NCT04530994

Brief Summary

An open-label, single-arm, multi-centre program providing treatment access to ALGS patients with cholestatic pruritus in the US. Access can be requested through Clinigen Healthcare Ltd via email MirumALGS@clinigengroup.com or telephone +1-877-768-4303.

Trial Health

55
Monitor

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Geographic Reach
1 country

14 active sites

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

August 25, 2020

Completed
3 days until next milestone

First Posted

Study publicly available on registry

August 28, 2020

Completed
Last Updated

October 20, 2021

Status Verified

October 1, 2021

First QC Date

August 25, 2020

Last Update Submit

October 12, 2021

Conditions

Keywords

Liver DiseaseALGSMaralixibatBile Duct DiseasesDigestive System DiseasesBiliary Tract DiseasesCholestasisPruritis

Interventions

Maralixibat is an Apical Sodium-dependent Bile acid Transporter (ASBT) inhibitor

Eligibility Criteria

Age12 Months+
Sexall
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)

You may qualify if:

  • Informed consent and assent provided, as applicable, per Institutional Review Board (IRB) or Ethics Committee (EC)
  • Clinical and/or genetic diagnosis of ALGS
  • Male or female participants aged \>12 months and ≥5 kg with clinically significant cholestatic pruritus associated with ALGS
  • Willingness to adhere to an acceptable method of contraception until treatment discontinuation by females of childbearing potential who are sexually active or who become sexually active during the program
  • No other therapeutic options or access to any ongoing ALGS clinical trials

You may not qualify if:

  • Diagnosis with a cholestatic liver disease other than ALGS
  • Female who is pregnant or breastfeeding
  • Clinically significant cardiovascular, hepatic, gastro-intestinal, pulmonary, neurologic, infectious or renal disease or other medical condition that, in the opinion of the physician or Medical Monitor, would preclude participation in the program
  • Past medical history of compensated or decompensated cirrhosis
  • Presence of any other disease or condition known to interfere with the absorption, distribution, metabolism, or excretion of maralixibat or its mode of action

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (14)

University of California, Los Angeles

Los Angeles, California, 90095, United States

Location

Stanford University

Redwood City, California, 94063, United States

Location

University of California San Francisco

San Francisco, California, 94158, United States

Location

Georgetown University

Washington D.C., District of Columbia, 20007, United States

Location

Advent Health

Orlando, Florida, 32804, United States

Location

Children's Healthcare of Atlanta/Emory University

Atlanta, Georgia, 30329, United States

Location

Ann & Robert H. Lurie Children's Hospital

Chicago, Illinois, 60611, United States

Location

Ochsner Clinic Foundation

New Orleans, Louisiana, 70121, United States

Location

University of Minnesota

Minneapolis, Minnesota, 55455, United States

Location

The Children's Hospital at Montefiore

New York, New York, 10467, United States

Location

University of Oklahoma

Oklahoma City, Oklahoma, 73104, United States

Location

Baylor College of Medicine

Houston, Texas, 77030, United States

Location

University of Virginia

Charlottesville, Virginia, 22903, United States

Location

Medical College of Wisconsin

Milwaukee, Wisconsin, 53226, United States

Location

Related Links

MeSH Terms

Conditions

Alagille SyndromeLiver DiseasesBile Duct DiseasesDigestive System DiseasesBiliary Tract DiseasesCholestasisPruritus

Interventions

maralixibat

Condition Hierarchy (Ancestors)

Cholestasis, IntrahepaticHeart Defects, CongenitalCardiovascular AbnormalitiesCardiovascular DiseasesAbnormalities, MultipleCongenital AbnormalitiesCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesGenetic Diseases, InbornSkin DiseasesSkin and Connective Tissue DiseasesSkin ManifestationsSigns and SymptomsPathological Conditions, Signs and Symptoms

Study Design

Study Type
expanded access
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

August 25, 2020

First Posted

August 28, 2020

Last Updated

October 20, 2021

Record last verified: 2021-10

Locations