NCT00903331

Brief Summary

The AC-055B201/MUSIC study is a Phase II study, comparing one dose of ACT-064922 (macitentan) 10 mg with placebo in patients with idiopathic pulmonary fibrosis (IPF). The main study objective is to demonstrate that macitentan positively affects the forced vital capacity (FVC) in comparison with placebo in patients with idiopathic pulmonary fibrosis (IPF). The secondary objectives are to evaluate the effect of macitentan on the time to disease worsening or death in patients with IPF, and to evaluate the benefit/risk profile of macitentan in the treatment of patients with IPF.

Trial Health

98
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
178

participants targeted

Target at P75+ for phase_2

Timeline
Completed

Started May 2009

Geographic Reach
12 countries

53 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

May 1, 2009

Completed
13 days until next milestone

First Submitted

Initial submission to the registry

May 14, 2009

Completed
4 days until next milestone

First Posted

Study publicly available on registry

May 18, 2009

Completed
2 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 1, 2011

Completed
2 months until next milestone

Study Completion

Last participant's last visit for all outcomes

August 1, 2011

Completed
2.6 years until next milestone

Results Posted

Study results publicly available

February 17, 2014

Completed
Last Updated

February 17, 2014

Status Verified

January 1, 2014

Enrollment Period

2.1 years

First QC Date

May 14, 2009

Results QC Date

October 29, 2013

Last Update Submit

January 2, 2014

Conditions

Keywords

idiopathic pulmonary fibrosisMUSIC

Outcome Measures

Primary Outcomes (1)

  • Forced Vital Capacity (FVC) at Baseline and End of Period 1

    FVC was measured at baseline and at the end of Period 1. The same equipment and tester were used during the course of the study. The equipment was calibrated and the calibration documented prior to each patient's measurement. The person responsible for conducting the pulmonary function tests was required to comply with the study guidelines and the American Thoracic Society/European Respiratory Society joint criteria on lung function testing.

    12 months

Secondary Outcomes (1)

  • Number of Patients at Risk of Event of Disease Worsening or Death up to the End of Study

    Up to end of study (Up to 24 months)

Study Arms (2)

ACT-064922

EXPERIMENTAL

ACT-064922 tablet (macitentan), 10 mg, once daily

Drug: ACT-064992 (macitentan)

Placebo

PLACEBO COMPARATOR

Matching placebo, once daily

Drug: Placebo

Interventions

ACT-064992 (macitentan) tablet, 10 mg, once daily

Also known as: macitentan
ACT-064922

matching placebo, once daily

Placebo

Eligibility Criteria

Age18 Years+
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64), Older Adult (65+)

You may qualify if:

  • Signed informed consent.
  • Male or female patients of at least 18 years of age (females of child-bearing potential must use a reliable method of contraception).
  • IPF diagnosis within 3 years prior to randomization, proven according to the American Thoracic Society/European Respiratory Society consensus conference criteria, with surgical lung biopsy.

You may not qualify if:

  • Interstitial lung disease due to conditions other than IPF.
  • Presence of extensive honeycombing on Baseline high-resolution computed tomography (HRCT) scan performed within 3 months prior to randomization.
  • Severe concomitant illness limiting life expectancy (\< 1 year).
  • Severe restrictive lung disease: forced vital capacity (FVC) \< 50% predicted, or FVC \< 1.2 liter.
  • Diffusing capacity of the lung for carbon monoxide (DLCO) \< 30% predicted.
  • Residual volume ≥ 120% predicted.
  • Obstructive lung disease: forced expiratory volume in 1 second (FEV1)/FVC) \< 0.70.
  • Documented sustained improvement of the patient's IPF condition up to 12 months prior to randomization with or without IPF-specific therapy.
  • Recent pulmonary or upper respiratory tract infection (up to 4 weeks prior to randomization).
  • Acute or chronic impairment (other than dyspnea) limiting the ability to comply with study requirements (e.g., pulmonary function tests).
  • Chronic heart failure with New York Heart Association class III/IV or known left ventricular ejection fraction \< 25%.
  • Moderate to severe hepatic impairment, i.e., Child-Pugh Class B or C.
  • Estimated creatinine clearance \< 30 mL/min.
  • Aspartate aminotransferase (AST) and/or alanine aminotransferase \> 1.5 x upper limit of normal.
  • Hemoglobin \< 75% of the lower limit of the normal range.
  • +14 more criteria

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (53)

University of Alabama at Birmingham

Birmingham, Alabama, 35294, United States

Location

Pulmonary Associates, P.A.

Phoenix, Arizona, 85006, United States

Location

Mayo Clinic - Arizona

Scottsdale, Arizona, 85259, United States

Location

U.C. Davis University of California

Sacramento, California, 95817, United States

Location

UCSD Pulmonary Critical Care

San Diego, California, 92103, United States

Location

University of California - San Francisco

San Francisco, California, 94143, United States

Location

Stanford University Medical Center - Chest Clinic

Stanford, California, 94305, United States

Location

National Jewish Medical & Research Center

Denver, Colorado, 80206, United States

Location

Yale University School of Medicine

New Haven, Connecticut, 06520, United States

Location

Wichita Clinic P.A

Wichita, Kansas, 67208, United States

Location

St. Luke's Medical Group

Chesterfield, Missouri, 63017, United States

Location

The Cleveland Clinic Foundation

Cleveland, Ohio, 44195, United States

Location

Temple University Hospital - Lung Center

Philadelphia, Pennsylvania, 19140, United States

Location

Baylor College of Medicine - Baylor Clinic

Houston, Texas, 77030, United States

Location

University of Wisconsin - Madison

Madison, Wisconsin, 53792, United States

Location

Prince Charles Hospital Lung Transplant

Chermside, Australia

Location

St. Vincent's Public Hospital

Darlinghurst, Australia

Location

The Alfred Hospital

Melbourne, Australia

Location

Royal Perth Hospital

Perth, Australia

Location

University of Alberta - Health Sciences Center

Edmonton, Alberta, T6G2B7, Canada

Location

Kelowna General Hospital

Kelowna, British Columbia, V1W3T1, Canada

Location

St. Paul's Hospital

Vancouver, British Columbia, V6Z1Y6, Canada

Location

St. Joseph's Healthcare

Hamilton, Ontario, L8N4A6, Canada

Location

Toronto General Hospital

Toronto, Ontario, M5G2N2, Canada

Location

Hospital Notre-Dame du CHUM

Montreal, Quebec, H2L4M1, Canada

Location

Hopital Avicenne

Bobigny, France

Location

Hôpital Cardiologique et Pneumologique Louis Pradel

Bron, France

Location

CHRU - Hopital Calmette Clinique des Maladies Respiratoires

Lille, France

Location

Helios Klinikum Emil von Behring

Berlin, Germany

Location

Universität zu Köln

Cologne, Germany

Location

Justus-Liebig-Universität Gießen

Giessen, Germany

Location

Fachklinik fur Lungenerkrankungen

Immenhausen, Germany

Location

Ludwig-Maximilian-Universität München

München, Germany

Location

Hadassah Ein Kerem Medical Center

Jerusalem, Israel

Location

Rabin Medical Center, Beilinson Hospital

Petach Tikvah, Israel

Location

Kaplan Medical Center

Rehovot, Israel

Location

Tel-Aviv Sourasky Medical Center

Tel Aviv, Israel

Location

The Chaim Sheba Medical Center

Tel Litwinsky, Israel

Location

Ospedale San Giuseppe Milanocuore

Milan, Italy

Location

Università degli Studi di Torino Clinica di Malattie dell'Apparato Respiratorio

Orbassano, Italy

Location

A.O.U Policlinico Tor Vergata

Roma, Italy

Location

Ospedale di Cattinara

Trieste, Italy

Location

Bolnišnica Golnik

Golnik, Slovenia

Location

Centre for Chest Diseases, Milpark Hospital

Johannesburg, South Africa

Location

Pretoria East Hospital

Pretoria, South Africa

Location

Hospital Clinic I Provincial de Barcelona

Barcelona, Spain

Location

Hospital General Vall d'Hebron

Barcelona, Spain

Location

Fundación Hospital Alcorcón

Madrid, Spain

Location

Hospital Clinico San Carlos

Madrid, Spain

Location

Hospital Universitario Ramón y Cajal

Madrid, Spain

Location

Karolinska Universitetssjukhuset Lung Allergi kliniken

Stockholm, Sweden

Location

Ankara University School of Medicine

Ankara, Turkey (Türkiye)

Location

Ege University School of Medicine

Izmir, Turkey (Türkiye)

Location

Related Publications (1)

  • Raghu G, Million-Rousseau R, Morganti A, Perchenet L, Behr J; MUSIC Study Group. Macitentan for the treatment of idiopathic pulmonary fibrosis: the randomised controlled MUSIC trial. Eur Respir J. 2013 Dec;42(6):1622-32. doi: 10.1183/09031936.00104612. Epub 2013 May 16.

MeSH Terms

Conditions

Idiopathic Pulmonary Fibrosis

Interventions

macitentan

Condition Hierarchy (Ancestors)

Pulmonary FibrosisLung Diseases, InterstitialLung DiseasesRespiratory Tract Diseases

Results Point of Contact

Title
Parisa Danaietash
Organization
Actelion Pharmaceuticals Ltd

Study Officials

  • Loic Perchenet, Ph.D.

    Actelion

    STUDY CHAIR

Publication Agreements

PI is Sponsor Employee
No
Restriction Type
LTE60
Restrictive Agreement
Yes

Study Design

Study Type
interventional
Phase
phase 2
Allocation
RANDOMIZED
Masking
QUADRUPLE
Who Masked
PARTICIPANT, CARE PROVIDER, INVESTIGATOR, OUTCOMES ASSESSOR
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

May 14, 2009

First Posted

May 18, 2009

Study Start

May 1, 2009

Primary Completion

June 1, 2011

Study Completion

August 1, 2011

Last Updated

February 17, 2014

Results First Posted

February 17, 2014

Record last verified: 2014-01

Locations