NCT01378676

Brief Summary

The study will generate data on safety, tolerability and pharmacokinetics after multiple daily doses of CK-2017357 in patients with ALS. Patients will be randomized into one of four different treatment groups, receiving daily oral doses of either placebo, 125 mg, 250 mg, or 375 mg of CK-2017357 for 14 days.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
49

participants targeted

Target at P25-P50 for phase_2

Timeline
Completed

Started Jun 2011

Shorter than P25 for phase_2

Geographic Reach
1 country

9 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

June 1, 2011

Completed
19 days until next milestone

First Submitted

Initial submission to the registry

June 20, 2011

Completed
2 days until next milestone

First Posted

Study publicly available on registry

June 22, 2011

Completed
8 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

March 1, 2012

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

March 1, 2012

Completed
Last Updated

May 7, 2019

Status Verified

May 1, 2019

Enrollment Period

9 months

First QC Date

June 20, 2011

Last Update Submit

May 2, 2019

Conditions

Outcome Measures

Primary Outcomes (1)

  • Number of Participants with Adverse Events as a Measure of Safety and Tolerability

    Safety and tolerability of CK-2017357 after multiple oral doses to steady state in patients with ALS

    21 days

Secondary Outcomes (8)

  • Amyotrophic Lateral Sclerosis Functional Rating Scale-Revised (ALSFRS-R)

    21 days

  • Measurement of Grip Strength and Handgrip Fatigue

    21 days

  • Measurement of muscle strength

    21 days

  • Measurement of Slow Vital Capacity (SVC)

    21 days

  • Measurement of Sniff Nasal Inspiratory Pressure (SNIP)

    21 days

  • +3 more secondary outcomes

Study Arms (4)

Matching Placebo

PLACEBO COMPARATOR
Drug: Placebo (Part A)Drug: Riluzole 50 MG (Part B)Drug: Placebo (Part B)

Active Drug Low Dose (CK-2017357 125 mg)

EXPERIMENTAL
Drug: Placebo (Part A)Drug: CK-2017357 (Part A)Drug: Riluzole 50 MG (Part B)Drug: Placebo (Part B)Drug: CK-2017357 (Part B)

Active Drug Mid Dose (CK-2017357 250 mg)

EXPERIMENTAL
Drug: Placebo (Part A)Drug: CK-2017357 (Part A)Drug: Riluzole 50 MG (Part B)Drug: Placebo (Part B)Drug: CK-2017357 (Part B)

Active Drug High Dose (CK-2017357 375 mg)

EXPERIMENTAL
Drug: CK-2017357 (Part A)Drug: Riluzole 50 MG (Part B)Drug: CK-2017357 (Part B)

Interventions

Placebo tablets once daily for 14 days (Part A)

Active Drug Low Dose (CK-2017357 125 mg)Active Drug Mid Dose (CK-2017357 250 mg)Matching Placebo

One 125 mg CK-2017357 tablet once daily for 14 days (Part A)

Also known as: tirasemtiv
Active Drug Low Dose (CK-2017357 125 mg)

One 50 mg tablet once daily for 14 days (Part B)

Active Drug High Dose (CK-2017357 375 mg)Active Drug Low Dose (CK-2017357 125 mg)Active Drug Mid Dose (CK-2017357 250 mg)Matching Placebo

Placebo tablets once daily for 14 days (Part B)

Active Drug Low Dose (CK-2017357 125 mg)Active Drug Mid Dose (CK-2017357 250 mg)Matching Placebo

One 125 mg tablet once daily for 14 days (Part B)

Also known as: tirasemtiv
Active Drug Low Dose (CK-2017357 125 mg)

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Able to comprehend and willing to sign an Informed Consent Form (ICF)
  • Males or females 18 years of age or older
  • A diagnosis of familial or sporadic ALS (defined as meeting the possible, laboratory-supported probable, probable, or definite criteria for a diagnosis of ALS according to the World Federation of Neurology El Escorial criteria)
  • Maximum voluntary grip strength in at least one hand between 10 \& 40 pounds (females) and 10 \& 60 pounds (males)
  • Upright Slow Vital Capacity (SVC) \>50% of predicted for age, height, and sex
  • Able to swallow tablets with water
  • Willing and able to remain off riluzole for 4 weeks (Part A only)
  • Currently taking and tolerating a stable dose of 50 mg BID riluzole (Part B only)
  • Willing and able to reduce daily dose of riluzole to 50 mg for 4 weeks (Part B only)
  • Willing and able to refrain from caffeine-containing products during study participation
  • Willing and able to remain off warfarin and theophylline-containing medications during study participation
  • Has a caregiver who is capable of observing and reporting patient status, and also assisting in the proper use of nocturnal oximetry equipment
  • Able to perform pulmonary function tests

You may not qualify if:

  • Life expectancy \<3 months
  • Participation in any trial in which receipt of investigational study drug occurred within 30 days or 5 half-lives of the prior agent, whichever is greater, prior to dosing
  • Any prior treatment with CK-2017357
  • Use of non-invasive positive pressure ventilation (NIPPV) for any part of the day or night

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (9)

California Pacific Medical Center

San Francisco, California, 94115, United States

Location

Mayo Florida

Jacksonville, Florida, 32224, United States

Location

University of Kansas

Kansas City, Kansas, 06053, United States

Location

Johns Hopkins Hospital

Baltimore, Maryland, 21287, United States

Location

Columbia University Medical Center

New York, New York, 10032, United States

Location

SUNY Upstate Medical Center

Syracuse, New York, 13210, United States

Location

Carolinas Neuromuscular ALS-MND Center

Charlotte, North Carolina, 28207, United States

Location

Penn State Hershey Medical Center

Hershey, Pennsylvania, 17033, United States

Location

Drexel University College of Medicine

Philadelphia, Pennsylvania, 19107, United States

Location

Related Publications (1)

  • Shefner JM, Watson ML, Meng L, Wolff AA; Neals/Cytokinetics STUDY Team. A study to evaluate safety and tolerability of repeated doses of tirasemtiv in patients with amyotrophic lateral sclerosis. Amyotroph Lateral Scler Frontotemporal Degener. 2013 Dec;14(7-8):574-81. doi: 10.3109/21678421.2013.822517. Epub 2013 Aug 19.

MeSH Terms

Conditions

Amyotrophic Lateral Sclerosis

Interventions

CK-2017357Riluzole

Condition Hierarchy (Ancestors)

Spinal Cord DiseasesCentral Nervous System DiseasesNervous System DiseasesMotor Neuron DiseaseNeurodegenerative DiseasesTDP-43 ProteinopathiesNeuromuscular DiseasesProteostasis DeficienciesMetabolic DiseasesNutritional and Metabolic Diseases

Intervention Hierarchy (Ancestors)

ThiazolesSulfur CompoundsOrganic ChemicalsBenzothiazolesAzolesHeterocyclic Compounds, 1-RingHeterocyclic CompoundsHeterocyclic Compounds, 2-RingHeterocyclic Compounds, Fused-Ring

Study Officials

  • Jeremy Shefner, MD, PhD

    State University of New York - Upstate Medical University

    STUDY CHAIR

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

June 20, 2011

First Posted

June 22, 2011

Study Start

June 1, 2011

Primary Completion

March 1, 2012

Study Completion

March 1, 2012

Last Updated

May 7, 2019

Record last verified: 2019-05

Locations