NCT00515398

Brief Summary

The purpose of this study is to see how molecules called pharmacological chaperones affect the cells of patients with Pompe disease. The study will last 1 or 2 visits which will include a blood collection, urine collection, and two skin biopsies. Information will also be collected from the medical records about disease history and diagnosis. Patients will not receive any study medication.

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
30

participants targeted

Target at below P25 for all trials

Timeline
Completed

Started Aug 2007

Shorter than P25 for all trials

Geographic Reach
1 country

4 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

Study Start

First participant enrolled

August 1, 2007

Completed
9 days until next milestone

First Submitted

Initial submission to the registry

August 10, 2007

Completed
3 days until next milestone

First Posted

Study publicly available on registry

August 13, 2007

Completed
5 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

January 1, 2008

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

January 1, 2008

Completed
Last Updated

June 5, 2008

Status Verified

June 1, 2008

Enrollment Period

5 months

First QC Date

August 10, 2007

Last Update Submit

June 4, 2008

Conditions

Outcome Measures

Primary Outcomes (1)

  • To evaluate and characterize the effects of pharmacological chaperones on enzyme activity and other markers of disease in cell lines derived from patients with Pompe disease

    1 week

Secondary Outcomes (1)

  • To study biomarkers associated with Pompe Disease and study the correlation between biomarkers and clinical disease state of patients with Pompe disease

    1 week

Study Arms (1)

1

Group 1 (all subjects)

Other: Observation

Interventions

Ex vivo administration of AT2220

1

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Patients with Pompe disease

You may qualify if:

  • Male or female of any age
  • Confirmed diagnosis of Pompe disease (early or late-onset)
  • Clinically stable
  • Written informed consent by subject or legal representative

You may not qualify if:

  • Other significant disease or otherwise unsuitable for the study, as determined by the investigator

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (4)

University of Florida

Gainesville, Florida, 32610-0296, United States

Location

Washington University

St Louis, Missouri, 63110, United States

Location

Center for Metabolic Disorders

Lake Success, New York, 11042, United States

Location

Duke University

Durham, North Carolina, 27708, United States

Location

Biospecimen

Retention: SAMPLES WITH DNA

White blood cells

MeSH Terms

Conditions

Glycogen Storage Disease Type II

Interventions

Observation

Condition Hierarchy (Ancestors)

Lysosomal Storage Diseases, Nervous SystemBrain Diseases, Metabolic, InbornBrain Diseases, MetabolicBrain DiseasesCentral Nervous System DiseasesNervous System DiseasesMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesGlycogen Storage DiseaseCarbohydrate Metabolism, Inborn ErrorsLysosomal Storage DiseasesMetabolic DiseasesNutritional and Metabolic Diseases

Intervention Hierarchy (Ancestors)

MethodsInvestigative Techniques

Study Officials

  • Irina Kline, MD

    Amicus Therapeutics

    STUDY DIRECTOR

Study Design

Study Type
observational
Observational Model
CASE ONLY
Time Perspective
CROSS SECTIONAL
Sponsor Type
INDUSTRY

Study Record Dates

First Submitted

August 10, 2007

First Posted

August 13, 2007

Study Start

August 1, 2007

Primary Completion

January 1, 2008

Study Completion

January 1, 2008

Last Updated

June 5, 2008

Record last verified: 2008-06

Locations