NCT00349453

Brief Summary

Systematical (retro- and prospective) investigation of the long-term safety (toxicity assessment according to CTCAE v3.0) and efficacy of deferiprone either given alone or in combination with desferrioxamine

Trial Health

87
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
24

participants targeted

Target at below P25 for phase_2

Timeline
Completed

Started Mar 2005

Longer than P75 for phase_2

Geographic Reach
1 country

13 active sites

Status
completed

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Start

First participant enrolled

March 1, 2005

Completed
1.3 years until next milestone

First Submitted

Initial submission to the registry

July 6, 2006

Completed
1 day until next milestone

First Posted

Study publicly available on registry

July 7, 2006

Completed
4.8 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

May 1, 2011

Completed
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

May 1, 2011

Completed
Last Updated

December 12, 2011

Status Verified

December 1, 2011

Enrollment Period

6.2 years

First QC Date

July 6, 2006

Last Update Submit

December 9, 2011

Conditions

Keywords

DeferiproneL1DesferrioxamineHemochromatosisIron overloadThalassemia

Outcome Measures

Primary Outcomes (2)

  • Liver Iron Concentration (LIC) by SQUID

    Yearly

  • Long-term safety profile

    Long-term

Secondary Outcomes (3)

  • Serum ferritin

    At quarterly control visits

  • Urinary Iron Excretion (UIE)

    At six-monthly control visits

  • Heart iron content (optional) by MRI T2* and MRI SIR

    Yearly

Study Arms (2)

Deferiprone (L1) monotherapy

EXPERIMENTAL

Deferiprone (L1) monotherapy

Drug: Deferiprone (L1)

Combination therapy

EXPERIMENTAL

Deferiprone (L1) and desferrioxamine combination treatment

Drug: Deferiprone (L1)Drug: Desferrioxamine

Interventions

50-100 mg/kg body weight daily

Deferiprone (L1) monotherapy

35-50 mg/kg body weight on 2 or more days per week

Combination therapy

Eligibility Criteria

Age4 Years+
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Iron overloaded male or female patients with primary or secondary hemochromatosis
  • Age: 4 years and older
  • Patients with desferrioxamine toxicity or allergy (e.g. visual or hearing defects, bone abnormalities, reactions at injection site)
  • Patients unable or unwilling to comply satisfactorily with regular desferrioxamine administration on 5-7 days/week
  • Combination treatment: patients not sufficiently chelated with desferrioxamine or deferiprone monotherapy
  • Patients must be willing to undergo routine screening including medical history, physical examination and hematology, biochemistry and other laboratory tests
  • Written informed consent

You may not qualify if:

  • Children under 4 years of age
  • Female and male of reproductive age, sexually active but not taking adequate contraceptive precaution
  • Woman who are pregnant or breast-feeding
  • Patients with HIV
  • Patients with active hepatitis requiring treatment
  • Patients with severe hepatic failure, cirrhosis
  • Patients with neutropenia (neutrophils less than 1.5 exp9/l, MDS: less than 0.5 exp9/l)
  • Patients with thrombocytopenia (platelets less than 100 exp9/l, MDS: less than 20 exp9/l)
  • Patients with decompensated heart failure (LVEF less than 40% or patients under continuous cardiac medication)
  • Patients with severe renal failure

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (13)

Cantonal Hospital, Children's Clinic

Aarau, Canton of Aargau, 5001, Switzerland

Location

Cantonal Hospital

Aarau, Canton of Aargau, 5001, Switzerland

Location

Private children's practice

Bern, Canton of Bern, 3014, Switzerland

Location

Children's Hospital of Eastern Switzerland

Sankt Gallen, Canton of St. Gallen, 9006, Switzerland

Location

University Children's Hospital

Zurich, Canton of Zurich, 8032, Switzerland

Location

University Hospital

Zurich, Canton of Zurich, 8091, Switzerland

Location

Private practice

Zürich (Kreis 11) / Oerlikon, Canton of Zurich, 8050, Switzerland

Location

Private practice

Arzo, Canton Ticino, 6864, Switzerland

Location

Private practice

Lugano, Canton Ticino, 6900, Switzerland

Location

Regional Hospital

Lugano, Canton Ticino, 6900, Switzerland

Location

Private practice

Riva San Vitale, Canton Ticino, 6826, Switzerland

Location

Cantonal Hospital Graubünden

Chur, Kanton Graubünden, 7000, Switzerland

Location

Private children's practice

Brig, Valais, 3900, Switzerland

Location

Related Publications (2)

  • Tondury P, Zimmermann A, Nielsen P, Hirt A. Liver iron and fibrosis during long-term treatment with deferiprone in Swiss thalassaemic patients. Br J Haematol. 1998 Jun;101(3):413-5. doi: 10.1046/j.1365-2141.1998.00725.x.

  • Tondury P, Kontoghiorghes GJ, Ridolfi-Luthy A, Hirt A, Hoffbrand AV, Lottenbach AM, Sonderegger T, Wagner HP. L1 (1,2-dimethyl-3-hydroxypyrid-4-one) for oral iron chelation in patients with beta-thalassaemia major. Br J Haematol. 1990 Dec;76(4):550-3. doi: 10.1111/j.1365-2141.1990.tb07915.x.

MeSH Terms

Conditions

HemochromatosisIron OverloadThalassemia

Interventions

DeferiproneLong Interspersed Nucleotide ElementsDeferoxamine

Condition Hierarchy (Ancestors)

Metal Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesIron Metabolism DisordersMetabolic DiseasesNutritional and Metabolic DiseasesAnemia, Hemolytic, CongenitalAnemia, HemolyticAnemiaHematologic DiseasesHemic and Lymphatic DiseasesHemoglobinopathies

Intervention Hierarchy (Ancestors)

PyridonesPyridinesHeterocyclic Compounds, 1-RingHeterocyclic CompoundsRetroelementsInterspersed Repetitive SequencesRepetitive Sequences, Nucleic AcidBase SequenceMolecular StructureBiochemical PhenomenaChemical PhenomenaGenetic StructuresGenetic PhenomenaGenome ComponentsGenomeHydroxamic AcidsHydroxylaminesAminesOrganic ChemicalsHydroxy AcidsCarboxylic Acids

Study Officials

  • Petrign FG Töndury, MD

    PRINCIPAL INVESTIGATOR
  • Markus Schmugge Liner, MD

    University Children's Hospital, Zurich

    PRINCIPAL INVESTIGATOR

Study Design

Study Type
interventional
Phase
phase 2
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
PARALLEL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

July 6, 2006

First Posted

July 7, 2006

Study Start

March 1, 2005

Primary Completion

May 1, 2011

Study Completion

May 1, 2011

Last Updated

December 12, 2011

Record last verified: 2011-12

Locations