NCT06591793

Brief Summary

The purpose of the 081-101 study is to evaluate the safety and tolerability of a single subretinal injection of AAVB-081 in USH1B patients with retinitis pigmentosa due to a mutation in the MYO7A gene. The study will also assess the initial efficacy following AAVB-081 administration.

Trial Health

80
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
15

participants targeted

Target at below P25 for phase_1

Timeline
38mo left

Started Jul 2024

Longer than P75 for phase_1

Geographic Reach
2 countries

3 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress37%
Jul 2024Jul 2029

Study Start

First participant enrolled

July 2, 2024

Completed
2 months until next milestone

First Submitted

Initial submission to the registry

August 16, 2024

Completed
1 month until next milestone

First Posted

Study publicly available on registry

September 19, 2024

Completed
10 months until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 1, 2025

Completed
4 years until next milestone

Study Completion

Last participant's last visit for all outcomes

July 1, 2029

Expected
Last Updated

May 2, 2025

Status Verified

May 1, 2025

Enrollment Period

12 months

First QC Date

August 16, 2024

Last Update Submit

May 1, 2025

Conditions

Keywords

Usher SyndromeMYO7AUSH1BRetinitis Pigmentosa

Outcome Measures

Primary Outcomes (1)

  • To measure the number and severity of treatment related adverse events following treatment with AAVB-081

    61 months

Secondary Outcomes (2)

  • Change from baseline in microperimetry following treatment with AAVB-081

    61 months

  • Change from baseline in static perimetry following treatment with AAVB-081

    61 months

Study Arms (3)

Cohort 1

EXPERIMENTAL

AAVB-081 dose level 1

Biological: AAVB-081

Cohort 2

EXPERIMENTAL

AAVB-081 dose level 2

Biological: AAVB-081

Cohort 3

EXPERIMENTAL

AAVB-081 dose level 3

Biological: AAVB-081

Interventions

AAVB-081BIOLOGICAL

Single subretinal administration

Cohort 1Cohort 2Cohort 3

Eligibility Criteria

Age18 Years - 50 Years
Sexall
Healthy VolunteersNo
Age GroupsAdult (18-64)

You may qualify if:

  • Molecular diagnosis of USB1B due to MYO7A mutation
  • Willingness to adhere to protocol per informed consent

You may not qualify if:

  • Unwillingness to meet the requirements of the study
  • Participation in a clinical study with an Investigation Product in the past 6 months
  • Previous participation in another Gene Therapy trial
  • Any condition that would preclude subretinal surgery
  • Complicating ocular and/or systemic diseases

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (3)

University of Campania Luigi Vanvitelli

Naples, Italy

RECRUITING

Moorfields Eye Hospital

London, United Kingdom

RECRUITING

Retina Clinic London

London, United Kingdom

RECRUITING

MeSH Terms

Conditions

Usher syndrome, type 1BUsher SyndromesRetinitis Pigmentosa

Condition Hierarchy (Ancestors)

Deaf-Blind DisordersDeafnessHearing LossHearing DisordersEar DiseasesOtorhinolaryngologic DiseasesHearing Loss, SensorineuralSensation DisordersNeurologic ManifestationsNervous System DiseasesBlindnessVision DisordersRetinal DystrophiesRetinal DegenerationRetinal DiseasesEye DiseasesAbnormalities, MultipleCongenital AbnormalitiesCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesEye Diseases, HereditaryGenetic Diseases, InbornSigns and SymptomsPathological Conditions, Signs and Symptoms

Central Study Contacts

Clinical Operations Manager

CONTACT

Study Design

Study Type
interventional
Phase
phase 1
Allocation
NON RANDOMIZED
Masking
NONE
Purpose
TREATMENT
Intervention Model
SEQUENTIAL
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

August 16, 2024

First Posted

September 19, 2024

Study Start

July 2, 2024

Primary Completion

July 1, 2025

Study Completion (Estimated)

July 1, 2029

Last Updated

May 2, 2025

Record last verified: 2025-05

Data Sharing

IPD Sharing
Will not share

Locations