NCT06491615

Brief Summary

Background: The eyeGENE (Registered Trademark) program is a research resource for inherited eye conditions which includes genotypic and phenotypic data, imaging, and a corresponding biobank of DNA samples from people with a variety of eye diseases. Since 2007 this registry has been helping researchers learn more about the genetic sources for many inherited eye diseases. These findings helped them create better treatments. Now researchers want to expand eyeGENE (Registered Trademark) to include more people for certain eye diseases. Objective: To collect information and DNA samples for the study of eye diseases.

  • Primary objective
  • -To expand the current eyeGENE (Registered Trademark) data repository with targeted participant accrual
  • Secondary objectives
  • To enhance recruitment for clinical trials and investigations in inherited eye diseases
  • To establish genotype-phenotype correlations for rare eye diseases Eligibility: People of any age with certain eye diseases. These can include aniridia; Best disease; blue-cone monochromacy; corneal dystrophy; and disorders of pigmentation, such as albinism. Relatives unaffected by the eye disease of interest may also be needed. Design: Researchers will select participants based on their diagnosis. The data may include images and test results from eye exams. Participants will provide a sample of saliva. They will receive a kit with written instructions. They will spit in a tube and mail it to the NIH. Participants may be asked to provide a blood sample. The blood may be drawn at the NIH or at a local clinic. The eyeGENE (Registered Trademark) repository will offer researchers data about the participants eye conditions. The data may include pictures of their eyes, results of the genetic testing, and history of other diseases. Researchers will be able to see data such as age and gender, but they will not see names, dates of birth, or contact information.

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
1,000

participants targeted

Target at P75+ for all trials

Timeline
343mo left

Started Jul 2024

Longer than P75 for all trials

Geographic Reach
1 country

2 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress6%
Jul 2024Jun 2054

First Submitted

Initial submission to the registry

July 8, 2024

Completed
1 day until next milestone

First Posted

Study publicly available on registry

July 9, 2024

Completed
3 days until next milestone

Study Start

First participant enrolled

July 12, 2024

Completed
30 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

June 27, 2054

Expected
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

June 27, 2054

Last Updated

May 4, 2026

Status Verified

April 30, 2026

Enrollment Period

30 years

First QC Date

July 8, 2024

Last Update Submit

May 1, 2026

Conditions

Keywords

eyeGENEGeneticsInherited

Outcome Measures

Primary Outcomes (1)

  • To expand the current eyeGENE data repository with targeted participant accrual.

    To expand the current eyeGENE data repository with targeted participant accrual.

    30 years

Secondary Outcomes (2)

  • To enhance recruitment for clinical trials and investigations in inherited eye diseases.

    30 years

  • To establish genotype-phenotype correlations for rare eye diseases.

    30 years

Study Arms (1)

Participants

Participants with inherited eye diseases or relative of affected participant

Eligibility Criteria

Age1 Day - 120 Years
Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Participants with inherited eye diseases or their unaffected relatives.

You may qualify if:

  • In order to be eligible to participate in this study, an individual must meet all of the following criteria:
  • The participant must present with characteristics consistent with one of the following diagnoses:
  • Aniridia
  • Best disease
  • Blue-cone monochromacy
  • Corneal dystrophy
  • Other hypopigmentation disorder affecting vision (e.g., Oculocutaneous and ocular albinism, Hermansky-Pudlak syndrome, Chediak-Higashi syndrome)
  • The participant must be a direct, close relative of an affected participant.
  • A participant who also participated in the eyeGENE Stage 1 protocol who may benefit from further genetic testing.

You may not qualify if:

  • An individual who meets any of the following criteria will be excluded from participation in this study:
  • Those with impaired decision-making capability who do not have a legally-authorized representative.
  • Those unable to provide a saliva sample OR have any disease or condition that makes it unsafe for a subject to provide a suitable blood sample of at least 5 mL to yield more than 50 micrograms of DNA.
  • An individual who meets any of the following criteria will be excluded from participation in the optional retinal imaging:
  • Those with a history of epilepsy.
  • Children under the age of 18.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (2)

National Eye Institute (NEI)

Bethesda, Maryland, 20892, United States

RECRUITING

National Institutes of Health Clinical Center

Bethesda, Maryland, 20892, United States

RECRUITING

Related Links

MeSH Terms

Conditions

VitiligoCorneal Dystrophies, HereditaryBlue cone monochromatismVitelliform Macular DystrophyAniridiaAlbinism

Condition Hierarchy (Ancestors)

HypopigmentationPigmentation DisordersSkin DiseasesSkin and Connective Tissue DiseasesCorneal DiseasesEye DiseasesEye Diseases, HereditaryGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesMacular DegenerationRetinal DegenerationRetinal DiseasesEye AbnormalitiesIris DiseasesUveal DiseasesCongenital AbnormalitiesAmino Acid Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsSkin Diseases, GeneticMetabolic DiseasesNutritional and Metabolic Diseases

Study Officials

  • Brian P Brooks, M.D.

    National Eye Institute (NEI)

    PRINCIPAL INVESTIGATOR

Central Study Contacts

eyeGene Coordinating Center

CONTACT

Brian P Brooks, M.D.

CONTACT

Study Design

Study Type
observational
Observational Model
COHORT
Time Perspective
OTHER
Sponsor Type
NIH
Responsible Party
SPONSOR

Study Record Dates

First Submitted

July 8, 2024

First Posted

July 9, 2024

Study Start

July 12, 2024

Primary Completion (Estimated)

June 27, 2054

Study Completion (Estimated)

June 27, 2054

Last Updated

May 4, 2026

Record last verified: 2026-04-30

Data Sharing

IPD Sharing
Will not share

Locations