NCT00778882

Brief Summary

The purpose of this study is to evaluate the safety and efficacy of administration of autologous hematopoietic stem cells transduced with MT-gp91 retroviral vector for patients with X-linked chronic granulomatous disease.

Trial Health

30
At Risk

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Trial has exceeded expected completion date
Timeline
Completed

Started Jan 2007

Typical duration for phase_1

Geographic Reach
1 country

1 active site

Status
withdrawn

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

January 1, 2007

Completed
1.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

October 1, 2008

Completed
20 days until next milestone

First Submitted

Initial submission to the registry

October 21, 2008

Completed
3 days until next milestone

First Posted

Study publicly available on registry

October 24, 2008

Completed
1.9 years until next milestone

Study Completion

Last participant's last visit for all outcomes

October 1, 2010

Completed
Last Updated

September 25, 2025

Status Verified

August 1, 2025

Enrollment Period

1.8 years

First QC Date

October 21, 2008

Last Update Submit

September 23, 2025

Conditions

Keywords

Chronic Granulomatous DiseaseRetroviral VectorGene Therapy

Outcome Measures

Primary Outcomes (1)

  • The incidence of adverse events through 1 year

    1 year

Secondary Outcomes (4)

  • RCR, insertional mutagenesis, immune response against normal gp91 protein

    1 year

  • Safety and efficacy of fludarabine/busulfan conditioning

    1 year

  • Functional reconstitution of respiratory burst

    1 year

  • Presence of vector-positive cells

    1 year

Study Arms (1)

VM106

EXPERIMENTAL
Drug: VM106

Interventions

VM106DRUG

Autologous hematopoietic stem cells with MT-gp91 retroviral vector

VM106

Eligibility Criteria

Sexmale
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • gp91 defective male patients with chronic granulomatous disease: confirmed by DHR
  • Weigh greater than or equal to 15 kg
  • History of severe infections: more than 2 times
  • Performance status: ECOG 0-2
  • Patients must be free of significant functional deficits in major organs, but the following eligibility criteria may be modified in individual cases.
  • Heart: a shortening fraction \> 28%; QTc interval \< 0.44
  • Liver: total bilirubin \< 2 × upper limit of normal; ALT \< 3 × upper limit of normal; AST \< 3 x upper limit of normal
  • Kidney: creatine \< 2 x normal
  • Blood: WBC \> 2,500/uL; platelet \> 100,000/uL; hematocrit \> 26%
  • Written informed consent obtained from patient (or guardian if patients age \< 19)

You may not qualify if:

  • Presence of a HLA-matched sibling for stem cell donation
  • Evidence or history of malignant tumor
  • Presence of a severe infection
  • Presence of an active tuberculosis
  • Uncorrectable electrolyte, Ca, P
  • Unable to comply with the protocol or to cooperate fully with the Investigator or site personnel

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (1)

Seoul National University Hospital

Seoul, 110-744, South Korea

Location

MeSH Terms

Conditions

Granulomatous Disease, Chronic

Condition Hierarchy (Ancestors)

Phagocyte Bactericidal DysfunctionLeukocyte DisordersHematologic DiseasesHemic and Lymphatic DiseasesGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesImmunologic Deficiency SyndromesImmune System DiseasesChronic DiseaseDisease AttributesPathologic ProcessesPathological Conditions, Signs and Symptoms

Study Officials

  • Joong Gon Kim, MD, PhD

    Seoul National University Hospital

    PRINCIPAL INVESTIGATOR
0

Study Design

Study Type
interventional
Phase
phase 1
Allocation
NA
Masking
NONE
Purpose
TREATMENT
Intervention Model
SINGLE GROUP
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

October 21, 2008

First Posted

October 24, 2008

Study Start

January 1, 2007

Primary Completion

October 1, 2008

Study Completion

October 1, 2010

Last Updated

September 25, 2025

Record last verified: 2025-08

Locations