NCT04074512

Brief Summary

This expanded access protocol provides subcutaneous copper histidinate for Menkes disease patients under 6 years of age.

Trial Health

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Trial Health Score

Automated assessment based on enrollment pace, timeline, and geographic reach

Geographic Reach
1 country

20 active sites

Status
unknown

Health score is calculated from publicly available data and should be used for screening purposes only.

Trial Relationships

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Study Timeline

Key milestones and dates

First Submitted

Initial submission to the registry

August 27, 2019

Completed
3 days until next milestone

First Posted

Study publicly available on registry

August 30, 2019

Completed
Last Updated

March 2, 2026

Status Verified

February 1, 2026

First QC Date

August 27, 2019

Last Update Submit

February 26, 2026

Conditions

Interventions

copper histidinate for subcutaneous injection

Also known as: CUTX-101

Eligibility Criteria

Age0 Years - 6 Years
Sexall
Age GroupsChild (0-17)

You may qualify if:

  • The subject must have been treated in protocol 09-CH-0059 or must be a newly diagnosed Menkes disease patient in the US.
  • Parent or legal guardian is willing and able to sign and date an informed consent form.
  • Male or female, aged 0 to \<6 years of age.
  • Diagnosis of Menkes disease: A confirmed gene mutation in ATP7A is not required; however, the test must be at least pending prior to initiating therapy. For those patients whose molecular ATP7A gene mutation confirmation is pending, they should have serum copper \<75 mcg/dL. If the mutation is subsequently not confirmed, the patient should discontinue treatment.
  • Ability to adhere to the prescribed subcutaneous copper histidinate injection regimen.
  • Willingness to adhere to all recommended visits and procedures.
  • Resident of the US.

You may not qualify if:

  • Diagnosis of Wilson disease.
  • Any disease or condition that, in the opinion of the Investigator, has a high probability of precluding the subject from completing the study or where the subject cannot or will not appropriately comply with study requirements.
  • Receipt of concomitant medication or device not approved for any use (i.e. experimental) by FDA within 30 days prior to screening for this study, except for participation in protocol 09-CH-0059.
  • Patient/caregiver cannot or will not appropriately comply with protocol recommendations (e.g., site visits, renal monitoring).
  • Currently receiving any concomitant copper-containing medications.

Contact the study team to confirm eligibility.

Sponsors & Collaborators

Study Sites (20)

Phoenix Children's Hospital

Phoenix, Arizona, 85016, United States

Location

University of California Davis Medical Center

Sacramento, California, 95817, United States

Location

Rady Children's Hospital

San Diego, California, 92123, United States

Location

Children's Hospital Colorado

Aurora, Colorado, 80045, United States

Location

Connecticut Children's Medical Center

Hartford, Connecticut, 06106, United States

Location

Memorial Healthcare Systems

Hollywood, Florida, 33021, United States

Location

Johns Hopkins All Children's Hospital

St. Petersburg, Florida, 33701, United States

Location

Emory University

Atlanta, Georgia, 30322, United States

Location

Lurie Children's Hospital of Chicago

Chicago, Illinois, 60611, United States

Location

University of Iowa Stead Family Children's Hospital

Iowa City, Iowa, 52242, United States

Location

Maine Medical Center

Portland, Maine, 04102, United States

Location

Helen DeVos Children's Hospital

Grand Rapids, Michigan, 49503, United States

Location

Shodair Children's Hospital

Helena, Montana, 59601, United States

Location

Duke University Hospital

Durham, North Carolina, 27710, United States

Location

Oregon Health & Science University

Portland, Oregon, 97239, United States

Location

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, 19104, United States

Location

Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, 15224, United States

Location

Monroe Carrell Jr. Children's Hospital at Vanderbilt University Medical Center

Nashville, Tennessee, 37232, United States

Location

Cook Children's Health Care System

Fort Worth, Texas, 76104, United States

Location

Seattle Children's Hospital

Seattle, Washington, 98105, United States

Location

Related Links

MeSH Terms

Conditions

Menkes Kinky Hair Syndrome

Interventions

copper bis(histidinate)

Condition Hierarchy (Ancestors)

Brain Diseases, Metabolic, InbornBrain Diseases, MetabolicBrain DiseasesCentral Nervous System DiseasesNervous System DiseasesX-Linked Intellectual DisabilityIntellectual DisabilityNeurobehavioral ManifestationsNeurologic ManifestationsGenetic Diseases, X-LinkedGenetic Diseases, InbornCongenital, Hereditary, and Neonatal Diseases and AbnormalitiesHeredodegenerative Disorders, Nervous SystemMetabolism, Inborn ErrorsMetal Metabolism, Inborn ErrorsHair DiseasesSkin DiseasesSkin and Connective Tissue DiseasesMetabolic DiseasesNutritional and Metabolic Diseases

Study Design

Study Type
expanded access
Sponsor Type
INDUSTRY
Responsible Party
SPONSOR

Study Record Dates

First Submitted

August 27, 2019

First Posted

August 30, 2019

Last Updated

March 2, 2026

Record last verified: 2026-02

Locations