NCT04199000

Brief Summary

The purpose of this research is to study the natural history of congenital disorders of glycosylation and its causes and treatments.

Trial Health

77
On Track

Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Enrollment
500

participants targeted

Target at P75+ for all trials

Timeline
52mo left

Started Oct 2019

Longer than P75 for all trials

Geographic Reach
1 country

12 active sites

Status
recruiting

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

Click on a node to explore related trials.

Study Timeline

Key milestones and dates

Study Progress61%
Oct 2019Jul 2030

Study Start

First participant enrolled

October 8, 2019

Completed
2 months until next milestone

First Submitted

Initial submission to the registry

December 8, 2019

Completed
5 days until next milestone

First Posted

Study publicly available on registry

December 13, 2019

Completed
10.6 years until next milestone

Primary Completion

Last participant's last visit for primary outcome

July 31, 2030

Expected
Same day until next milestone

Study Completion

Last participant's last visit for all outcomes

July 31, 2030

Last Updated

August 26, 2025

Status Verified

August 1, 2025

Enrollment Period

10.8 years

First QC Date

December 8, 2019

Last Update Submit

August 24, 2025

Conditions

Keywords

CDGCDDGCongenital Disorders of GlycosylationCongenital Disorders of DeglycosylationALG1ALG3ALG6ALG12ALG13COG6DPAGT1DPM1EDEM3MAN1B1MPDU1MPINGLY1PGAP3PGM1PIGAPIGGPIGNPIGSPIGTPMM2SLC35A2SLC35C1SLC39A8SRD5A3SSR4FUT8GALNT2MAN2B2VMA21

Outcome Measures

Primary Outcomes (3)

  • Indicators of Disease Severity and Progression - organ system involvement

    Establish the prevalence and severity of specific morbid indicators of disease severity through use of the Nijmegen Progression CDG rating scale.

    Length of study, up to 5 years

  • Indicators of Disease Severity and Progression - degree of cognitive disability

    Establish the prevalence and severity of specific morbid indicators of disease severity through use of the Nijmegen Progression CDG rating scale.

    Length of study, up to 5 years

  • Indicators of Disease Severity and Progression - case-fatality

    Establish the prevalence and severity of specific morbid indicators of disease severity through use of the Nijmegen Progression CDG rating scale.

    Length of study, up to 5 years

Eligibility Criteria

Sexall
Healthy VolunteersNo
Age GroupsChild (0-17), Adult (18-64), Older Adult (65+)
Sampling MethodNon-Probability Sample
Study Population

Individuals with a genetically, enzymatically, or molecularly confirmed diagnosis of a congenital disorder of glycosylation (CDG) or NGLY1 deficiency, or individuals whose laboratory values are highly suggestive of CDG

You may qualify if:

  • Individuals with a genetically, enzymatically, or molecularly confirmed diagnosis of CDG or NGLY1 deficiency

You may not qualify if:

  • None

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (12)

Rady Children's Hospital

San Diego, California, 92123, United States

RECRUITING

Children's Hospital of Colorado

Aurora, Colorado, 80045, United States

RECRUITING

Mayo Clinic Florida

Jacksonville, Florida, 32224, United States

RECRUITING

Tulane University School of Medicine

New Orleans, Louisiana, 70112, United States

NOT YET RECRUITING

Boston Children's Hospital

Boston, Massachusetts, 02115, United States

RECRUITING

University of Minnesota

Minneapolis, Minnesota, 55454, United States

RECRUITING

Mayo Clinic in Rochester

Rochester, Minnesota, 55905, United States

RECRUITING

Icahn School of Medicine at Mount Sinai

New York, New York, 10029, United States

RECRUITING

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19146, United States

RECRUITING

Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, 15224, United States

RECRUITING

Baylor College of Medicine

Houston, Texas, 77030, United States

RECRUITING

Seattle Children's Hospital

Seattle, Washington, 98105, United States

RECRUITING

Related Links

Biospecimen

Retention: SAMPLES WITH DNA

Stool, urine, and blood can be retained for biomarker testing. DNA may be a part of this testing in the future.

MeSH Terms

Conditions

Congenital Disorders of Glycosylation

Condition Hierarchy (Ancestors)

Carbohydrate Metabolism, Inborn ErrorsMetabolism, Inborn ErrorsGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesMetabolic DiseasesNutritional and Metabolic Diseases

Study Officials

  • Eva Morava-Kozicz, MD, PhD

    Icahn School of Medicine at Mount Sinai

    PRINCIPAL INVESTIGATOR

Central Study Contacts

Eva Morava-Kozicz, PhD, MD

CONTACT

Mary Freeman, MS, CGC

CONTACT

Study Design

Study Type
observational
Observational Model
CASE ONLY
Time Perspective
OTHER
Sponsor Type
OTHER
Responsible Party
PRINCIPAL INVESTIGATOR
PI Title
Principal Investigator

Study Record Dates

First Submitted

December 8, 2019

First Posted

December 13, 2019

Study Start

October 8, 2019

Primary Completion (Estimated)

July 31, 2030

Study Completion (Estimated)

July 31, 2030

Last Updated

August 26, 2025

Record last verified: 2025-08

Data Sharing

IPD Sharing
Will share

De-identified data and samples may be shared with other investigators at the discretion of the PI. Only participants who have consented to sharing data/samples will be included in this portion.

Shared Documents
STUDY PROTOCOL, ICF
Time Frame
Length of study and beyond

Locations