

Interventions

900 mg idebenone/day (2 tablets to be taken 3 times a day with meals)

Eligibility Criteria

Age8 Years+
Sexall
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Documented diagnosis of DMD (severe dystrophinopathy) and clinical features consistent of typical DMD at diagnosis (i.e., documented delayed motor skills and muscle weakness by age 5 years) and who in the opinion of the Treating physician would benefit from treatment with idebenone. DMD should be confirmed by mutation analysis in the dystrophin gene or by substantially reduced levels of dystrophin protein (i.e., absent or \<5% of normal) on Western blot or immunostaining.
  • Minimum 8 years old at Prescreening.
  • PEF or FVC ≤80% and \>25% of predicted value based on most recent assessment noted in the patient's medical record and subsequently confirmed at the Enrollment Visit.
  • Able to understand program requirements and swallow program medication.
  • Signed and dated Informed Consent Form (to be obtained at the Enrollment Visit from patient or parent/legal guardian (if applicable) prior to performing any program-specific procedures and dispensing idebenone to the patient).

You may not qualify if:

  • Eligible for and able to participate in an ongoing clinical trial of idebenone.
  • Is at high-risk of a fatal outcome from lung infection and/or advanced cardiomyopathy in the opinion of the Treating physician.
  • Known moderate or severe impairment of hepatic function or severe impairment of renal function.
  • Prior or ongoing medical condition or laboratory abnormality which in the Treating physician's opinion may put the patient at significant risk or may interfere significantly with the patient's participation in the program.
  • Abuse of drugs or alcohol, which in Treating physician's opinion would interfere with the compliance to treatment.
  • Known individual hypersensitivity to idebenone or to any of the ingredients/excipients of the program medication.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (12)

Phoenix Children's Hospital

Phoenix, Arizona, 85016, United States

Location

Yale New Haven Hospital

New Haven, Connecticut, 06510, United States

Location

Lurie Children's Hospital of Chicago

Chicago, Illinois, 60611, United States

Location

University of Iowa

Iowa City, Iowa, 52242, United States

Location

University of Kansas Medical Center

Kansas City, Kansas, 66160, United States

Location

Kennedy Krieger

Baltimore, Maryland, 21287, United States

Location

Columbia University Pediatric Neuromuscular Center

New York, New York, 10032, United States

Location

Carolina's Healthcare System

Charlotte, North Carolina, 28207, United States

Location

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, 45229, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

University of Virginia Children's Hospital

Charlottesville, Virginia, 22904, United States

Location

St. Luke's Rehabilitation Institute

Spokane, Washington, 99202, United States

Location

MeSH Terms

Conditions

Muscular Dystrophy, Duchenne

Interventions

idebenone

Condition Hierarchy (Ancestors)

Muscular DystrophiesMuscular Disorders, AtrophicMuscular DiseasesMusculoskeletal DiseasesNeuromuscular DiseasesNervous System DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and Abnormalities

Study Design

Study Type
expanded access
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

February 8, 2018

First Posted

February 15, 2018

Last Updated

April 21, 2023

Record last verified: 2023-04

Locations